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"steroid sulfatase deficiency"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
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  • ¿µ¹®
    ÇѱÛ
  • biotin deficiency syndrome
    ºñ¿Àƾ°áÇÌÁõÈıº
  • deficiency
    1. °áÇÌ 2. °áÇÌÁõ
  • deficiency disease
    °áÇ̺´
  • erythropoietin deficiency anemia
    ¿¡¸®Æ®·ÎÆ÷ÀÌ¿¡Æ¾°áÇ̺óÇ÷
  • fat deficiency disease
    Áö¹æ°áÇ̺´
  • folate deficiency anemia
    ¿±»ê°áÇ̺óÇ÷
  • iron deficiency anemia
    ö°áÇ̺óÇ÷
  • immune deficiency
    ¸é¿ª°áÇÌ
  • leukocyte adhesion deficiency
    ¹éÇ÷±¸ºÎÂø°áÇÌ
  • nutritional deficiency disease
    ¿µ¾ç°áÇ̺´
  • nutritional deficiency state
    ¿µ¾ç°áÇÌ»óÅÂ
  • nutritional deficiency syndrome
    ¿µ¾ç°áÇÌÁõÈıº
  • vitamin deficiency
    ºñŸ¹Î°áÇÌ(Áõ)
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
  • adhesion deficiency disorder
    À¯Âø°áÇÌÀå¾Ö
  • antibody deficiency syndrome
    Ç×ü°áÇÌÁõÈıº
  • erythropoietin deficiency anemia
    ¿¡¸®Æ®·ÎÆ÷¿¡Æ¾°áÇ̺óÇ÷
  • folate deficiency anemia
    ¿±»ê°áÇÌ
  • iron deficiency anemia
    ö°áÇ̺óÇ÷
  • ceruloplasmin deficiency
    ¼¼·ê·ÎÇö󽺹ΰáÇÌ
  • complement deficiency
    µµ¿òü°áÇÌ
  • deficiency
    °áÇÌ(Áõ)
  • deficiency disease
    ¿µ¾ç°áÇ̺´
  • fat deficiency disease
    Áö¹æ°áÇÌÁõ
  • functional deficiency
    ±â´É°áÇÌ
  • histogenetic deficiency
    Á¶Á÷¹ß»ý°áÇÌ
  • immune deficiency
    (¢¡immunodeficiency) ¸é¿ª°áÇÌ
  • latent deficiency
    ÀáÀç°áÇÌÁõ
  • leukocyte adhesion deficiency
    ¹éÇ÷±¸ºÎÂø°áÇÌÁõ
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
  • abdominal muscle deficiency syndrome
    º¹±Ù°á¼ÕÁõÈıº(ÜÙÐÉÌÀáßñøý¦ÏØ).
  • acid lipase deficiency
    »ê¼º ¸®ÆÄÁ¦ °áÇÌÁõ(ß«àõ¡­ÌÀù¹ñø)
  • acquired immune deficiency
    ÈÄõ¼º ¸é¿ª°áÇÌ
  • acquired immune deficiency syndrome
    ÈÄõ¼º ¸é¿ª°áÇÌ ÁõÈıº
  • acquired immune deficiency syndrome
    ÈÄõ¼º ¸é¿ª°áÇÌÁõÈıº(ý­ô¸àõ Øóæ¹ÌÀù¹ñøý¦ÏØ)
  • adenosine,deficiency
    °áÇÌÁõ(ÌÀù¹ñø)
  • adrenocortical deficiency
    ºÎ½ÅÇÇÁú°áÇÌÁõ.
  • aids=£¾acquired immune deficiency syndrome
    ÈÄõ¼º¸é¿ª°áÇÌÁõÈıº(ý­ô¸àõØóæ¹ÌÀù¹ñøý¦ÏØ)
  • alimentary deficiency =dietary d.
    ½Ä»çºÎÁ·, ¿µ¾çºÎÁ·.
  • anemia iron deficiency
    ö°áÇ̼º ºóÇ÷.
  • anemia,folate deficiency
    ¿±»ê°áÇÌ(ç¨ß«ÌÀù¹)
  • anterior pituitary deficiency
    ³úÇϼöüÀü¿±±â´ÉºÎÀü(Áõ)
  • anterior pituitary deficiency
    ÇϼöüÀü¿±±â´ÉºÎÀü(Áõ).
  • antibody deficiency syndrome
    Ç×ü°áÇÌÁõÈıº(ù÷ô÷ÌÀù¹ñøý¦ÏØ).
  • antitrypsin deficiency
    Çׯ®¸³½Å°áÇÌ
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  • ¿µ¹®
    ÇѱÛ
  • steroid cataract
    ½ºÅ×·ÎÀ̵å¹é³»Àå
  • steroid folliculitis
    ½ºÅ×·ÎÀÌµå ¸ð³¶¿°
  • steroid glaucoma
    ½ºÅ×·ÎÀ̵å³ì³»Àå
  • steroid hormone
    ½ºÅ×·ÎÀ̵åÈ£¸£¸ó(ºÎ½ÅÇÇÁúÈ£¸£¸ó)((¡­Üùãìù«òõ¡­)
  • steroid myopathy
    ½ºÅ×·ÎÀ̵å±Ùº´Áõ(¡­Ü»ñø)
  • steroid psychosis
    ½ºÅ×·ÎÀ̵å Á¤½ÅÁõ(º´).
  • steroid purpura
    ½ºÅ×·ÎÀ̵å ÀÚ¹Ý
  • steroid rebound phenomenon
    ½ºÅ×·ÎÀÌµå ¹ÝµµÇö»ó(¡­ÚãÔ¯úÞßÚ).
  • steroid-induced atrophy
    ½ºÅ×·ÎÀ̵å À§Ãà
  • steroid-induced disorders
    ½ºÅ×·ÎÀ̵å À¯¹ßÀå¾Ö(º´).
  • steroid-induced glaucoma
    ½ºÅ×·ÎÀ̵å³ì³»Àå
  • steroid-related disorders
    ½ºÅ×·ÎÀÌµå °ü·ÃÀå¾Ö(º´).
  • abdominal muscle deficiency syndrome
    º¹±Ù°á¼ÕÁõÈıº(ÜÙÐÉÌÀáßñøý¦ÏØ).
  • acid lipase deficiency
    »ê¼º ¸®ÆÄÁ¦ °áÇÌÁõ(ß«àõ¡­ÌÀù¹ñø)
  • acquired immune deficiency
    ÈÄõ¼º ¸é¿ª°áÇÌ
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  • ¿µ¹®
    ÇѱÛ
  • Secretion deficiency
    ºÐºñ°áÇÌ
    [¿¾ ¿ë¾î] ºÐºñ°áÇÌ
  • Cytogenetic deficiency
    ¼¼Æ÷¹ß»ý°áÇÌ
    [¿¾ ¿ë¾î] ¼¼Æ÷¹ß»ý°áÇÌ
  • Stimulus deficiency
    ÀڱذáÇÌ
    [¿¾ ¿ë¾î] ÀڱذáÇÌ
  • Histogenetic deficiency
    Á¶Á÷¹ß»ý°áÇÌ
    [¿¾ ¿ë¾î] Á¶Á÷¹ß»ý°áÇÌ
  • Synthesis deficiency
    ÇÕ¼º°áÇÌ
    [¿¾ ¿ë¾î] ÇÕ¼º°áÇÌ
  • Hormone deficiency
    È£¸£¸ó°áÇÌ
    [¿¾ ¿ë¾î] È£¸£¸ó°áÇÌ
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  • ¿µ¹®
    ÇѱÛ
  • cardiotonic steroid
    °­½É(Ë­ãý) ½ºÅ×·ÎÀ̵å
  • catatoxic steroid
    µ¶¼º¹æ¾î(Ô¸àõÛÁåÝ) ½ºÅ×·ÎÀ̵å
  • sex steroid binding plasma protein
    ¼º(àõ)½ºÅ×·ÎÀÌµå °áÇÕ(Ì¿ùê) Ç÷Àå(úìíì) ´Ü¹éÁú(úìíìÓ±ÛÜòõ)
  • steroid
    ½ºÅ×·ÎÀ̵å
  • steroid alkaloids
    ½ºÅ×·ÎÀÌµå ¾ËÄ®·ÎÀ̵å
  • steroid alkaloid saponin
    ½ºÅ×·ÎÀÌµå ¾ËÄ®·ÎÀÌµå »çÆ÷´Ñ
  • steroid conjugate
    ½ºÅ×·ÎÀ̵å Á¢ÇÕü(ïÈùêô÷)
  • steroid diabetes
    ½ºÅ×·ÎÀÌµå ´ç´¢º´(ÓØÒãÜ»)
  • steroid hormone
    ½ºÅ×·ÎÀ̵å È£¸£¸ó
  • steroid number
    ½ºÅ×·ÎÀÌµå ¹øÈ£(ÛãûÜ)
  • steroid receptor
    ½ºÅ×·ÎÀÌµå ¼ö¿ëü (áôé»ô÷)
  • steroid saponin
    ½ºÅ×·ÎÀÌµå »çÆ÷´Ñ
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 2
G6S glucosamine-6-sulfatase
SIDS sudden infant death syndrome; sulfo-iduronate sulfatase
IGD idiopathic growth hormone deficiency; interglobal distance; isolated gonadotropin deficiency
MCD magnetic circular dichroism; mast-cell degranulation; mean cell diameter; mean of consecutive differ...
ACTH Adreno-Cortico-Tropic(=Tropin)(or steroid) Hormone
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 2
3 beta-HSD 3 beta hydroxy steroid dehydrogenase
3 beta-HSD 3 beta-hydroxy-steroid dehydrogenase/delta 5-delta 4 isomerase
AAS Anabolic androgenic steroid
NSAID Non Steroid Anti-Inflammatory Drugs
SBP Steroid Binding Protein
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • ascorbic acid deficiency
    ¾Æ½ºÄÚ¸£ºó»ê °áÇÌÁõ
    Ư¡ÀûÀÎ ±«Ç÷º´ÀÌ ³ªÅ¸³ª¸ç ÀÌÀÇ Áõ»óÀ¸·Î´Â ÀÕ¸öÀÌ º×°í ½±°Ô ÃâÇ÷ÀÌ µÇ°í, Ä¡¾Æ Çü¼º Àå¾Ö Ä¡Á¶°ñ Èí¼ö ÇÇÇÏ ÃâÇ÷ µîÀÌ ÀÖÀ¸¸ç â»ó Ä¡À¯°¡ ´Ê¾îÁø´Ù.
  • cell adhesion molecular deficiency
    ¼¼Æ÷ À¯Âø ºÐÀÚ °áÇÌ
  • cellular deficiency
    ¼¼Æ÷ °áÇÌ
    ¼¼Æ÷°¡ À¯ÀüÀû ȤÀº ÀÚ°¡¸é¿ªÀû ¿äÀÎÀ¸·Î ÀÎÇØ¼­ °áÇÌµÈ °Í.
  • chromosomal deficiency
    ¿°»öü °áÇÌ
  • color deficiency
    »ö °áÇÌ
  • deficiency anemia
    °áÇ̼º ºóÇ÷
    Ç÷»ö¼Ò °áÇÌÀ¸·Î ÀÎÇÑ ºóÇ÷.
  • deficiency symptom
    °áÇÌ Áõ»ó
    ³»ºÐºñ¼±ÀÇ ºÐºñ Àå¾Ö¿¡ ÀÇÇÑ Áõ»ó.
  • diphosphatase deficiency
    µðÆ÷½ºÆÄŸÁ¦ °áÇÌ
  • electrolyte deficiency syndrome
    ÀüÇØÁú °áÇÌ ÁõÈıº
  • erythropoietin deficiency anemia
    ¿¡¸®Æ®·ÎÆ÷¿¡Æ¾ °áÇ̼º ºóÇ÷, ÀûÇ÷±¸ Á¶Ç÷ ÀÎÀÚ °áÇ̼º ºóÇ÷
  • factor deficiency
    ÀÎÀÚ °áÇÌ, Á¦ÀÎÀÚ °áÇÌÁõ
  • factor IX deficiency
    Á¦ 9ÀÎÀÚ °áÇÌÁõ, Á¦9ÀÎÀÚ °áÇÌ
  • factor VII deficiency
    Á¦ 7ÀÎÀÚ °áÇÌÁõ
  • factor VIII deficiency
    Á¦ 8ÀÎÀÚ °áÇÌ
  • factor XI deficiency
    Á¦11ÀÎÀÚ °áÇÌ
    ÀÌ ÀÎÀÚ°¡ ºÎÁ·µÇ¸é Ç÷¿ìº´ C³ª Rosenthal ÁõÈıºÀ¸·Î ºÒ¸®´Â Àü½Å¼º Ç÷¾× ÀÀ°í Àå¾Ö¸¦ ÀÏÀ¸Å°´Âµ¥ °íÀüÀû Ç÷¿ìº´°ú À¯»çÇÏ´Ù.
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
sulfatase 1. Trivial name for enzymes in EC group 3.1.6, the sulfuric ester hydrolases, which catalyze the hydrolysis of sulfuric esters (sulfates) to the corresponding alcohols plus inorganic sulfate; includes aryl-, sterol, glycol-, chondroitin, choline-, cellulose, cerebroside, and chondro-sulfatases.
Synonym: arylsulfatase.
(05 Mar 2000)
disulfoglucosamine-6-sulfatase <enzyme> Acts on various n-substituted glucosamine-6-o-sulfates
Registry number: EC 3.1.6.11
Synonym: disulphoglucosamine-6-sulphatase, glucosamine o,n-disulfate o-sulfohydrolase, glucosamine sulfatase, n-sulfoglucosamine-6-sulfatase
(26 Jun 1999)
iduronate sulfatase <enzyme> An enzyme that specifically cleaves the ester sulfate of iduronic acid, and is required for the desulfation of 2-sulfate iduronate residues in heparan sulfate. It is also required in dermatan sulfate degradation.
Its deficiency has been demonstrated in Hunter's syndrome, which is characterised by an excess of dermatan sulfate and heparan sulfate.
Chemical name: L-Iduronate-2-sulfate 2-sulfohydrolase
Registry number: EC 3.1.6.13
(20 Sep 2002)
oligosaccharide 2-O-sulfatase <enzyme> Hydrolyzes the 2-o-sulfate of the disaccharide 4-deoxy-2-o-sulfato-alpha-l-threo-hex-4-enopyranosyluronic acid-(1-4)-2-deoxy-2-sulfamido-6-o-sulfato-d-glucose from heparin
Registry number: EC 3.1.6.-
Synonym: flavobacterium heparinum 2-o-sulphatase, heparo-2-o-sulfatase
(26 Jun 1999)
oligosaccharyl sulfatase <enzyme> From keyhole limpet; hydrolyzes sulfate esters in asparagine-linked oligosaccharides preferentially to 4-nitrocatechol sulfate
Registry number: EC 3.1.6.-
(26 Jun 1999)
lactate-2-sulfate sulfatase <enzyme> Shows no activity for (l)-isomer
Registry number: EC 3.1.6.-
Synonym: d-lactate-2-sulfate sulfatase, d-lactate-2-sulfatase
(26 Jun 1999)
3b-hydroxysteroid sulfate sulfatase <enzyme> An enzyme, found in most mammalian tissues, that is capable of hydrolyzing the sulfate ester bonds of a variety of sulfated sterols; a deficiency of this enzyme will result in X-linked ichthyosis.
(05 Mar 2000)
anabolic steroid <endocrinology> A type of steroid hormone that stimulates the synthesis of protein. Anabolic steroids are compounds which stimulate the body into anabolism. This process involves the building of complex compounds from smaller simpler ones (for example proteins are built from amino acids). This process requires energy.
(13 Nov 1997)
receptors, steroid Proteins found usually in the cytoplasm or nucleus that specifically bind steroid hormones and trigger changes influencing the behaviour of cells. The steroid receptor-steroid hormone complex regulates the transcription of specific genes.
(12 Dec 1998)
gonadal steroid-binding globulin A protein that transports 65% of the testosterone in plasma.
Synonym: sex steroid-binding globulin.
(05 Mar 2000)
saturated steroid 6 alpha-hydroxylase <enzyme> Acts on 5 alpha-androstane-3 beta,17 beta-diol and 5 alpha-pregnan-3 beta-ol-20-one; does not require cytochrome p-450
Registry number: EC 1.14.99.-
Synonym: sat steroid 6alpha-hydroxylase
(26 Jun 1999)
sex steroid-binding globulin A protein that transports 65% of the testosterone in plasma.
Synonym: sex steroid-binding globulin.
(05 Mar 2000)
steroid A group name for lipids that contain a hydrogenated cyclopentanoperhydrophenanthrene ring system. Some of the substances included in this group are progesterone, adrenocortical hormones, the gonadal hormones, cardiac aglycones, bile acids, sterols (such as cholesterol), toad poisons, saponins and some of the carcinogenic hydrocarbons.
(18 Nov 1997)
steroid 11-alpha-hydroxylase <enzyme> Converts 11-deoxycortisol to 11-alpha cortisol (the 11-alpha isomer of hydrocortisone)
Registry number: EC 1.14.99.-
(26 Jun 1999)
steroid 11 beta-monooxygenase <enzyme> A steroid hydroxylase system found in adrenal tissues. It catalyses the 11-hydroxylation of steroids in the presence of molecular oxygen and consists of an NADPH-specific flavoprotein, a non-haem iron protein, and cytochrome p-450. Its deficiency is a cause of congenital adrenal hyperplasia (adrenal hyperplasia, congenital).
Chemical name: Steroid, reduced-adrenal-ferredoxin:oxygen oxidoreductase (11 beta-hydroxylating)
Registry number: EC 1.14.15.4
(12 Dec 1998)
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