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¿µ¹® immune system ÇÑ±Û ¸é¿ªÃ¼°è
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¿µ¹® urinary system ÇÑ±Û ºñ´¢±â°èÅë
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  ºñ´¢±â°èÅëÀ̶óÇϸé ÄáÆÏÀ¸·ÎºÎÅÍ ½ÃÀÛÇØ¼­ ¿ä°ü, ¹æ±¤, ¿äµµ¿¡ À̸£´Â ÀÏ·ÃÀÇ ¿ÀÁÜ»ý¼º ¹× ÀúÀå, ¹è¼³±â°üÀ» ÀÏÄ´´Ù. ÄáÆÏÀº ±æÀÌ ¾à 2.5cm, Æø ¾à 5.1cm, µÎ²² ¾à 2.5cm, ¹«°Ô ¾à 120~160gmÀ¸·Î¼­, ³»Ãø¿¡ ÄáÆÏ¹®ÀÌ ÀÖ¾î Ç÷°ü, ½Å°æ, ¿ä°üÀÌ ÃâÀÔÇϰí ÀÖ´Ù. ÄáÆÏÀº ¼ÓÁú°ú °ÑÁú·Î ÀÌ·ç¾îÁ® ÀÖÀ¸¸ç ¼öÁúÀº 10~15°³ÀÇ Ãßü(¿ÀÁÜÀ» ¸ðÀ¸´Â ¿ªÇÒ)¸¦ Çü¼ºÇ졒ʡÑÁúÀº ¾à 100¸¸°³ÀÇ ÄáÆÏ´ÜÀ§À¸·Î ±¸¼ºµÇ¾î ÀÖ´Ù. ¿ä¼¼°üÀº Å丮ÂÊ´¢¼¼°ü, Çî·¹°í¸®, ¸ÕÂÊ´¢¼¼°ü, ÁýÇÕ°üÀ¸·Î Çü¼ºµÇ¾î ÀÖÀ¸¸ç, Ãßü¿Í ¼úÀÜ, ±ò¶§±â¸¦ °ÅÃÄ ¿ä°üÀ¸·Î ¿¬°áµÈ´Ù.
  
  ÄáÆÏÀº Ç÷¾×À» ¿©°úÇÏ¿© ½Åü ½ÅÁø´ë»çÀÇ ÃÖÁ¾»ê¹°À» ¿ÀÁÜÀÇ ÇüÅ·Π¹è¼³Çϸç, ¼¼Æ÷¿Ü¾×(extracellular fluid)ÀÇ ÀüÇØÁú³óµµ¸¦ Á¶ÀýÇÑ´Ù. ÄáÆÏ¿¡¼­ Çü¼ºµÈ ¿ÀÁܴ ¿ä°üÀ» °ÅÃÄ ¹æ±¤¿¡¼­ ÀúÀåµÇ°í ÀÖ´Ù°¡ Àû´çÇÑ ½Ã±â°¡ µÇ¸é ¿äµµ¸¦ ÅëÇØ ¿Ü°è·Î ¹èÃâµÈ´Ù.
¿µ¹® reproductive system ÇÑ±Û »ý½Ä±â°èÅë
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  1.³²¼º»ý½Ä°èÅë: ³²¼º»ý½Ä±â´Â Á¤ÀÚ(sperm)¸¦ »ý¼ºÇϴ °íȯ°ú Á¤ÀÚÀÇ ¼º¼÷, ¿î¹Ý, ±×¸®°í »çÁ¤¿¡ °ü¿©Çϴ ºÎ°íȯ, Á¤°ü, À½°æ(penis) µîÀ¸·Î ÀÌ·ç¾îÁ® ÀÖÀ¸¸ç, ºÎ¼Ó±â°üÀ¸·Î ¿ÜºÐºñ»ùÀΠÁ¤³¶(seminal vesicle), Àü¸³»ù(prostate), ¿äµµ¸Á¹°»ù(bulbourethral gland, Cowper¡¯s gland) µîÀ» °®Ãß°í ÀÖ´Ù. °íȯÀº Á¤ÀÚ¸¦ »ý»êÇϴ »ý½Ä»ùÀΠµ¿½Ã¿¡ ³²¼ºÈ£¸£¸ó(testosterone)À» ºÐºñÇϴ ³»ºÐºñ»ùÀÌ´Ù. °íȯ¿¡¼­ ºÐºñµÇ´Â ³²¼ºÈ£¸£¸óÀº Á¤ÀÚ»ý¼º°ú »ý½Ä±âÀÇ ¹ß´Þ ¹× À¯Áö¿¡ ÇʼöÀûÀΠ¿ªÇÒÀ» ÇϹǷΠ³²¼º»ý½Ä±â´ÉÀÇ ¿øÃµÀº °íȯ¿¡ ÀÖ´Ù°í º¼ ¼ö ÀÖ´Ù.
  
  2.¿©¼º»ý½Ä°èÅë: ¿©¼º»ý½Ä±â´Â ³­ÀÚ¸¦ »ý¼ºÇϴ ³­¼Ò¿Í ³­ÀÚ¸¦ ÀÚ±ÃÀ¸·Î ¿î¹ÝÇϴ ³­°ü, ±×¸®°í Àڱðú Áú·Î ÀÌ·ç¾îÁ® ÀÖÀ¸¸ç ¿ÜºÐºñ¼±ÀΠ¹Ù¸£Å縰»ù¸¦ °®Ãß°í ÀÖ´Ù. ³­¼Ò´Â ³­ÀÚ¸¦ »ý¼ºÇϴ »ý½Ä»ùÀΠµ¿½Ã¿¡ ¿©¼ºÈ£¸£¸óÀ» ºÐºñÄÉÇϴ ³»ºÐºñ»ùÀÌ´Ù. ¿ù°æÁÖ±â Àü¹ÝºÎ¿¡ ³­ÀÚ¸¦ »ý¼º½Ã۱âÀ§ÇØ ¼º¼÷µÇ°í Àִ ³­Æ÷¿¡¼­ ºÐºñµÇ´Â ¿¡½ºÆ®·Î°ÕÀº ¿©¼º 2Â÷ ¼ºÂ¡ÀÇ ¹ß´ÞÀ» °üÀåÇÒ »Ó ¾Æ´Ï¶ó Àڱ󻸷À» ÀåÂ÷ ¼öÁ¤µÉ ¼öÁ¤¶õÀÌ Âø»óÇϱ⿡ ¾Ë¸ÂÀº »óÅ·Π¸¸µé¾îÁØ´Ù. ³­ÀÚ°¡ ºÐºñµÇ°í ³²Àº È²Ã¼¿¡¼­ ºÐºñµÇ´Â Çª·Î°Ô½ºÅ×·ÐÀº Àڱ󻸷À» º×µµ·Ï Çϸ頺кñ¾×À» Áõ°¡½Ã۸ç ÀڱñÙÀÇ ¼öÃàÀ» ¹æÇØÇÏ¿© ÀӽŽàÀÓ½ÅÀ» Áö¼Ó½Ã۴ ¿ªÇÒÀ» ÇÑ´Ù.
¿µ¹® digestive system ÇÑ±Û ¼ÒÈ­±â°èÅë
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  ¸ÔÀº À½½ÄÀÇ ºÐÇØ, ¼ÒÈ­, Èí¼ö¿¡ °ü°èµÈ Àå±â¸¦ ÅëÄªÇØ¼­ ºÎ¸£´Â ¸».
¿µ¹® nervous system ÇÑ±Û ½Å°æ°è
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  ¿©·¯ ±â°üµéÀÇ ¼­·Î°£ »óÈ£¿¬°áü°è°¡ ¹Ù·Î ½Å°æ°èÀÌ´Ù. ¿©±â¿¡´Â ÁßÃ߽Űæ°è(central nerve system: CNS)¿Í ¸»ÃʽŰæ°è(peripheral nerve system: PNS)°¡ Àִµ¥, ÁßÃ߽Űæ°è¶õ ³ú¿Í Ã´¼ö¸¦ ¸»ÇÑ´Ù. ±×¸®°í ¸»ÃʽŰæ°è¿¡´Â 12½ÖÀÇ ³ú½Å°æ(cranial nerve: ³ú¿¡¼­ ±â½ÃÇÏ¿© ÁַΠ¾ó±¼ºÎÀ§¿Í ¸ñ ºÎÀ§¿¡ ºÐÆ÷ÇÑ´Ù)°ú 31½ÖÀǠô¼ö½Å°æ(spinal nerve:spinal cord¿¡¼­ °¢±â ¾çÂÊÀ¸·Î ½ÖÀ» ÀÌ·ç¾î ³ª¿À´Âµ¥ ÁַΠ¸ñÀÌÇϺÎÀ§ÀÇ ½Åü °¢ºÎºÐÀ¸·Î ºÐÆ÷ÇϰԠµÈ´Ù)À¸·Î ±¸¼ºµÇ¾î ÀÖ´Ù.
  
  ¶ÇÇÑ ¸»ÃʽŰæ°è´Â 3°¡ÁöÀÇ ½Å°æÁ¶Á÷µé·Î ±¸¼ºµÇ¾î Àִµ¥ ¾Õ¿¡¼­ ¸»ÇÑ ³ú½Å°æ°ú Ã´¼ö½Å°æ¿Ü¿¡ ÀÚÀ²½Å°æ°è°¡ ¿©±â¿¡ ÇØ´çµÈ´Ù. ÀÚÀ²½Å°æ°è´Â ´Ù½Ã ±³°¨½Å°æ°ú ºÎ±³°¨½Å°æÀ¸·Î ³ª´µ¾îÁ® ¼­·Î°£ÀÇ ¿Ã¹Ù¸¥ »óÈ£ÀÛ¿ëÀ¸·Î »ýü ¿©·¯ °¡Áö ÀÛ¿ëÀ» ¼öÇàÇÑ´Ù.
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  • ¿µ¹®
    ÇѱÛ
  • buffer system
    ¿ÏÃæ°è
  • circuit system
    ¼øÈ¯½Äȸ·Î
  • circulatory system
    ¼øÈ¯°èÅë, ¼øÈ¯°è
  • closed drainage system
    ´ÝÈû¹èÃâÀåÄ¡
  • clotting system
    ÀÀ°í°èÅë
  • collecting system
    ÁýÇÕ°è
  • combined system disease
    º¹ÇÕ°èÅ뺴
  • complement system
    º¸Ã¼°è, µµ¿òü°èÅë
  • conduction system
    Àüµµ°è
  • control system
    Á¦¾îÀåÄ¡
  • countercurrent system
    ¿ª·ù°è
  • culture system
    ¹è¾ç½Ã½ºÅÛ
  • cytochrome P-450 system
    ½ÃÅäÅ©·ÒP-450½Ã½ºÅÛ
  • cardiovascular system
    ½ÉÀåÇ÷°ü°èÅë, ½ÉÇ÷°ü°è
  • case payment system
    Æ÷°ý¼ö°¡Á¦
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 3
  • ¿µ¹®
    ÇѱÛ
  • venous blood
    Á¤¸ÆÇ÷¾×, Á¤¸ÆÇÇ
  • whole blood
    ÀüÇ÷, ¿ÂÇ÷¾×
  • blood concentration
    Ç÷Áß³óµµ
  • blood collection
    äÇ÷
  • blood cell
    Ç÷¾×¼¼Æ÷, Ç÷±¸
  • blood count
    Ç÷±¸°è»ê
  • complete blood count
    ¿ÂÇ÷±¸°è»ê, ÀüüÇ÷±¸°è»ê
  • packed red blood cell
    ³óÃàÀûÇ÷±¸
  • red blood cell
    ÀûÇ÷±¸
  • red blood corpuscle
    ÀûÇ÷±¸
  • white blood corpuscle
    ¹éÇ÷±¸
  • blood donor
    ÇåÇ÷ÀÚ, °øÇ÷ÀÚ
  • blood donation
    ÇåÇ÷
  • blood film examination
    Ç÷¾×Æì¹Ù¸¥°Ë»ç, Ç÷¾×µµ¸»°Ë»ç
  • blood film
    Ç÷¾×Æì¹Ù¸¥Ç¥º», Ç÷¾×µµ¸»
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 3
  • ¿µ¹®
    ÇѱÛ
  • array system
    ¹è¿­ÀåÄ¡, ¹è¿­Ã¼°è
  • auditory system
    û°¢°èÅë
  • autonomic nervous system
    ÀÚÀ²½Å°æ°èÅë
  • system analysis
    °èÅëºÐ¼®
  • biliary system
    ´ãµµ°è, ¾µ°³°èÅë
  • bioenergetic system
    »ý¹°¿¡³ÊÁö°è
  • breathing system
    È£ÈíÀåÄ¡
  • buffer system
    ¿ÏÃæ°è
  • capitation system
    ȯÀÚµî·ÏÁ¦
  • cardiovascular system
    ½ÉÀåÇ÷°ü°èÅë
  • case payment system
    Æ÷°ý¼ö°¡Á¦
  • central nervous system
    ÁßÃ߽Űæ°èÅë
  • central piping system
    Áß¾Ó¹è°ü½Ã¼³
  • chemoreception system
    È­Çмö¿ë°è
  • circle absorption system
    ¼øÈ¯Èí¼ö½Äȸ·Î
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  • ¿µ¹®
    ÇѱÛ
  • glucose effect
    Æ÷µµ´çÈ¿°ú
  • glucose equivalent
    ±Û·çÄÚ¿À½º´ç·®.
  • glucose fermenter
    Æ÷µµ´ç¹ßÈ¿¼Ò
  • glucose fluctuation
    Æ÷µµ´çº¯µ¿
  • glucose insulin tolerance test =GITT
    Æ÷µµ´çÀν¶¸°ºÎÇϽÃÇè.
  • glucose intolerance
    Æ÷µµ´ç ºÒ³»¼º
  • glucose lactate cycle
    ±Û·çÄÚ¿À½º¶ôÆ®»ê ȸ·Î.
  • glucose level
    Æ÷µµ´çÄ¡<--ÁØÀ§>
  • glucose measurement
    Æ÷µµ´çÃøÁ¤
  • glucose monitoring
    Æ÷µµ´ç°¨½Ã
  • glucose oxidase
    Æ÷µµ´ç»êÈ­È¿¼Ò
  • glucose oxidase =GOD
    ±Û·çÄÚ¿À½º »êÈ­È¿¼Ò(¡­ß«ûùý£áÈ), ±Û·çÄÚ¿À½º¿Á½Ã ´ÙÁ¦.
  • glucose oxidizer
    Æ÷µµ´ç»êÈ­Á¦
  • glucose oxydase test
    Æ÷µµ´ç»êÈ­È¿¼Ò¹ý.
  • glucose oxydation fermentation test
    Æ÷µµ´ç»êÈ­¹ßÈ¿½ÃÇè.
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 3
  • ¿µ¹®
    ÇѱÛ
  • glucose equivalent
    ±Û·çÄÚ¿À½º´ç·®.
  • glucose fermenter
    Æ÷µµ´ç¹ßÈ¿¼Ò
  • glucose fluctuation
    Æ÷µµ´çº¯µ¿
  • glucose insulin tolerance test =GITT
    Æ÷µµ´çÀν¶¸°ºÎÇϽÃÇè.
  • glucose intolerance
    Æ÷µµ´ç ºÒ³»¼º
  • glucose lactate cycle
    ±Û·çÄÚ¿À½º¶ôÆ®»ê ȸ·Î.
  • glucose level
    Æ÷µµ´çÄ¡<--ÁØÀ§>
  • glucose measurement
    Æ÷µµ´çÃøÁ¤
  • glucose monitoring
    Æ÷µµ´ç°¨½Ã
  • glucose oxidase
    Æ÷µµ´ç»êÈ­È¿¼Ò
  • glucose oxidase =GOD
    ±Û·çÄÚ¿À½º »êÈ­È¿¼Ò(¡­ß«ûùý£áÈ), ±Û·çÄÚ¿À½º¿Á½Ã ´ÙÁ¦.
  • glucose oxidizer
    Æ÷µµ´ç»êÈ­Á¦
  • glucose oxydase test
    Æ÷µµ´ç»êÈ­È¿¼Ò¹ý.
  • glucose oxydation fermentation test
    Æ÷µµ´ç»êÈ­¹ßÈ¿½ÃÇè.
  • glucose storage disease
    ´çÃàÀûÁúȯ.
´ëÇÑ»ýÈ­ÇкÐÀÚ»ý¹°ÇÐȸ ¿ë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 3
  • ¿µ¹®
    ÇѱÛ
  • UDP-glucose
    UDP-±Û·çÄÚ½º
  • uridine diphosphate glucose
    À¯¸®µò ÀÌÀλê(ì£×òß«) ±Û·çÄÚ½º
  • absorption optical system
    Èí¼ö(ýåâ¥) ±¤ÇÐ(ÎÃùÊ) ½Ã½ºÅÛ
  • adiabatic system
    ´Ü¿­(Ó¨æð)½Ã½ºÅÛ
  • ATP regeneration system
    ATPÀç»ý(î¢ßæ) ½Ã½ºÅÛ
  • binding protein transport system
    °áÇÕ ´Ü¹éÁú ¼ö¼Û(Ì¿ùêÓ±ÛÜòõâÃáê) ½Ã½ºÅÛ
  • brain barrier system
    ³úÀ庮(Òàî¡Ûú) ½Ã½ºÅÛ
  • cell-free amino acid incorporating system
    ¹«¼¼Æ÷(Ùíá¬øà) ¾Æ¹Ì³ë»ê ÆíÀÔ(øºìý)¾¾½ºÅÛ
  • cell-free system
    ¹«¼¼Æ÷(Ùíá¬øà)½Ã½ºÅÛ
  • charge relay system
    ÀüÇÏ(ï³ùÃ) ¸±·¹ÀÌ ½Ã½ºÅÛ
  • charge transfer relay system
    ÀüÇÏÀ̵¿(ï³ùÃì¹ÔÑ) ¸±·¹ÀÌ ¾¾½ºÅÛ
  • closed circuit system
    Æó¼âȸ·Î(øÍáðüÞÖØ) ½Ã½ºÅÛ
  • closed system
    ´ÝÈù ½Ã½ºÅÛ
  • cyclophorase system
    »çÀÌŬ·ÎÆ÷·¹À̽º ½Ã½ºÅÛ
  • digestive system
    ¼ÒÈ­(á¼ûù)½Ã½ºÅÛ
KI ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 3
  • ¿µ¹®
    ÇѱÛ
  • blood cell
    Ç÷±¸
  • blood concentration
    Ç÷Áõ³óµµ
  • blood disorder
    Ç÷¾×Áúȯ
  • blood flow
    Ç÷·ù·®
  • blood gas
    Ç÷¾×°¡½º
  • blood oxygenation level dependant [=BOLD]
    Ç÷Áß»ê¼ÒÄ¡ÀÇÁ¸
  • blood oxygenation level dependant contrast
    Ç÷Áß»ê¼ÒÄ¡ÀÇÁ¸´ëÁ¶µµ
  • blood pool scan
    Ç÷¾×Àú·ùÁÖ»ç
  • blood stained
    ÇǼ¯ÀÎ, Çǹ¯Àº
  • blood stream
    Ç÷·ù
  • blood sugar
    Ç÷´ç
  • blood supply
    Ç÷¾×°ø±Þ
  • blood vessel
    Ç÷°ü, ÇÍÁÙ
  • blood volume
    Ç÷¾×¾ç
  • BOLD [=blood oxygenation level dependent]
    Ç÷Áß»ê¼ÒÄ¡ÀÇÁ¸
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 3
ECG Electro-Cardio-Graphy(-Gram); ½ÉÀüµµ
   = EKG
  1. Conducting System Structu...
GA Gamblers Anonymous; gastric analysis; gastric antrum; general anesthesia; general angiography; gener...
HGO hepatic glucose output; human glucose output
BLS bare lymphocyte syndrome; basic life support; blind loop syndrome; blood and lymphatic system; blood...
MN a blood group in the MNSs blood group system; malignant nephrosclerosis; Master of Nursing; meganewt...
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 3
HBGM Home Blood Glucose Monitoring
MBG Mean blood glucose
SMBG Self-monitoring of blood glucose
CBG capillary blood glucose
AMS AUTO-MICROBIC-SYSTEM
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 3
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • blood compatibility testing
    Ç÷¾× ÀûÇÕ¼º °Ë»ç
  • blood concentration
    Ç÷Áß ³óµµ
  • blood count
    Ç÷±¸°è»ê
    ÀÏÁ¤ÀÇ Ç÷¾×·® 1§§Áß À¯Çü ¼ººÐ¼öÀÇ ÃøÁ¤.
  • blood culture
    Ç÷¾× ¹è¾ç
  • blood disease
    Ç÷¾× ÀÌ»ó
    µ¿ÀǾî=hemic disease.
  • blood disorder
    Ç÷¾× Áúȯ
  • blood donation
    °øÇ÷
  • blood dust
    ÇǸÕÁö
  • blood examination
    Ç÷¾× °Ë»ç, Ç÷¾× °Ë»ç¹ý
  • blood factor
    Ç÷¾× ÀÎÀÚ
  • blood film preparation
    Ç÷¾× Çʸ§ Á¦ÀÛ
  • blood flow pattern
    Ç÷·ù ¾ç»ó
  • blood flow velocity
    Ç÷·ù ¼Óµµ
  • blood formation
    Ç÷¾× Çü¼º
  • blood gas
    Ç÷¾× °¡½º
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 3
glucose-1-phosphate adenylyltransferase <enzyme> Shrunken-2 (sh2) protein is a subunit of this enzyme
Registry number: EC 2.7.7.27
Synonym: adpg synthetase, adpglucose pyrophosphorylase, ADP-glucose synthetase, shrunken-2 protein, shrunken gene product, ADP-glucose pyrophosphorylase, glgc gene product, bt2 gene product, brittle-2 gene product
(26 Jun 1999)
glucose-1-phosphate kinase <enzyme> An enzyme that, in the presence of ATP, catalyses the phosphorylation of d-glucose 1-phosphate to form d-glucose 1,6-bisphosphate and ADP; found in yeast and muscle; d-glucose 1,6-bisphosphate is a required cofactor of one of the enzymes in glycogenolysis.
Synonym: glucose-1-phosphate kinase.
(05 Mar 2000)
glucose-1-phosphate phosphodismutase A phosphotransferase catalyzing the reversible transfer of a phosphate residue from one d-glucose 1-phosphate to another, yielding d-glucose 1,6-bisphosphate and d-glucose. This enzyme provides a crucial intermediate needed for glucose-phosphate isomerase.
(05 Mar 2000)
glucose-1-phosphate uridylyltransferase <enzyme> An enzyme that activates d-glucose by reacting d-glucose 1-phosphate with UTP, producing pyrophosphate and UDP glucose; a crucial step in glycogen biosynthesis.
(05 Mar 2000)
glucose-1-phospho-D-mannosylglycoprotein phosphodiesterase <enzyme> Removes the glucose-1-phosphate from glc-alpha-1-p-6-mannose residues in glycoproteins as a unit; pH optimum 7.5
Registry number: EC 3.1.4.51
Synonym: ag1p phosphodiesterase, alpha-glucose-1-phosphate phosphodiesterase
(26 Jun 1999)
glucose-3-phosphatase <enzyme> From rat liver; has glucose-3-phosphate hydrolytic activity
Registry number: EC 3.1.3.-
(26 Jun 1999)
glucose-6-dehydrogenase deficiency <biochemistry> An inherited condition that results in a deficiency in glucose-6-phosphate dehydrogenase. Particular drugs (sulphonamides) can exacerbate this problem. The result is haemolytic anaemia.
(27 Sep 1997)
glucose-6-phosphatase <enzyme> An enzyme that catalyses the conversion of d-glucose-6-phosphate and water to d-glucose and orthophosphate. This enzyme is deficient in glycogen storage disease Ia.
Chemical name: D-Glucose-6-phosphate phosphohydrolase
Registry number: EC 3.1.3.9
(12 Dec 1998)
glucose-6-phosphatase hepatorenal glycogenosis Glycogenosis due to glucose-6-phosphatase deficiency, resulting in accumulation of excessive amounts of glycogen of normal chemical structure, particularly in liver and kidney.
Synonym: Gierke's disease, glucose-6-phosphatase hepatorenal glycogenosis, von Gierke's disease.
(05 Mar 2000)
glucose-6-phosphate <biochemistry> Glucose 6-phosphate is a phosphomonoester of glucose that is formed by transfer of phosphate from ATP, catalysed by the enzyme hexokinase.
It is an intermediate both of the glycolytic pathway (next converted to fructose 6 phosphate) and of the NADPH generating pentose phosphate pathway, formed from glucose via hexokinase. However it is not strictly a glycolytic intermediate and it is readily converted to glycogen or oxidized to NADPH.
(10 Oct 1997)
glucose-6-phosphate dehydrogenase <enzyme> An NADP+ enzyme that catalyses the dehydrogenation (oxidation) of d-glucose-6-phosphate to 6-phospho-d-glucono-d-lactone, this reaction initiating the Dickens shunt.
Deficiency of this enzyme is the commonest disease-causing enzyme defect in humans affecting an estimated 400 million people.
The gene for this enzyme is on the X chromosome. Males with the enzyme deficiency develop haemolytic anaemia when red blood cells are exposed to oxidant drugs such as the antimalarial primaquine, the sulfonamide antibiotics or sulfones, naphthalene moth balls, or fava beans.
Synonym: Robison ester dehydrogenase, Zwischenferment.
Acronym: G6PD
(12 Sep 2002)
glucose-6-phosphate dehydrogenase deficiency A deficiency of glucose-6-phosphate dehydrogenase, an enzyme important for maintaining cellular concentrations of reduced nucleotides.
Deficiency of this enzyme is the commonest disease-causing enzyme defect in humans affecting an estimated 400 million people.
The gene for this enzyme is on the X chromosome and there are various polymorphic forms.
Males with the enzyme deficiency develop haemolytic anaemia when red blood cells are exposed to oxidant drugs such as the antimalarial primaquine, the sulfonamide antibiotics or sulfones, naphthalene moth balls, or fava beans. It can also cause anaemia of the newborn, and chronic nonspherocytic haemolytic anaemia.
Inheritance: X-linked.
(12 Sep 2002)
glucose-6-phosphate isomerase <enzyme> An enzyme that catalyses the reversible interconversion of glucose-6-phosphate and fructose-6-phosphate, and is a part of the glycolytic and gluconeogenic pathways. Deficiency of the enzyme, an autosomal recessive trait, results in liver glycogenesis and haemolytic anaemia.
Chemical name: D-Glucose-6-phosphate ketol-isomerase
Registry number: EC 5.3.1.9
(12 Dec 1998)
glucose-6-phosphate translocase <enzyme> A component of EC 3.1.3.9 which transports glucose phosphate into endoplasmic reticulum
Registry number: EC 2.7.-
Synonym: t1 transport protein
(26 Jun 1999)
glucose clamp technique <technique> Maintenance of a constant blood glucose level by perfusion or infusion with glucose or insulin. It is used for the study of metabolic rates (e.g., in glucose, lipid, amino acid metabolism) at constant glucose concentration.
(12 Dec 1998)
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