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Creutzfeldt-Jakob disease An type of spongiform encephalopathy. The brain develops numerous tiny holes. Symptoms include personality changes, hallucinations, muscle twitching and muscle stiffness, gait changes, poor coordination, trouble speaking, drowsiness, dementia, memory loss, and anxiety.
Ãâó: www3.uta.edu/sswtech/sapvc/information/teens13_15/...
Creutzfeldt-Jakob disease This is a rare neurological disease thought to be caused by organic substances called prions. It has been linked to eating beef products that are contaminated with BSE.
Ãâó: www.bodyandmind.co.za/info_glossary.html
Creutzfeldt-Jakob disease A disease of humans hypothesized to be caused by a prion, or a small protein, which alters the structure of a normal brain protein, resulting in destruction of brain neural tissue. The most common form is thought to have genetic origins. There is strong epidemiologic and laboratory evidence for a causal association between new variant CJD and BSE.
Ãâó: www.csrees.usda.gov/nea/biotech/res/biotechnology_...
Creutzfeldt-Jakob d. a rare prion disease, associated with a number of different mutations of the prion protein gene, existing in sporadic, familial (as an autosomal dominant), and infectious forms, with onset usually in middle life, and having a wide variety of clinical and pathological features. The most commonly seen are varying degrees of spongiform degeneration of neurons, neuronal loss, gliosis, and amyloid plaque formation, accompanied by rapidly progressive dementia, myoclonus, motor disturbances, and characteristic changes in the electroencephalogram. Death generally occurs within a year of onset, although longer courses up to 5 years are not uncommon. Sporadic cases account for 85–95 per cent of all occurrences. Infectious cases generally result from surgical procedures or injection of human growth hormone prepared from infected pituitary glands. Called also Jakob's d. and Jakob-Creutzfeldt d.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
Creutzfeldt-Jakob d., new variant a variant of Creutzfeldt-Jakob disease occurring almost exclusively in the United Kingdom, having a younger age of onset than is seen in Creutzfeldt-Jakob disease, and caused by the same agent that causes bovine spongiform encephalopathy.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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