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tyrosine-repressible transaminase <enzyme> From E coli; catalyses the amination of 2-ketoisocaproate to leucine; encoded by tyrb; a functional leuabcd operon is required for leucine synthesis by this enzyme
Registry number: EC 2.6.1.-
Synonym: transaminase d, tyrosine-2-ketoisocaproate aminotransferase
(26 Jun 1999)
tyrosine-trna ligase <enzyme> An enzyme that activates tyrosine with its specific transfer RNA.
Chemical name: L-Tyrosine:tRNA-(Tyr) ligase (AMP-forming)
Registry number: EC 6.1.1.1
(12 Dec 1998)
tyrosinosis A very rare, possibly heritable disorder of tyrosine metabolism that may be caused by defective formation of p-hydroxyphenylpyruvic acid oxidase or of tyrosine transaminase; characterised by enhanced urinary excretion of p-hydroxyphenylpyruvic acid and of other tyrosyl metabolites upon ingestion of tyrosine or proteins containing that amino acid.
Origin: tyrosine + G. -osis, condition
(05 Mar 2000)
tyrosinuria The excretion of tyrosine in the urine.
Origin: tyrosine + G. Ouron, urine
(05 Mar 2000)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 2 ÆäÀÌÁö: 2
  • Tyrosine-tRNA Ligase - »õâ An enzyme that activates tyrosine with its specific transfer RNA. EC 6.1.1.1.
    Synonyms : Tyr-tRNA Ligase, Tyrosyl-tRNA Synthetase, Ligase, Tyr-tRNA, Ligase, Tyrosine-tRNA, Synthetase, Tyrosyl-tRNA, Tyr tRNA Ligase, Tyrosine tRNA Ligase, Tyrosyl tRNA Synthetase
  • Tyrosinemias - »õâ A group of disorders which have in common elevations of tyrosine in the blood and urine secondary to an enzyme deficiency. Type I tyrosinemia features episodic weakness, self-mutilation, hepatic necrosis, renal tubular injury, and seizures and is caused by a deficiency of the enzyme fumarylacetoacetase. Type II tyrosinemia features mental retardation, painful corneal ulcers, and keratoses of the palms and plantar surfaces and is caused by a deficiency of the enzyme TYROSINE TRANSAMINASE. Type III tyrosinemia features mental retardation and is caused by a deficiency of the enzyme 4-HYDROXYPHENYLPYRUVATE DIOXYGENASE. (Menkes, Textbook of Child Neurology, 5th ed, pp42-3)
    Synonyms : 4-Hydroxyphenol Pyruvic Acid Oxidase Deficiency Disease, Deficiency Disease, 4-Hydroxyphenol Pyruvic Acid Oxidase, Deficiency Disease, Fumarylacetoacetase, Deficiency Disease, Tyrosine Transaminase, Hereditary Tyrosinemia, Type I, Hypertyrosinemia, Type I
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tyrosine b -(r -Hydroxyphyl) adanine ? C 9 H 11 NO 3 an amino acid widely distributed in proteins; a precursor of epinephrine, thyroxine and melanin
Ãâó: members.ozemail.com.au/~lindafrd/page20.html
tyrosine A variety of tiny wild grass found in parts of Central and South America that is believed to be the ancestor of modern day corn.
Ãâó: www.natureshift.org/Whawk/glossaryT-Z.html
tyrosine A nonessential amino acid used to manufacture adrenal and thyroid hormones, and converted into the skin pigment melanin.
Ãâó: www.enzy.com/glossary/searchresults.asp
tyrosine A nonessential amino acid but may be essential for individuals with certain diseases or nutritional concerns. May be important for neurotransmitter synthesis and mood regulation. May be useful for depression, allergies and addictive states.
Ãâó: www.criticalbench.com/supplementinfo.htm
tyrosinase-negative (ty-neg) oculocutaneous a. a recessive disorder characterized by absence of pigment in hair, skin, and eyes. Signs include white hair throughout life, skin that is pink and highly susceptible to neoplasias, absence of pigmented nevi or freckles, gray to blue eyes, prominent red reflexes from the fundi, severe nystagmus, photophobia, and reduced visual acuity (most patients are legally blind). Called also albinism, a. I, and complete perfect a.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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