| UDP-N-acetylglucosamine-galactose(1-6)-N-acetylglucosaminyltransferase | <enzyme> Forms oligosaccharide core class 4(glcnac beta 1-3(glcnac beta 1-6)galnac) in mucins and various glycoproteins Registry number: EC 2.4.1.148 Synonym: udp-nagagf (26 Jun 1999) |
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| UDP-N-acetylglucosamine-lysosomal-enzyme-N-acetylglucosaminephosphotransferase | <enzyme> Fibroblasts from patients with i-cell (mucolipidosis II) and pseudo-hurler polydystrophy (mucolipidosis III) are deficient in above enzyme; for n-acetylglucosamine transferred to dolichyl phosphate see EC 2.7.8.15 Registry number: EC 2.7.8.17 Synonym: udpgnac gp gnac phosphotransferase, udpgnac phosphotransferase, uridine 5'-diphosphate-n-acetylglucosamine glycoprotein n-acetylglucosaminylphosphotransferase, n-acetylglucosamine-1-phosphotransferase, n-agapt, udp-n-acetylglucosamine-lysosomal glycoprotein n-acetylglucosaminylphosphotransferase, udp-acetylglucosamine-glycoprotein n-acetylglucosamine-1-phosphotransferase (26 Jun 1999) |
| UDP-N-acetylglucosamine:lysosomal enzyme N-acetylglucosaminyl-1-phosphotransferase | <enzyme> An enzyme that participates in the posttranslational modification of a number of lysosomal proteins; a deficiency or defect in this enzyme results in two forms of mucolipidoses, I-cell disease, and pseudo-Hurler polydystrophy. (05 Mar 2000) |
| UDP-N-acetylglucosamine-peptide beta-N-acetylglucosaminyltransferase | <enzyme> Responsible for the addition of o-linked n-acetylglucosamine to proteins Registry number: EC 2.4.1.- Synonym: udp-glcnac-peptide-glcnac-transferase, glcnac transferase (26 Jun 1999) |
| uridine diphosphate n-acetylglucosamine | <chemical> Serves as the biological precursor of insect chitin, of muramic acid in bacterial cell walls, and of sialic acids in mammalian glycoproteins. Chemical name: Uridine 5'-(trihydrogen diphosphate), P'-(2-(acetylamino)-2-deoxy-alpha-D-glucopyranosyl) ester (12 Dec 1998) |