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"methylmalonate saemialdehyde"¿¡ ´ëÇÑ ¿µ¿µ ÀÇÇлçÀü ¼¼ºÎ °Ë»ö °á°úÀÔ´Ï´Ù
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2-hydroxymuconic saemialdehyde lyase <enzyme> Forms 2-ketopent-4-enoate plus formate
Registry number: EC 4.1.2.-
Synonym: hydroxymuconic saemialdehyde hydrolase, 2-hydroxymuconic saemialdehyde hydrolase
(26 Jun 1999)
L-aminoadipate saemialdehyde dehydrogenase <enzyme> Degrades saccharopine, enzyme defect in saccharopinuria
Registry number: EC 1.2.1.31
Synonym: alpha-aminoadipate reductase system, 2-aminoadipate reductase, aminoadipate-saemialdehyde dehydrogenase, alpha-aminoadipate reductase
(26 Jun 1999)
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