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"arginosuccinate lyase deficiency"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
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  • ¿µ¹®
    ÇѱÛ
  • nutritional deficiency syndrome
    ¿µ¾ç°áÇÌÁõÈıº
  • vitamin deficiency
    ºñŸ¹Î°áÇÌ(Áõ)
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 14 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
  • histogenetic deficiency
    Á¶Á÷¹ß»ý°áÇÌ
  • immune deficiency
    (¢¡immunodeficiency) ¸é¿ª°áÇÌ
  • latent deficiency
    ÀáÀç°áÇÌÁõ
  • leukocyte adhesion deficiency
    ¹éÇ÷±¸ºÎÂø°áÇÌÁõ
  • mental deficiency
    Á¤½Å¹Ú¾à
  • milk dietary deficiency
    ¿ìÀ¯¿µ¾çÀå¾Ö
  • mineral deficiency
    ¹«±âÁú°áÇÌ(Áõ)
  • nutritional deficiency disease
    ¿µ¾ç°áÇ̺´
  • thyroid hormone deficiency
    ¹æÆÐ»ùÈ£¸£¸ó°áÇÌ, °©»ó»ùÈ£¸£¸ó°áÇÌ
  • vitamin deficiency
    ºñŸ¹Î°áÇÌ(Áõ)
  • electrolyte deficiency syndrome
    ÀüÇØÁú°áÇÌÁõÈıº
  • immunologic deficiency state
    ¸é¿ª°áÇÌ»óÅÂ
  • nutritional deficiency state
    ¿µ¾ç°áÇÌ»óÅÂ
  • nutritional deficiency syndrome
    ¿µ¾ç°áÇÌÁõÈıº
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  • ¿µ¹®
    ÇѱÛ
  • aids=£¾acquired immune deficiency syndrome
    ÈÄõ¼º¸é¿ª°áÇÌÁõÈıº(ý­ô¸àõØóæ¹ÌÀù¹ñøý¦ÏØ)
  • alimentary deficiency =dietary d.
    ½Ä»çºÎÁ·, ¿µ¾çºÎÁ·.
  • anemia iron deficiency
    ö°áÇ̼º ºóÇ÷.
  • anemia,folate deficiency
    ¿±»ê°áÇÌ(ç¨ß«ÌÀù¹)
  • anterior pituitary deficiency
    ³úÇϼöüÀü¿±±â´ÉºÎÀü(Áõ)
  • anterior pituitary deficiency
    ÇϼöüÀü¿±±â´ÉºÎÀü(Áõ).
  • antibody deficiency syndrome
    Ç×ü°áÇÌÁõÈıº(ù÷ô÷ÌÀù¹ñøý¦ÏØ).
  • antitrypsin deficiency
    Çׯ®¸³½Å°áÇÌ
  • apolipoprotein C-Il deficiency
    ¾ÆÆ÷Áö´Ü¹é C-II °áÇÌ
  • apolipoprotein b, deficiency
    ¾ÆÆ÷¸®Æ÷´Ü¹éB°áÇÌÁõ(¡­Ó±ÛÜ¡­ÌÀù¹ñø)
  • arylsulfatase a deficiency
    ¾Æ¸±¼³ÆÄŸÁ¦ A °áÇÌÁõ(¡­ÌÀù¹ñø)
  • aspartylglycosamine amide hydrolase, deficiency
    Aspartylglycosamine amide hydrolase°áÇÌ(¡­ÌÀù¹)
  • functional deficiency
    ±â´É°áÇÌ
  • g6pd deficiency
    G6PD(Æ÷µµ´ç-6-Àλ꿰 Å»¼ö¼ÒÈ¿¼Ò) °áÇÌÁõ
  • galactosidase, alpha-galactosidase a, deficiency
    #NAME?
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  • ¿µ¹®
    ÇѱÛ
  • anterior pituitary deficiency
    ÇϼöüÀü¿±±â´ÉºÎÀü(Áõ).
  • antibody deficiency syndrome
    Ç×ü°áÇÌÁõÈıº(ù÷ô÷ÌÀù¹ñøý¦ÏØ).
  • antitrypsin deficiency
    Çׯ®¸³½Å°áÇÌ
  • apolipoprotein C-Il deficiency
    ¾ÆÆ÷Áö´Ü¹é C-II °áÇÌ
  • apolipoprotein b, deficiency
    ¾ÆÆ÷¸®Æ÷´Ü¹éB°áÇÌÁõ(¡­Ó±ÛÜ¡­ÌÀù¹ñø)
  • arylsulfatase a deficiency
    ¾Æ¸±¼³ÆÄŸÁ¦ A °áÇÌÁõ(¡­ÌÀù¹ñø)
  • aspartylglycosamine amide hydrolase, deficiency
    Aspartylglycosamine amide hydrolase°áÇÌ(¡­ÌÀù¹)
  • biotin-deficiency
    ¹ÙÀÌ¿Àƾ°áÇÌÁõ (¡­ÌÀù¹ñø).
  • biotin-deficiency
    ¹ÙÀÌ¿Àƾ°áÇÌÁõ (¡­ÌÀù¹ñø)
  • brancher enzyme deficiency
    ºÐÁöÈ¿¼Ò°áÇÌ(Áõ)
  • brancher enzyme deficiency
    ºÐÁöÈ¿¼Ò°áÇÌ(¡­ý£áÈÌÀù¹).
  • c inhibitor deficiency
    º¸Ã¼ ÀúÁöÀÎÀÚ °áÇÌÁõ(ÜÍô÷îÁò­ì×í­ÌÀù¹ñø)
  • c3 deficiency
    C3 °áÇÌÁõ (¡­ÌÀù¹ñø)
  • carnitine palmitoyl transferase, deficiency
    Carnitine palmitoyl transferase, deficiency
  • cell adhesion molecular deficiency
    ¼¼Æ÷À¯ÂøºÐÀÚ°áÇÌ
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  • Cytogenetic deficiency
    ¼¼Æ÷¹ß»ý°áÇÌ
    [¿¾ ¿ë¾î] ¼¼Æ÷¹ß»ý°áÇÌ
  • Stimulus deficiency
    ÀڱذáÇÌ
    [¿¾ ¿ë¾î] ÀڱذáÇÌ
  • Histogenetic deficiency
    Á¶Á÷¹ß»ý°áÇÌ
    [¿¾ ¿ë¾î] Á¶Á÷¹ß»ý°áÇÌ
  • Synthesis deficiency
    ÇÕ¼º°áÇÌ
    [¿¾ ¿ë¾î] ÇÕ¼º°áÇÌ
  • Hormone deficiency
    È£¸£¸ó°áÇÌ
    [¿¾ ¿ë¾î] È£¸£¸ó°áÇÌ
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 2
IGD idiopathic growth hormone deficiency; interglobal distance; isolated gonadotropin deficiency
MCD magnetic circular dichroism; mast-cell degranulation; mean cell diameter; mean of consecutive differ...
AAMD American Association on Mental Deficiency; ¹Ì±¹ Á¤½Å ¹Ú¾à Çùȸ
AAMD-ABS American Association on Mental Deficiency-Adaptive Behavior Scale; ¹Ì±¹ Á¤½Å ¹Ú¾à Çùȸ ÀûÀÀ Çൿ ôµµ...
AIDS Acquired Immuno(Immune)-Deficiency Syndrome; ÈÄõ¼º ¸é¿ª °áÇÌ ÁõÈıº
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 2
P-450c17 P-450 17alpha-hydroxylase-C17,20 lyase
PL Pectate lyase
Pel Pectate lyase
PFL Pyruvate formate lyase
TPL Tyrosine phenol-lyase
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
  • ¿µ¹®
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    ¼³¸í
  • erythropoietin deficiency anemia
    ¿¡¸®Æ®·ÎÆ÷¿¡Æ¾ °áÇ̼º ºóÇ÷, ÀûÇ÷±¸ Á¶Ç÷ ÀÎÀÚ °áÇ̼º ºóÇ÷
  • factor deficiency
    ÀÎÀÚ °áÇÌ, Á¦ÀÎÀÚ °áÇÌÁõ
  • factor IX deficiency
    Á¦ 9ÀÎÀÚ °áÇÌÁõ, Á¦9ÀÎÀÚ °áÇÌ
  • factor VII deficiency
    Á¦ 7ÀÎÀÚ °áÇÌÁõ
  • factor VIII deficiency
    Á¦ 8ÀÎÀÚ °áÇÌ
  • factor XI deficiency
    Á¦11ÀÎÀÚ °áÇÌ
    ÀÌ ÀÎÀÚ°¡ ºÎÁ·µÇ¸é Ç÷¿ìº´ C³ª Rosenthal ÁõÈıºÀ¸·Î ºÒ¸®´Â Àü½Å¼º Ç÷¾× ÀÀ°í Àå¾Ö¸¦ ÀÏÀ¸Å°´Âµ¥ °íÀüÀû Ç÷¿ìº´°ú À¯»çÇÏ´Ù.
  • folate deficiency anemia
    ¿±»ê °áÇ̼º ºóÇ÷
  • folic acid deficiency anemia
    ¿±»ê °áÆð¼º ºóÇ÷
  • fructokinase deficiency
    ÇÁÁ¦ °áÇÌ
  • hexokinase deficiency
    Çí¼ÒŰ³ªÁ¦ °áÇÌ
  • immune deficiency disease
    ¸é¿ª °áÇÌ Áúȯ, ¸é¿ª °áÇ̺´
    ¸é¿ª °èÅëÀ» ±¸¼ºÇÏ´Â ¿ä¼ÒÀÇ ±â´É Àå¾Ö¿¡ ÀÇÇÏ¿© ÃÊ·¡µÇ´Â Áúȯ ±º.
  • immunity deficiency
    ¸é¿ª °áÇÌ
    µ¿ÀǾî=immunodeficiency.
  • immunological deficiency state
    ¸é¿ª °áÇÌ »óÅÂ
  • iron deficiency anemia
    ö °áÇ̼º ºóÇ÷
    1. Àú»ö¼Ò¼º, ¼Ò±¸¼º ÀûÇ÷±¸¼º ºóÇ÷ÀÇ ´ëÇ¥Àû Áúȯ. öÀÇ °áÇÌ¿¡ ÀÇÇÏ¿© Ç÷»ö¼ÒÀÇ »ý¼ºÀÌ ÃæºÐÈ÷ ÇàÇÏ¿©ÁöÁö ¾Ê±â ¶§¹®¿¡ ÀûÇ÷±¸ ¼öº¸´Ùµµ Ç÷»ö¼Ò ³óµµ°¡ ÇöÀúÇÏ°Ô °¨¼ÒÇÑ´Ù. 2. ö ÀúÀå·®ÀÇ ÀúÇÏ, °áÇÌ, Ç÷û ö ³óµµÀÇ ÀúÇÏ, transferrin¾ç »ó½Â, transferrin Æ÷È­µµÀÇ ÀúÇÏ, Àú»ö¼Ò¼º ´ëÀûÇ÷±¸¸¦ Ư¡À¸·Î ÇÏ´Â ºóÇ÷.
  • isolated T-cell deficiency
    T ¼¼Æ÷ °áÇÌ
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
mandelonitrile lyase <enzyme> Catalyses the reversible condensation of hcn with aldehydes to form d-alpha-hydroxynitriles; contains fad
Registry number: EC 4.1.2.10
Synonym: mandelonitrile benzaldehyde-lyase, oxynitrilase
(26 Jun 1999)
gellan lyase <enzyme> Cleaves beta-d-glucosyl-1-4-beta-d-glucuronosyl sequence in gellan
Registry number: EC 4.2.2.-
Synonym: gellanase
(26 Jun 1999)
glucuronan lyase <enzyme> Catalyses beta-elimination cleavage of acetylated and deacetylated (1->4)-beta-d-glucuronan
Registry number: EC 4.2.2.-
(26 Jun 1999)
pectin lyase <enzyme> Catalyses elimination of 6-methyl-delta-4,5-galacturonate residues from pectin; brings about depolymerization of pectin; does not act on deesterified pectin
Registry number: EC 4.2.2.10
Synonym: poly(methoxygalacturonide)lyase, protopectinase-r, ppase-r, pnla protein, pnla gene product, psx1 gene product, polymethoxygalacturonase
(26 Jun 1999)
peptidylamidoglycolate lyase <enzyme> Second step in the production of alpha-amidated peptides from their glycine-extended precursors; first step is EC 1.14.17.3 (amide synthetase)
Registry number: EC 4.3.2.5
Synonym: pahgaa lyase, peptidyl-alpha-hydroxyglycine alpha amidating lyase, peptidylhydroxyglycine n-c lyase
(26 Jun 1999)
chondroitin abc lyase <enzyme> An enzyme that catalyses the eliminative degradation of polysaccharides containing 1,4-beta-d-hexosaminyl and 1,3-beta-d-glucuronosyl or 1,3-alpha-l-iduronosyl linkages to disaccharides containing 4-deoxy-beta-d-gluc-4-enuronosyl groups. (enzyme nomenclature, 1992)
Chemical name: chondroitin ABC lyase
Registry number: EC 4.2.2.4
(12 Dec 1998)
chorismate pyruvate-lyase <enzyme> Forms 4-hydroxybenzoic acid for ubiquinone biosynthesis; chorismate pyruvate-lyase (amino-accepting) is anthranilate synthase
Registry number: EC 4.1.3.-
Synonym: ubic gene product, chorismate lyase
(26 Jun 1999)
phenylalanine ammonia lyase <enzyme> An enzyme that catalyses the deamination of l-phenylalanine to form trans-cinnamate and ammonia. It may also act on l-tyrosine. Since the enzyme deprives neoplastic tissue of phenylalanine, it has been used experimentally in the treatment of acute lymphoblastic leukaemia. The enzyme is obtained from many plants and is used as an enzymic marker for lignification and other developmental processes in plant cells.
Pharmacological action: antineoplastic agent.
Chemical name: L-Phenylalanine ammonia-lyase
Registry number: EC 4.3.1.5
(12 Dec 1998)
citrate lyase Citrate (pro-3S)-lyase;an enzyme that catalyses the cleavage of citrate to oxaloacetate and acetate, in the absence of coenzyme A.
Synonym: citrase, citratase, citrate aldolase, citridesmolase.
(05 Mar 2000)
citrate (pro-3S)-lyase <enzyme> Consists of two enzymes and an acyl carrier protein
Registry number: EC 4.1.3.6
Synonym: citrate lyase
(26 Jun 1999)
citrate (pro-3S)-lyase deacetylase <enzyme> Catalyses conversion of enzymatically active acetyl-s-citrate lyase (4.1.3.6) into inactive hs-form and acetate
Registry number: EC 3.1.2.-
Synonym: citrate lyase deacetylase
(26 Jun 1999)
citrate (pro-3S)-lyase ligase <enzyme> Deacetylcitrate lyase, acetate and ATP forms citrate lyase, AMP, pi
Registry number: EC 6.2.1.22
Synonym: citc gene product, acetate-sh-citrate lyase ligase, citrate lyase ligase
(26 Jun 1999)
phycocyanin alpha-subunit phycocyanobilin lyase <enzyme> Cleaves thioether bond attaching phycocyanobilin to the alpha subunit of phycocyanin; product of the cpce and cpcf genes of synechococcus
Registry number: EC 4.4.-
Synonym: phycocyanobilin lyase
(26 Jun 1999)
phycoerythrocyanin alpha-subunit phycobiliviolin lyase <enzyme> Shows high degree of homology to phycocyanobilin lyase
Registry number: EC 4.4.-
Synonym: phycobiliviolin lyase, pece protein, pecf protein, pec alpha-subunit phycobiliviolin lyase
(26 Jun 1999)
poly(beta-D-mannuronate) lyase <enzyme> Amino acid sequence has been determined for sp1 and sp2 isoenzymes from midgut of wreath shell, turbo cornutus
Registry number: EC 4.2.2.3
Synonym: poly(1,4-beta-d-mannuronide)lyase, alginate lyase I, alginate lyase, aly gene product, mannuronate lyase sp1, mannuronate lyase sp2
(26 Jun 1999)
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