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"inner ear dysplasia"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
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¿µ¹® ear ÇÑ±Û ±Í
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  ±Í´Â ¿À°¨ÀÇ ÇϳªÀΠû°¢À» ¹Þ¾Æµé¿© ¼Ò¸®¸¦ µè°í, È¸È­¸¦ ÀÌÇØÇϴ Áß¿äÇÑ »ýȰÁ¤º¸ÀÇ ÀԷ Àå¼ÒÀÌ´Ù. ½ÅüÀÇ ÆòÇü°¨°¢À» ´ã´çÇϴ Áß¿äÇÑ ÀüÁ¤, ¹Ý°í¸®°üÀÌ À־ Àΰ£ÀÌ ÀÏ»ó»ýȰÀ» ¿µÀ§Çϴ µ¥¿¡ ¸Å¿ì Áß¿äÇÑ ±â´ÉÀ» Çϴ °÷ÀÌ´Ù. ¾î¶² ÀÌÀ¯·Î À̵頱â´ÉÀÌ ¶³¾îÁö¸é ³­Ã»À̳ª ±Í¿ïÀ½, ¶Ç´Â Çö±âÁõ, ºñƲ°Å¸² µîÀÇ ÆòÇüÀå¾Ö°¡ ³ªÅ¸³ª°í, ½É°¢ÇÑ Á¤º¸Àå¾Ö°¡ ÀϾ¹Ç·Î ÃæºÐÇÑ ÁÖÀǰ¡ ÇÊ¿äÇÏ´Ù.
  
  ±Í´Â Å©°Ô ¹Ù±ù±Í, °¡¿îµ¥±Í, ¼Ó±ÍÀÇ 3ºÎºÐÀ¸·Î ³ª´©´Âµ¥ ¹Ù±ù±Í¶ó°í Çϴ °ÍÀº ¼Ò¸®¸¦ °í¸·±îÁö Àü´ÞÇϴ ¿ÜÀ̵µºÎºÐÀ» ¸»ÇÑ´Ù. ±×¸®°í ÁßÀ̶õ °í¸·¿¡¼­ ³»ÀÌ »çÀÌÀÇ °ø°£À¸·Î ¿©±â¿¡´Â °í¸·ÀÇ Áøµ¿À» ¼Ò¸®¸¦ ´À³¢´Â ´ÞÆØÀÌ(cochlea)±îÁö Àü´ÞÇØ Áִ ÀÛÀº »ÀÀΠ3°³ÀÇ ±Ó¼Ó»À(ossicle)ÀÌ Àִ °÷ÀÌ´Ù. ¼Ó±Í¶õ ¼Ò¸®¸¦ Á÷Á¢ ´À³¢´Â ±â°üÀΠ´ÞÆØÀÌ, ÆòÇà°¨°¢À» ´ã´çÇϴ ¹Ý°í¸®°ü, ±¸Çü³¶(saccule), Å¸¿ø³¶(utricle)ÀÌ Àִ °÷À» ¸»ÇÑ´Ù.
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
  • dentin dysplasia
    »ó¾ÆÁúÇü¼ºÀÌ»ó
  • diaphyseal dysplasia
    »À¸öÅëÇü¼ºÀÌ»ó, °ñ°£Çü¼ºÀÌ»ó
  • ectrodactyly-ectodermal dysplasia clefting syndrome
    °áÁö¿Ü¹è¿±Çü¼ºÀ̻󰥸²ÁõÈıº
  • epidermal dysplasia
    Ç¥ÇÇÇü¼ºÀÌ»ó
  • epiphyseal dysplasia
    »À³¡Çü¼ºÀÌ»ó, °ñ´ÜÇü¼ºÀÌ»ó
  • ectodermal dysplasia
    ¿Ü¹è¿±Çü¼ºÀÌ»ó
  • fibromuscular dysplasia
    ¼¶À¯±ÙÀ°Çü¼ºÀÌ»ó
  • fibrous dysplasia
    ¼¶À¯Çü¼ºÀÌ»ó
  • fibrous dysplasia of bone
    »À¼¶À¯Çü¼ºÀÌ»ó
  • fibrous dysplasia polyostotic
    ¿©·¯»À¼¶À¯Çü¼ºÀÌ»ó, ´Ù°ñ¼¶À¯ÀÌÇü¼º
  • hypohidrotic ectodermal dysplasia
    ¶¡ÀúÇϿܹ迱Çü¼ºÀÌ»óÁõ, ¹ßÇÑÀúÇϼº¿Ü¹è¿±Çü¼ºÀÌ»óÁõ
  • hidrotic ectodermal dysplasia
    ¶¡È긲¿Ü¹è¿±Çü¼ºÀÌ»óÁõ, ¹ßÇѼº¿Ü¹è¿±Çü¼ºÀÌ»óÁõ
  • multiple epiphyseal dysplasia
    ¹µ»À³¡Çü¼ºÀÌ»ó, ´Ù¹ß°ñ´ÜÇü¼ºÀÌ»ó
  • mammary dysplasia
    À¯¹æÇü¼ºÀÌ»ó
  • metaphyseal dysplasia
    »À¸öÅ볡Çü¼ºÀÌ»ó, °ñ°£´ÜÇü¼ºÀÌ»ó
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
  • cortical dysplasia
    °ÑÁúÇü¼ºÀÌ»ó
  • craniometaphyseal dysplasia
    ¸Ó¸®»À»À¸öÅ볡Çü¼ºÀÌ»ó, µÎ°³°ñ°£´ÜÇü¼ºÀÌ»ó
  • cystic renal dysplasia
    ³¶¼ºÄáÆÏÇü¼ºÀÌ»ó, ³¶¼º½ÅÀåÇü¼ºÀÌ»ó
  • dysplasia
    Çü¼ºÀÌ»ó
  • diaphyseal dysplasia
    »À¸öÅëÇü¼ºÀÌ»ó, °ñ°£Çü¼ºÀÌ»ó
  • ectodermal dysplasia
    ¿Ü¹è¿±Çü¼ºÀÌ»ó
  • epidermal dysplasia
    Ç¥ÇÇÇü¼ºÀÌ»ó
  • epiphyseal dysplasia
    »À³¡Çü¼ºÀÌ»ó, °ñ´ÜÇü¼ºÀÌ»ó
  • fibrous dysplasia
    ¼¶À¯Çü¼ºÀÌ»ó
  • hidrotic ectodermal dysplasia
    ¶¡È긲¿Ü¹è¿±Çü¼ºÀÌ»ó
  • hypohidrotic ectodermal dysplasia
    ¶¡ÀúÇϿܹ迱Çü¼ºÀÌ»óÁõ
  • mammary dysplasia
    À¯¹æÇü¼ºÀÌ»ó
  • metaphyseal dysplasia
    »À¸öÅ볡Çü¼ºÀÌ»ó, °ñ°£´ÜÇü¼ºÀÌ»ó
  • multiple dysplasia
    ¹µÇü¼ºÀå¾Ö
  • neural dysplasia
    ½Å°æÇü¼ºÀå¾Ö
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
  • Engelmanns diaphyseal dysplasia
    ¿¨°Ö¸¸ °ñ°£ ÀÌÇü¼ºÁõ.
  • Goldenhars syndrome->oculo-auriculo-vertebral dysplasia
    °ñµçÇÏÁõÈıº
  • Scheibe dysplasia
    »þÀ̺£ÀÌÇü¼º
  • X-linked hypohidrotic ectodermal dysplasia
    ¼º¿°»öü ¿¬°ü ¼ÒÇÑ ¿Ü¹è¿°Çü¼ºÀå¾Ö
  • acetabular dysplasia
    ºñ±¸ ÀÌÇü¼ºÁõ(ºñÏ¿ì¶û¡àõñø), °ü°ñ±¸ ÀÌÇü¼º(Áõ)(ΰÍéÏ¿ì¶û¡à÷ñø), ºñ±¸Çü¼ººÎÀüÁõ(ºñÏ¿ì¶û¡Üôàõñø).
  • anhidrotic ectodermal dysplasia
    ¹«ÇѼº ¿Ü¹è¿± ÀÌÇü¼º.
  • anhidrotic ectodermal dysplasia
    ¶¡°áÇ̼º ¿Ü¹è¿± ÀÌÇü¼º
  • hereditary ectodermal dysplasia
    À¯Àü¼º ¿Ü¹è¿±¼º ÀÌÇü¼ºÁõ(¡­èâÛÏç¨àõì¶û¡à÷ ñø).
  • hereditary oral mucoepithelial dysplasia
    À¯Àü¼º ±¸°­ Á¡¸· »óÇÇ ÀÌÇü¼º
  • hidrotic ectodermal dysplasia
    ¹ßÇѼº ¿Ü¹è¿± ÀÌÇü¼º
  • polyostotic fibrous dysplasia
    ´Ù°ñ¼º ¼¶À¯¼º °ñÀÌÇü¼º(Áõ).
  • polyostotic fibrous dysplasia
    ´Ù°ñ¼º ¼¶À¯¼º °ñÀÌÇü¼º(Áõ)(ÒýÍéàõ àéë«àõ °ñÀÌÇü¼º(Áõ))
  • progressive diaphyseal dysplasia
    ÁøÇ༺ °ñ°£¼º ÀÌÇü¼º(Áõ)(òäú¼àõÍéÊÏàõì¶ û¡à÷ñø).
  • progressive diaphyseal dysplasia
    ÁøÇ༺ °ñ°£¼º ÀÌÇü¼º(Áõ)(òäú¼àõ ÍéÊÏàõ ì¶û¡à÷(ñø))
  • pterygo arthromyo dysplasia congenita
    ¼±Ãµ¼º ÀÍ»óÆí °üÀý±Ù ÀÌÇü¼º(Áõ)(à»ô¸àõìÏßÒø¸Î¼ï½ÐÉì¶û¡à÷ñø).
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
  • cochleo-saccular dysplasia
    ¿Í¿ì±¸Çü³¶Çü¼ººÎÀüÁõ
  • congenital alveolar dysplasia
    ¼±Ãµ¼º ÆóÆ÷ÀÌÇü¼º(Áõ)(¡­øËøàì¶û¡à÷ñø).
  • craniometaphyseal dysplasia
    µÎ°³°ñ-°ñ°£´ÜÀÌÇü¼º(ÔéËÏÍéÍéÊÏÓ®ì¶û¡à÷).
  • cystic renal dysplasia
    ³¶¼º ½ÅÀÌÇü¼º(Áõ)
  • cystic renal dysplasia
    ³¶¼º ½Å ÀÌÇü¼ºÁõ(¡­ãìì¶û¡à÷ñø)
  • dentin dysplasia
    »ó¾ÆÁúÀÌÇü¼ºÁõ (¡­ì¶û¡à÷ñø).
  • diaphyseal dysplasia
    °ñ°£ ÀÌÇü¼ºÁõ(ÍéÊÏì¶û¡à÷ñø), ÁøÇ༺ °ñ°£ ÀÌÇü¼ºÁõ(òäú¼àõÍéÊÏû¡à÷ñø)
  • dysplasia
    ÀÌÇü¼º(Áõ)(ì¶û¡à÷ñø), Çü¼ºÀå¾Ö(û¡à÷î¡äô)
  • dysplasia
    ÀÌÇü¼º;Çü¼ºÀå¾Ö
  • dysplasia
    ÀÌÇü¼ºÁõ
  • dysplasia
    Çü¼ºÀå¾Ö
  • ectodermal dysplasia (anhidrosis)
    ¿Ü¹è¿±Çü¼ºÀå¾Ö (¶¡°á¿©Áõ)
  • ectrodactyly ectodermal dysplasia cleftlip syndrome =EEC s.
    ÁöÁö°á¼Õ ¼º ¿Ü¹è¿± ÀÌÇü¼º Åä¼øÁõÈıº(ò¦ò¿ÌÀáßàõèâÛÏç¨ì¶û¡à÷÷Íâîñøý¦ÏØ).
  • epidermal dysplasia
    Ç¥ÇÇÀÌÇü¼º(Áõ)(¡­ì¶û¡à÷ñø)
  • epidermal dysplasia (ichthyosis)
    Ç¥ÇÇÇü¼ºÀå¾Ö (ºñ´Ã¹öÁò)
´ëÇÑÇØºÎÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 13 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
  • Inner cell mass (Embryoblast)
    ¼Ó¼¼Æ÷µ¢ÀÌ [¹èÀÚ¸ðü]
    [¿¾ ¿ë¾î] ³»¼¼Æ÷±«
  • Inner cell mass [Embryoblast]
    ¼Ó¼¼Æ÷µ¢ÀÌ [¹èÀÚ¸ðü]
    [¿¾ ¿ë¾î] ³»ºÎ¼¼Æ÷±«
  • Inner phalangeal cell
    ¼Ó¼Õ°¡¶ô¼¼Æ÷
    [¿¾ ¿ë¾î] ³»Áö»ó¼¼Æ÷
  • Inner plexiform layer
    ¼Ó¾ó±âÃþ
    [¿¾ ¿ë¾î] ³»¸Á»óÃþ
  • Inner circumferential lamella
    ¼ÓÁÖÀ§ÃþÆÇ
    [¿¾ ¿ë¾î] ³»ÁÖÀ§ÃþÆÇ
  • Inner acrosomal membrane
    ¼Ó÷´Üü¸·
    [¿¾ ¿ë¾î] ³»Ã·´Üü¸·
  • Inner hair cell
    ¼ÓÅм¼Æ÷
    [¿¾ ¿ë¾î] ³»À¯¸ð¼¼Æ÷
  • Inner layer
    ¼ÓÆÇ
    [¿¾ ¿ë¾î] ³»ÆÇ
  • Inner table
    ¼ÓÆÇ
    [¿¾ ¿ë¾î] ³»ÆÇ
  • Inner nuclear layer
    ¼ÓÇÙÃþ
    [¿¾ ¿ë¾î] ³»ÇÙÃþ
  • Inner tunnel
    ¼Ó±¼
    [¿¾ ¿ë¾î] ³»ÅͳÎ
  • Inner bulb
    ¼Ó¸Á¿ï
    [¿¾ ¿ë¾î] ³»±¸
  • Inner segment
    ¼ÓºÐÀý
    [¿¾ ¿ë¾î] ³»Àý
KI ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 3 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
  • internal ear
    ³»ÀÌ
  • middle ear
    ÁßÀÌ
  • rudimentary ear
    ÈçÀûÀÌ
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 2
fem intern at inner side of the thighs [Lat. femoribus internus]
IC icteric, icterus; immune complex; immunoconjugate; immunocytochemistry; immunocytotoxicity; impedanc...
ICBF inner cortical blood flow
ICM inner cell mass; integrated conditional model; intercostal margin; International Confederation of Mi...
IEE inner enamel epithelium
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 2
ILM inner limiting membrane
IM inner medulla
IM inner membrane
IMM inner mitochondrial membrane
IML inner molecular layer
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • fibrous dysplasia
    ¼¶À¯¼º ÀÌÇü¼ºÁõ, ¼¶À¯ ÀÌÇü¼ºÁõ, ¼¶À¯¼º ÀÌÇü¼º, ¼¶À¯¼º Çü¼º Àå¾Ö
    °ñ¼ö°¡ ºñÁ¤»óÀûÀ¸·Î ¼¶À¯ Á¶Á÷À¸·Î ´ëÄ¡µÈ °ÍÀ¸·Î¼­ º¸Åë ¾î¸° ½ÃÀý¿¡ ¹ßº´ÇÑ´Ù.
  • hereditary ectodermal dysplasia
    À¯Àü¼º ¿Ü¹è¿±¼º ÀÌÇü¼ºÁõ
  • mesoectodermal dysplasia
    Á߿ܹ迱¼º ÀÌÇü¼ºÁõ
    ¿¬°ñ ¿Ü¹è¿±¼º ÀÌÇü¼ºÁõ. ¿¤¸®½º ¹Ý Å©·¹º§Æ® ÁõÈıº.
  • monostotic fibrous dysplasia
    ´Ü°ñ ¼¶À¯¼º ÀÌÇü¼ºÁõ
  • multiple epiphyseal dysplasia
    ´Ù¹ß¼º °ñ´Ü ÀÌÇü¼ºÁõ
  • oculo-dento-osseous dysplasia
    ´«-ÀÌ-»À ÀÌÇü¼º
  • periapical cemental dysplasia
    Ä¡±Ù´Ü ¹é¾ÇÁú ÀÌÇü¼º, Ä¡±Ù´Ü ¹é¾ÇÁú ÀÌÇü¼ºÁõ
    1. ¹é¾ÇÁúÀ̳ª Ä¡±Ù´Ü °ñÁúÀÇ ÀÌ»óÀû ¹ÝÀÀÀ¸·Î Á߳⠿©¼º¿¡ ¼±È£ÇÏ´Â °æÇâÀÌ ÀÖ´Ù. ÇÏ¾Ç ÀüÄ¡ Ä¡±Ù ºÎÀ§¿¡ ÀÎÁ¢ÇÏ¿© È£¹ßÇϸç ÈæÀο¡ ¸¹´Ù. 2. Á߳⠿©¼º¿¡ ¼±È£ÇÏ´Â °æÇâÀÌ ÀÖ°í ÇÏ¾Ç ÀüÄ¡ Ä¡±Ù ºÎÀ§¿¡ ÀÎÁ¢ÇÏ¿© È£¹ßÇϸç ÈæÀο¡ ¸¹´Ù. ºÎÁõÈļºÀ̸ç Ä¡¾Æ°¡ ¹ß°ÅµÈ ÈÄ¿¡µµ °³Á¶¾øÀÌ ¾Ç°ñ ³»¿¡¼­ Á¸¼ÓÇÑ´Ù. óÀ½ÀÇ °ñ ¿¬È­±â¿¡¼­´Â ÇÑ °³ ³»Áö ¼ö °³ Ä¡¾ÆÀÇ ±Ù´Ü ºÎÀ§¿¡ °æ°è°¡ ºÒºÐ¸íÇÑ ¾Ï¿µÀÌ ³ªÅ¸³ª¼­ À°¾ÆÁ¾°ú ºñ½ÁÇÏ°Ô º¸À̳ª Ä¡¼öÀÇ »ýȰ·ÂÀÌ ÀÖ´Ù´Â Á¡À¸·Î ±¸º° ÇÒ ¼ö ÀÖ´Ù. ÁÖ±âÀû °üÂû¸¸ ÇØÁÖ¸é Ä¡·á´Â ºÒÇÊ¿äÇÏ´Ù.
  • polyostotic fibrous dysplasia
    ´Ù°ñ¼º ¼¶À¯¼º ÀÌÇü¼ºÁõ
  • pterygo arthromyo dysplasia congenita
    ¼±Ãµ¼º ÀÍ»ó Æí°üÀý±Ù ÀÌÇü¼ºÁõ
    »çÁö¿¡ ÀÍ»óÃéÆíÀ» Çü¼ºÇÏ°í °üÀý ¸¸°îÁõÀ» ÇÕº´ÇÏ´Â ÁõÈıº.
  • renal dysplasia
    ½Å ÀÌÇü¼º, ½Å ÀÌÇü¼ºÁõ
  • X-linked hypohidrotic ectodermal dysplasia
    ¼º¿°»öü ¿¬°ü ¼ÒÇÑ ¿Ü¹è¿± Çü¼ºÀå¾Ö
  • artificial ear drum
    Àΰø °í¸·
    ÀΰøÀûÀ¸·Î ¸¸µç °í¸·. °í¸·¿¡ Å« õ°øÀÌ À־ ±Í°¡ Àß µé¸®Áö ¾Ê´Â °æ¿ì¿¡ Àΰø °í¸·À» ±Í¿¡ ÀåÄ¡ÇÔÀ¸·Î½á û·ÂÀ» ÁÁ°Ô ÇÒ ¼ö ÀÖ´Ù. Àç·á·Î´Â ¸ñÈ­¡¤°í¹«¸·¡¤³­¸· µîÀÌ »ç¿ëµÇ°í, ¸ð¾ç¿¡´Â ¿©·¯ °¡Áö°¡ ÀÖ´Ù. Àΰø °í¸·ÀÌ È¿·ÂÀÌ ÀÖ±â À§Çؼ­´Â, ±Í°¡ Àß µé¸®Áö ¾Ê´Â ¿øÀÎÀÌ ÀüÀ½°èÀå¾Ö
  • Balinville ear
    ºí¶ûºó ÀÌ
    ÁÂ¿ì ºñ´ëĪÀÇ ±Í.
  • bat ear
    ÇØ¾È ÀÌ
    ÇØ¼ö¿å¿¡ ÀÇÇÑ ±Í ¾ÈÀÇ ¿°Áõ.
  • Blainville ear
    ºí¶ûºô ÀÌ
    ÁÂ¿ì ºñ´ëĪÀÇ ±Í.
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
mandibulofacial dysplasia A hereditary disorder occurring in two forms: the complete form (franceschetti's syndrome) is characterised by antimongoloid slant of the palpebral fissures, coloboma of the lower lid, micrognathia and hypoplasia of the zygomatic arches, and microtia. It is transmitted as an autosomal trait. The incomplete form (treacher collins syndrome) is characterised by the same anomalies in less pronounced degree. It occurs sporadically, but an autosomal dominant mode of transmission is suspected.
(12 Dec 1998)
ventriculoradial dysplasia A congenital syndrome consisting of a ventricular septal defect with associated absence of thumb or radius.
(05 Mar 2000)
cerebral dysplasia Abnormal development of the telencephalon.
(05 Mar 2000)
retinal dysplasia <ophthalmology> Congenital, often bilateral, retinal abnormality characterised by the arrangement of outer nuclear retinal cells in a palisading or radiating pattern surrounding a central ocular space. This disorder is sometimes hereditary.
(12 Dec 1998)
cervical dysplasia A term which describes precancerous changes to the epithelial cells lining the cervix. The diagnosis is made from the microscopic examination of a PAP smear acquired tissue specimen. Less than 5% of all PAP smears will show cervical dysplasia. The peak incidence is in women 25 to 35 years of age. Risk factors include multiple sexual partners, early onset of sexual activity (less than 18), early childbearing (less than 16) and past medical history of a sexually transmitted disease (for example genital warts, genital herpes, HIV infection). Treatment is based on the degree of dysplasia present, as judged by a pathologist. Treatments include cryotherapy and conisation.
Origin: Gr. Plassein = to form
(27 Sep 1997)
cervix dysplasia A spectrum of histologic changes in the epithelium of the cervix uteri which may begin as a superficial lesion and progress to invasive carcinoma.
(12 Dec 1998)
periapical cemental dysplasia <dentistry> A benign, painless, non-neoplastic condition of the jaws which occurs almost exclusively in middle-aged black females.
The lesions are usually multiple, most frequently involve vital mandibular anterior teeth, surround the root apices, and are initially radiolucent (becoming more opaque as they mature).
Synonym: periapical osteofibrosis.
(21 Jun 2000)
metaphyseal dysplasia <radiology> (Pyle disease) also known as: craniometaphyseal dysplasia, autosomal recessive, failure of modeling of cylindrical bones, Erlenmeyer flask appearance of metaepiphyses
(12 Dec 1998)
metaphysial dysplasia An abnormality that occurs when new bone at the metaphyses of long bones fails to undergo remodeling to the normal tubular structure; the ends of long bones appear to be expanded and porotic, with thin cortex; there may be an associated overgrowth of cranial bones (craniometaphysial dysplasia).
(05 Mar 2000)
chondroectodermal dysplasia Triad of chondrodysplasia, ectodermal dysplasia, and polydactyly, with congenital heart defects in over half of patients; autosomal recessive inheritance.
Synonym: Ellis-van Creveld syndrome.
(05 Mar 2000)
cleidocranial dysplasia <paediatrics> An inherited disorder of bone development transmitted with an autosomal dominant pattern.
Characteristics include absent or incompletely formed collar bones, dental abnormalities, joint laxity and a characteristic facial appearance (heavy brow, protruding jaw, wide nasal bridge and malaligned teeth).
Inheritance: autosomal dominant.
Origin: Gr. Plassein = to form
(27 Sep 1997)
Mondini dysplasia Congenital anomaly of osseus and membranous labyrinth characterised by aplastic cochlea, and deformity of the vestibule and saemicircular canals with partial or complete loss of auditory and vestibular function; may be associated with spontaneous cerebrospinal fluid otorrhoea resulting in meningitis.
See: Mondini deafness.
(05 Mar 2000)
monostotic fibrous dysplasia Fibrous dysplasia of a single bone.
Synonym: localised osteitis fibrosa, osteitis fibrosa circumscripta.
(05 Mar 2000)
mucoepithelial dysplasia An epithelial cell dishesive disease characterised by red, periorificial mucosal lesions of oral, nasal, vaginal, urethral, anal, bladder, and conjunctival mucosa, with cataracts, follicular keratosis, non-scarring alopecia, frequent pulmonary infections, pneumothorax, and sometimes cor pulmonale; autosomal dominant inheritance.
(05 Mar 2000)
congenital dysplasia of the hip A malformation of the hip joint that is present at birth. Genetic factors likely play a role in this disorder. Features include hip dislocation, asymmetry of leg positions, asymmetric fat folds and diminished movement on the affected side. Some children will exhibit little or no features and must be diagnosed by physical examination of the hip joints.
(27 Sep 1997)
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