| BSSE | bile salt-stimulated esterase |
|---|---|
| BSSL | bile salt-stimulated lipase |
| G6S | glucosamine-6-sulfatase |
| IDS | iduronate sulfatase; immune deficiency state; inhibitor of DNA synthesis; integrated delivery system... |
| MSD | material safety data; mean square deviation; mild sickle cell disease; most significant digit; multi... |
| steroid sulfatase deficiency | A form of ichthyosis, due to 3-beta-hydroxysteroidsulfate sulfatase deficiency, that appears at birth or in early infancy and affects males; characterised by scaling predominantly on the neck and trunk but not on the palms and soles; histologically, there is hyperkeratosis, a granular layer in the epidermis, and normal epidermal cell turnover. Synonym: steroid sulfatase deficiency. (05 Mar 2000) |
|---|---|
| steryl-sulfatase | <enzyme> Arylsulfatases a and b hydrolyze nitrocatechol sulfate, but p-nitrophenyl sulfate is hydrolyzed only slightly by both enzymes; arylsulfatase c hydrolyzes both p-nitrophenyl sulfate and nitrocatechol sulfate, low substrate specificity located chiefly in microsomes; a and b are found in lysosomes; arylsulfatase a is cerebroside sulfatase and arylsulfatase b is chondro-4-sulfatase Registry number: EC 3.1.6.2 Synonym: arylsulfatase c, dehydroepiandrosterone sulfate sulfatase, steroid sulfatase, estrone sulfate sulfohydrolase, steroid sulphatase, cholesterol sulfatase, dhea sulfatase, 3 beta-hydroxysteroid sulfate sulfatase, estrone sulfate sulfatase, sterylsulfatase, steroid sulfohydrolase, cholesterol sulfate sulfatase, arylsulphatase c (26 Jun 1999) |
| N-sulfoglucosamine-3-sulfatase | <enzyme> Acts on n-acetylglucosamine-3-sulfate and n-sulfoglucosamine-3-sulfate Registry number: EC 3.1.6.15 Synonym: n-substituted glucosamine 3-o-sulphatase (26 Jun 1999) |
| sulfatase | 1. Trivial name for enzymes in EC group 3.1.6, the sulfuric ester hydrolases, which catalyze the hydrolysis of sulfuric esters (sulfates) to the corresponding alcohols plus inorganic sulfate; includes aryl-, sterol, glycol-, chondroitin, choline-, cellulose, cerebroside, and chondro-sulfatases. Synonym: arylsulfatase. (05 Mar 2000) |
| disulfoglucosamine-6-sulfatase | <enzyme> Acts on various n-substituted glucosamine-6-o-sulfates Registry number: EC 3.1.6.11 Synonym: disulphoglucosamine-6-sulphatase, glucosamine o,n-disulfate o-sulfohydrolase, glucosamine sulfatase, n-sulfoglucosamine-6-sulfatase (26 Jun 1999) |
| iduronate sulfatase | <enzyme> An enzyme that specifically cleaves the ester sulfate of iduronic acid, and is required for the desulfation of 2-sulfate iduronate residues in heparan sulfate. It is also required in dermatan sulfate degradation. Its deficiency has been demonstrated in Hunter's syndrome, which is characterised by an excess of dermatan sulfate and heparan sulfate. Chemical name: L-Iduronate-2-sulfate 2-sulfohydrolase Registry number: EC 3.1.6.13 (20 Sep 2002) |
| oligosaccharide 2-O-sulfatase | <enzyme> Hydrolyzes the 2-o-sulfate of the disaccharide 4-deoxy-2-o-sulfato-alpha-l-threo-hex-4-enopyranosyluronic acid-(1-4)-2-deoxy-2-sulfamido-6-o-sulfato-d-glucose from heparin Registry number: EC 3.1.6.- Synonym: flavobacterium heparinum 2-o-sulphatase, heparo-2-o-sulfatase (26 Jun 1999) |
| oligosaccharyl sulfatase | <enzyme> From keyhole limpet; hydrolyzes sulfate esters in asparagine-linked oligosaccharides preferentially to 4-nitrocatechol sulfate Registry number: EC 3.1.6.- (26 Jun 1999) |
| lactate-2-sulfate sulfatase | <enzyme> Shows no activity for (l)-isomer Registry number: EC 3.1.6.- Synonym: d-lactate-2-sulfate sulfatase, d-lactate-2-sulfatase (26 Jun 1999) |
| 3b-hydroxysteroid sulfate sulfatase | <enzyme> An enzyme, found in most mammalian tissues, that is capable of hydrolyzing the sulfate ester bonds of a variety of sulfated sterols; a deficiency of this enzyme will result in X-linked ichthyosis. (05 Mar 2000) |
| aberrant bile ducts | Small duct's occasionally present in the ligaments of the liver or originating from the surface of the liver. (05 Mar 2000) |
| adenoma, bile duct | A benign tumour of the intrahepatic bile ducts. (12 Dec 1998) |
| bile | <gastroenterology> A greenish-yellow fluid secreted by the liver and stored in the gallbladder. Bile plays an important role in the intestinal absorption of fats. Bile is secreted by the liver and contains cholesterol, bile salts and waste products such as bilirubin. Bile salts aid in the digestion of fats. Bile passes out of the liver via the bile duct where it is stored in the gallbladder and released in response to a fat-containing meal. (27 Sep 1997) |
| bile acid 3alpha-sulfate sulfohydrolase | <enzyme> Used for determination of serum 3alpha-sulfated bile acids; converts 3alpha-sulfated bile acids into 3beta-hydroxy bile acids Registry number: EC 3.1.6.- Synonym: 3alpha-sulfated bile acid sulfohydrolase, ba-3s sulfohydrolase (26 Jun 1999) |
| bile acid 7alpha-dehydratase | <enzyme> Enzyme in the bacterial bile acid 7alpha-dehydroxylation pathway Registry number: EC 4.2.1.- Synonym: c24 bile acid 7alpha-dehydratase, ba7alphad, baie gene product (26 Jun 1999) |