| ICF(M)A | International Cystic Fibrosis (Mucoviscidosis) Association |
|---|---|
| IPF | Idiopathic Pulmonary Fibrosis |
| PMF | Progressive Massive Fibrosis = Silicosis |
| CHF | chick embryo fibroblast; chronic heart failure; congenital hepatic fibrosis; congestive heart failur... |
| CIPF | classic interstitial pneumonitis-fibrosis; clinical illness promoting factor |
| diffuse interstitial pulmonary fibrosis | This represents a group of pulmonary disorders (lower respiratory tract) that leads to a functional loss in the alveolar air sacs and a compromise in the diffusion of oxygen from air to blood. There is widespread inflammation and scar tissue (fibrosis) formation within the lung. The causes are varied and include: inorganic and organic dusts, gases, fumes, vapors, infections, radiation, medications, coal dust, silicosis and byssinosis. When the cause is not identifiable it is referred to as idiopathic diffuse interstitial pulmonary fibrosis (27 Sep 1997) |
|---|---|
| idiopathic interstitial fibrosis | A progressive inflammatory condition starting with diffuse alveolar damage and resulting in fibrosis and honeycombing over a variable time period; also a common feature of collagen-vascular diseases. Synonym: fibrosing alveolitis, Hamman-Rich syndrome, idiopathic interstitial fibrosis. (05 Mar 2000) |
| idiopathic pulmonary fibrosis | <radiology> Aka: usual interstitial pneumonia (UIP), 5-6th decade; M:F = 1:1, clubbing of fingers (83%), lymphocytosis on lavage, increased occurence of bronchogenic CA, average survival of 4-6 years; 87% mortality CXR findings: occasional ground glass pattern in early stage of alveolitis, diffuse reticulations (60%) predominantly at bases, honeycombing, pleural effusion (4%); pleural thickening (6%), pneumothorax in 7% (late stage), progressive volume loss see: interstitial pulmonary fibrosis (12 Dec 1998) |
| interstitial pulmonary fibrosis | <radiology> Idiopathic, idiopathic pulmonary fibrosis (AKA: usual interstitial pneumonitis), Hamman-Rich syndrome (rapidly progressive), drug-related, collagen-vascular disease, rheumatoid lung disease, scleroderma (12 Dec 1998) |
| oral submucous fibrosis | A precancerous condition of the oral mucosa and upper aerodigestive tract characteristically in a native of India. (05 Mar 2000) |
| endocardial fibrosis | Scarring or collaginosis of the endocardium. Synonym: endocardial sclerosis. (05 Mar 2000) |
| endomyocardial fibrosis | A disease characterised by thickening of the endocardium, and frequently the inner third of the myocardium. The left ventricle is most frequently involved. Cardiomegaly and congestive heart failure may also be present. (12 Dec 1998) |
| fibrosis | The formation of fibrous tissue, fibroid or fibrous degeneration (18 Nov 1997) |
| leptomeningeal fibrosis | A fibrous reaction within the subarachnoid space; sometimes a sequel to infectious or chemical meningitis. See: adhesive arachnoiditis. (05 Mar 2000) |
| adenoid cystic carcinoma | <tumour> A histologic type of carcinoma characterised by large epithelial masses containing round, glandlike spaces or cysts which frequently contain mucus or collagen and are bordered by a few or many layers of epithelial cells without intervening stroma, forming a cribriform pattern like a slice of Swiss cheese; perineural invasion and haematogenous metastasis are common; occurs most commonly in salivary glands. Synonym: cylindromatous carcinoma. (05 Mar 2000) |
| carcinoma, adenoid cystic | Carcinoma characterised by bands or cylinders of hyalinised or mucinous stroma separating or surrounded by nests or cords of small epithelial cells. When the cylinders occur within masses of epithelial cells, they give the tissue a perforated, sievelike, or cribriform appearance. Such tumours occur in the mammary glands, the mucous glands of the upper and lower respiratory tract, and the salivary glands. They are malignant but slow-growing, and tend to spread locally via the nerves. (12 Dec 1998) |
| pancreatic cystic neoplasms | <radiology> Microcystic adenoma, glycogen, benign, mucinous cystic neoplasm, macrocystic adenoma, cystadenoma/cystadenocarcinoma, mucin, pre-malignant, Both occur more commonly in women, peak in middle age (12 Dec 1998) |
| papillary cystic adenoma | <tumour> An adenoma in which the lumens of the acini are frequently distended by fluid, and the neoplastic epithelial elements tend to form irregular, fingerlike projections. (05 Mar 2000) |
| medullary cystic disease | <disease> A rare hereditary kidney disease characterised by the gradual loss of kidney function due to the presence of cysts in the renal medulla. Symptoms include high urine output (cannot concentrate the urine), weakness, weight loss, nocturia, fatigue and headache. There is no cure and usually progresses from chronic renal failure to end stage renal disease. (27 Sep 1997) |
| medullary cystic kidney disease | <radiology> Mode of inheritance uncertain, usually affects young adults (early 20s), associated with red or blond hair (!!), causes salt wasting, polyuria, azotaemia, affects both kidneys, with progressive disease patients need dialysis or transplant (12 Dec 1998) |