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iron-storage disease The storage of excess iron in the parenchyma of many organs, as in idiopathic haemochromatosis or transfusion haemosiderosis.
(05 Mar 2000)
glycogen <biochemistry> Branched polymer of D glucose (mostly _(1-4) linked, but some _(1-6) at branch points).
Size range very variable, up to 10exp5 glucose units. Major short term storage polymer of animal cells and is particularly abundant in the liver and to a lesser extent in muscle. In the electron microscope glycogen has a characteristic asterisk or star appearance.
(18 Nov 1997)
glycogen debranching enzyme system 1,4-alpha-d-glucan-1,4-alpha-d-glucan 4-alpha-d-glucosyltransferase/dextrin 6 alpha-d-glucanohydrolase. An enzyme system having both 4-alpha-glucanotransferase (ec 2.4.1.25) and amylo-1,6-glucosidase (ec 3.2.1.33) activities. As a transferase it transfers a segment of a 1,4-alpha-d-glucan to a new 4-position in an acceptor, which may be glucose or another 1,4-alpha-d-glucan. As a glucosidase it catalyses the endohydrolysis of 1,6-alpha-d-glucoside linkages at points of branching in chains of 1,4-linked alpha-d-glucose residues. Amylo-1,6-glucosidase activity is deficient in glycogen storage disease type III.
(12 Dec 1998)
glycogen granule Glycogen occurring in cells as beta granule's which average about 300 A
glycogen phosphorylase <enzyme> Enzyme that catalyses the sequential removal of glycosyl residues from glycogen to yield one glucose-1-phosphate per reaction. Its activity is controlled by phosphorylation (by phosphorylase kinase).
(21 Jun 2000)
glycogen synthase <enzyme> An enzyme of the transferase class that catalyses the reaction of udpglucose and (1,4-alpha-d-glucosyl)n to yield udp and 1,4-alpha-d-glucosyl)n+1. The reaction is highly regulated by allosteric effectors, by phosphorylation reactions, and by insulin.
Chemical name: UDPglucose:glycogen 4-alpha-D-glucosyltransferase
Registry number: EC 2.4.1.11
(12 Dec 1998)
glycogen synthase-d phosphatase <enzyme> An enzyme that catalyses the conversion of phosphorylated, inactive glycogen synthase d to active dephosphoglycogen synthase I.
Chemical name: (UDPglucose:glycogen 4-alpha-D-glucosyltransferase-D) phosphohydrolase
Registry number: EC 3.1.3.42
(12 Dec 1998)
glycogen synthetase <enzyme> An enzyme which makes amylose out of glucose molecules (a type of sugar) and attaches them to glycogen (a type of polysaccharide).
(09 Oct 1997)
UDPglucose-glycogen glucose 1-phosphotransferase <enzyme> Catalyses the transfer of glucose 1-phosphate onto c-6 of glucose residues in glycogen to form a phosphodiester
Registry number: EC 2.7.8.-
Synonym: ugg-glcptase
(26 Jun 1999)
liver glycogen Glycogen stored in the liver.
(12 Dec 1998)
computer storage devices Devices capable of receiving data, retaining data for an indefinite or finite period of time, and supplying data upon demand.
(12 Dec 1998)
platelet storage pool deficiency A group of disorders characterised by a decrease or lack of platelet dense bodies in which the releasable pool of adenine nucleotides and 5ht are normally stored.
(12 Dec 1998)
storage 1. The act of depositing in a store or warehouse for safe keeping; also, the safe keeping of goods in a warehouse.
2. Space for the safe keeping of goods.
3. The price changed for keeping goods in a store. Storage battery.
<physics> See the Note under Battery.
Source: Websters Dictionary
(01 Mar 1998)
storage granule 1. <cell biology> Membrane bounded vesicles containing condensed secretory materials (often in an inactive, zymogen, form). Otherwise known as zymogen granules or condensing vacuoles.
2. Granules found in plastids or in cytoplasm, assumed to be food reserves, often of glycogen or other carbohydrate polymer.
(18 Nov 1997)
storage protein deamidase <enzyme> Deamidates glutaminyl residues; isolated from germinating wheat grains
Registry number: EC 3.5.1.-
Synonym: seed storage protein deamidase
(26 Jun 1999)
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