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  • acute intermittent porphyria
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EPP Erythropoietic Proto-Porphyria
HCP Hereditary Copro-Porphyria; À¯Àü¼º CoproPorphyria
PP   1) Presenting Part
  2) Plasma-Pheresis
  3) Pancreatic Polype...
PTC   1) Percutaneous Transhepatic Cholangiography
    = PTHC
 ...
AIP acute idiopathic pericarditis; acute infectious polyneuritis; acute intermittent porphyria; aldoster...
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BSA 125)I-bovine serum albumin
BSA AGE-bovine serum albumin
ABAE Adult bovine aortic endothelial
Bo Bovine
b Bovine
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hepatoerythropoietic porphyria An autosomal recessive disorder in which there is a deficiency or absence of uroporphyrinogen decarboxylase; results in photosensitivity and excessive hepatic production of 8-and 7-carboxylate porphyrins.
(05 Mar 2000)
South African type porphyria Porphyria characterised by abdominal pain and neuropsychiatric abnormalities, by dermal sensitivity to light and mechanical trauma, by increased faecal excretion of proto-and coproporphyrin, and by increased urinary excretion of d-aminolevulinic acid, porphobilinogen, and porphyrins; due to a deficiency of protoporphyrinogen oxidase; autosomal dominant inheritance.
Synonym: protocoproporphyria hereditaria, South African type porphyria.
(05 Mar 2000)
squirrel porphyria Porphyria as an apparently normal metabolic state seen in the Florida fox squirrel (Sciurus niger).
(05 Mar 2000)
d-aminolevulinate dehydratase porphyria An inherited disorder in which there is a deficiency of porphobilinogen synthase; d-aminolevulinate levels are elevated, leading to neurological disturbances.
Synonym: porphobilinogen synthase porphyria.
(05 Mar 2000)
swine porphyria Porphyria as a dominant trait seen in swine.
(05 Mar 2000)
symptomatic porphyria A form of hepatic porphyria (porphyria, hepatic) characterised by photosensitivity resulting in bullae that rupture easily to form shallow ulcers. This condition occurs in two forms: a sporadic, nonfamilial form that begins in middle age and has normal amounts of uroporphyrinogen decarboxylase with diminished activity in the liver; and a familial form in which there is an autosomal dominant inherited deficiency of uroporphyrinogen decarboxylase in the liver and red blood cells.
(12 Dec 1998)
intermittent acute porphyria <gastroenterology, haematology> A group of rare inherited metabolic disorders that result from a disturbance in porphyrin metabolism, causing increased formation and excretion of porphyrin or its precursors.
It is caused by hepatic overproduction of d-aminolevulinic acid, which has greatly increased urinary excretion and of porphobilinogen, and some increase of uroporphyrin, due to a deficiency of porphobilinogen deaminase.
Clinical features: intermittent acute attacks of hypertension, abdominal colic, psychosis, and polyneuropathy, but with no photosensitivity.
It is exacerbated by the ingestion of certain drugs such as; barbiturates).
Inheritance: autosomal dominant.
(20 Sep 2002)
ovulocyclic porphyria Acute episodic exacerbations of porphyria occurring in the premenstrual period.
(05 Mar 2000)
erythropoietic porphyria A classification of porphyria that includes congenital erythropoietic porphyria and erythropoietic protoporphyria.
(05 Mar 2000)
bovine Relating to, affecting, resembling or derived from a cow or bull.
(09 Oct 1997)
bovine acetonaemia bovine ketosis
bovine achondroplasia A calf with a short muzzle and brachycephalic skull, usually resulting from chondrodystrophy; associated with this condition are shortened limbs and anomalies of the vertebral centra; it often results in respiratory and feeding difficulties, and is sometimes fatal.
Synonym: bovine achondroplasia.
(05 Mar 2000)
bovine adenovirus type 3 proteinase <enzyme> Amino acid sequence given in first source
Registry number: EC 3.4.-
Synonym: bav-3 proteinase
(26 Jun 1999)
bovine adenovirus type 7 proteinase <enzyme> Amino acid sequence given in first source
Registry number: EC 3.4.-
Synonym: bav-7 proteinase
(26 Jun 1999)
bovine antitoxin Antitoxin prepared from cattle instead of horses, used in the treatment of persons who are sensitive to horse serum; the cattle are immunised against the toxin for which specific antitoxin is desired.
(05 Mar 2000)
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