| galactose-6-sulfatase | <enzyme> An enzyme that eliminates sulfur from the galactose-6-sulfate residues of certain mucopolysaccharides, producing 3,6-anhydrogalactose residues; it is absent in Morquio's syndrome type A. Synonym: galactose-6-sulfurase. (05 Mar 2000) |
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| galactose-6-sulfurase | <enzyme> An enzyme that eliminates sulfur from the galactose-6-sulfate residues of certain mucopolysaccharides, producing 3,6-anhydrogalactose residues; it is absent in Morquio's syndrome type A. Synonym: galactose-6-sulfurase. (05 Mar 2000) |
| galactose binding protein | <protein> A bacterial periplasmic protein, most studied in E. Coli, that acts both as a sensory element in the detection of galactose as a chemotactic signal and in the uptake of the sugar. (18 Nov 1997) |
| galactose cataract | A neonatal cataract associated with intralenticular accumulation of galactose alcohol. See: galactosaemia. (05 Mar 2000) |
| galactose dehydrogenases | <enzyme> D-galactose:NAD(p)+ 1-oxidoreductases. Catalyses the oxidation of d-galactose in the presence of NAD+ or NADP+ to d-galactono-gamma-lactone and NADH or NADPH. Registry number: EC 1.1.1. (12 Dec 1998) |
| galactose diabetes | <biochemistry> A rare genetic (autosomal recessive) disorder characterised by the inability a defect in the enzyme (galactose 1 phosphate uridyl transferase) that converts galactose 1 phosphate into glucose 1 phosphate is absent. Excess galactose 1 phosphate accumulates in the blood and a variety of problems result. Inheritance: autosomal recessive. Origin: Gr. Haima = blood (27 Sep 1997) |
| galactose-diphosphoglycosyl carrier lipid synthetase | <enzyme> Catalyses synthesis of gcl-pp-gal from udp gal and p-gcl; also catalyses exchange between the uridylyl moiety of udpgal and ump Registry number: EC 2.4.1.- (26 Jun 1999) |
| galactose oxidase | <enzyme> An enzyme that oxidises galactose in the presence of molecular oxygen to d-galacto-hexodialdose. It is a copper protein. Chemical name: D-Galactose:oxygen 6-oxidoreductase Registry number: EC 1.1.3.9 (12 Dec 1998) |
| galactose permease | <chemical> (26 Jun 1999) |
| galactose tolerance test | A liver function test, based on the ability of the liver to convert galactose to glycogen, measured by the rate of excretion of galactose following ingestion or intravenous injection of a known amount; normally, less than 3 g appear in the urine within 5 hours after the ingestion of 40 g. (05 Mar 2000) |
| UDPgalactosamine-galactose acetylgalactosaminyltransferase | <enzyme> Transfers sugars from udp-n-acetylgalactosamine to terminal galactose of h substance, producing a antigen; consider also fucosyl galactose alpha-n-acetylgalactosaminyltransferase which is called a-transferase Registry number: EC 2.4.1.- Synonym: blood group a-enzyme, blood group glycosyltransferase a, alpha-3-d-n-acetylgalactosaminyltransferase, alpha-3-n-acetyl-d-galactosaminyltransferase (26 Jun 1999) |
| UDP-galactose 4-O-beta-D-galactosyl-D-xylose galactosyltransferase | <enzyme> Involved in chondroitin sulfate synthesis Registry number: EC 2.4.1.- (26 Jun 1999) |
| UDP-galactose hydrolase | <enzyme> Hydrolyzes udp-galactose to galactose Registry number: EC 3.1.4.- (26 Jun 1999) |
| UDP-galactose-lactosylceramide alpha 1-4-galactosyltransferase | <enzyme> Catalyses transfer of galactose from udp-galactose to lactosylceramide; exclusively an alpha1-4-galactosyltransferase Registry number: EC 2.4.1.- Synonym: udpgal-galactosyl-beta-1-4-glucosylceramide alpha1-4-galactosyltransferase, globotriaosylceramide synthase, udp-glcg-transferase, udp galactose lactosylceramide alpha-galactosyltransferase, udp-gal lcgtase, udp-gal-galactose alpha(1,4)-galactosyltransferase, alpha1,4galt (26 Jun 1999) |
| UDP-galactose-lactosylceramide beta 1-3-galactosyltransferase | <enzyme> Catalyses transfer of galactose from udp-galactose to lactose or lactosylceramide Registry number: EC 2.4.1.- Synonym: udp-galactose-lactose beta 1-3 galactosyltransferase, udp-galactose-lactose (lactosylceramide) beta-3-galactosyltransferase, udpgal-lac-3-transferase (26 Jun 1999) |