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"Deficiency, phenylalanine hydroxylase"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
  • functional deficiency
    ±â´É°áÇÌ
  • histogenetic deficiency
    Á¶Á÷¹ß»ý°áÇÌ
  • immune deficiency
    (¢¡immunodeficiency) ¸é¿ª°áÇÌ
  • latent deficiency
    ÀáÀç°áÇÌÁõ
  • leukocyte adhesion deficiency
    ¹éÇ÷±¸ºÎÂø°áÇÌÁõ
  • mental deficiency
    Á¤½Å¹Ú¾à
  • milk dietary deficiency
    ¿ìÀ¯¿µ¾çÀå¾Ö
  • mineral deficiency
    ¹«±âÁú°áÇÌ(Áõ)
  • nutritional deficiency disease
    ¿µ¾ç°áÇ̺´
  • thyroid hormone deficiency
    ¹æÆÐ»ùÈ£¸£¸ó°áÇÌ, °©»ó»ùÈ£¸£¸ó°áÇÌ
  • vitamin deficiency
    ºñŸ¹Î°áÇÌ(Áõ)
  • electrolyte deficiency syndrome
    ÀüÇØÁú°áÇÌÁõÈıº
  • immunologic deficiency state
    ¸é¿ª°áÇÌ»óÅÂ
  • nutritional deficiency state
    ¿µ¾ç°áÇÌ»óÅÂ
  • nutritional deficiency syndrome
    ¿µ¾ç°áÇÌÁõÈıº
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
  • Folate deficiency
    ¿±»ê°áÇÌÁõ(ç¨ß«ÌÀù¹ñø)
  • Iodine deficiency
    ¿äµå °áÇÌÁõ(ÌÀù¹ñø)
  • Iron deficiency anemia
    ö°áÇ̼ººóÇ÷(ôÑÌÀù¹àõÞ¸úì)
  • Rh deficiency syndrome
    Rh °áÇÌÁõÈıº
  • T cell deficiency
    T¼¼Æ÷°áÇÌ
  • abdominal muscle deficiency syndrome
    º¹±Ù°á¼ÕÁõÈıº(ÜÙÐÉÌÀáßñøý¦ÏØ).
  • acid lipase deficiency
    »ê¼º ¸®ÆÄÁ¦ °áÇÌÁõ(ß«àõ¡­ÌÀù¹ñø)
  • acquired immune deficiency
    ÈÄõ¼º ¸é¿ª°áÇÌ
  • acquired immune deficiency syndrome
    ÈÄõ¼º ¸é¿ª°áÇÌ ÁõÈıº
  • acquired immune deficiency syndrome
    ÈÄõ¼º ¸é¿ª°áÇÌÁõÈıº(ý­ô¸àõ Øóæ¹ÌÀù¹ñøý¦ÏØ)
  • adenosine,deficiency
    °áÇÌÁõ(ÌÀù¹ñø)
  • adrenocortical deficiency
    ºÎ½ÅÇÇÁú°áÇÌÁõ.
  • aids=£¾acquired immune deficiency syndrome
    ÈÄõ¼º¸é¿ª°áÇÌÁõÈıº(ý­ô¸àõØóæ¹ÌÀù¹ñøý¦ÏØ)
  • alimentary deficiency =dietary d.
    ½Ä»çºÎÁ·, ¿µ¾çºÎÁ·.
  • anemia iron deficiency
    ö°áÇ̼º ºóÇ÷.
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
  • aids=£¾acquired immune deficiency syndrome
    ÈÄõ¼º¸é¿ª°áÇÌÁõÈıº(ý­ô¸àõØóæ¹ÌÀù¹ñøý¦ÏØ)
  • alimentary deficiency =dietary d.
    ½Ä»çºÎÁ·, ¿µ¾çºÎÁ·.
  • alpha antitrypsin deficiency panniculitis
    ¾ËÆÄ Çׯ®¸³½Å°áÇÌÁö¹æÃþ¿°
  • anemia iron deficiency
    ö°áÇ̼º ºóÇ÷.
  • anemia,folate deficiency
    ¿±»ê°áÇÌ(ç¨ß«ÌÀù¹)
  • anterior pituitary deficiency
    ³úÇϼöüÀü¿±±â´ÉºÎÀü(Áõ)
  • anterior pituitary deficiency
    ÇϼöüÀü¿±±â´ÉºÎÀü(Áõ).
  • antibody deficiency syndrome
    Ç×ü°áÇÌÁõÈıº(ù÷ô÷ÌÀù¹ñøý¦ÏØ).
  • antitrypsin deficiency
    Çׯ®¸³½Å°áÇÌ
  • apolipoprotein C-Il deficiency
    ¾ÆÆ÷Áö´Ü¹é C-II °áÇÌ
  • apolipoprotein b, deficiency
    ¾ÆÆ÷¸®Æ÷´Ü¹éB°áÇÌÁõ(¡­Ó±ÛÜ¡­ÌÀù¹ñø)
  • arylsulfatase a deficiency
    ¾Æ¸±¼³ÆÄŸÁ¦ A °áÇÌÁõ(¡­ÌÀù¹ñø)
  • aspartylglycosamine amide hydrolase, deficiency
    Aspartylglycosamine amide hydrolase°áÇÌ(¡­ÌÀù¹)
  • biotin-deficiency
    ¹ÙÀÌ¿Àƾ°áÇÌÁõ (¡­ÌÀù¹ñø).
  • biotin-deficiency
    ¹ÙÀÌ¿Àƾ°áÇÌÁõ (¡­ÌÀù¹ñø)
´ëÇÑÇØºÎÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 2
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    ÇѱÛ
  • Cytogenetic deficiency
    ¼¼Æ÷¹ß»ý°áÇÌ
    [¿¾ ¿ë¾î] ¼¼Æ÷¹ß»ý°áÇÌ
  • Stimulus deficiency
    ÀڱذáÇÌ
    [¿¾ ¿ë¾î] ÀڱذáÇÌ
  • Histogenetic deficiency
    Á¶Á÷¹ß»ý°áÇÌ
    [¿¾ ¿ë¾î] Á¶Á÷¹ß»ý°áÇÌ
  • Synthesis deficiency
    ÇÕ¼º°áÇÌ
    [¿¾ ¿ë¾î] ÇÕ¼º°áÇÌ
  • Hormone deficiency
    È£¸£¸ó°áÇÌ
    [¿¾ ¿ë¾î] È£¸£¸ó°áÇÌ
´ëÇÑ»ýÈ­ÇкÐÀÚ»ý¹°ÇÐȸ ¿ë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 2 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
  • simian acquired immune deficiency syndrome
    ¿ø¼þÀÌ ÈÄõ¼º¸é¿ª°áÇÌÁúȯ(ý­ô¸àõØóæ¹ÌÀù¹òðü´)
  • sulfite oxidase deficiency
    ¾ÆÈ²»ê(ä¬üÜß«) ¿Á½Ãµ¥À̽º °áÇÌ(ÌÀù¹)
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 2
TH tension headache; tetrahydrocortisol; T helper [cell]; theophylline; thorax; thrill; thyrohyoid; thy...
TPH transplacental hemorrhage; tryptophan hydroxylase
IGD idiopathic growth hormone deficiency; interglobal distance; isolated gonadotropin deficiency
MCD magnetic circular dichroism; mast-cell degranulation; mean cell diameter; mean of consecutive differ...
CGP N-carbobenzoxy-glycyl-L-phenylalanine; chorionic growth hormone-prolactin; choline glycerophosphatid...
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 2
PAL L-Phenylalanine ammonia-lyase
L-PAM L-Phenylalanine mustard
L-Phe L-phenylalanine
PME L-phenylalanine methyl ester
TPCK N,alpha-tosyl-L-phenylalanine chloromethyl ketone
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • factor IX deficiency
    Á¦ 9ÀÎÀÚ °áÇÌÁõ, Á¦9ÀÎÀÚ °áÇÌ
  • factor VII deficiency
    Á¦ 7ÀÎÀÚ °áÇÌÁõ
  • factor VIII deficiency
    Á¦ 8ÀÎÀÚ °áÇÌ
  • factor XI deficiency
    Á¦11ÀÎÀÚ °áÇÌ
    ÀÌ ÀÎÀÚ°¡ ºÎÁ·µÇ¸é Ç÷¿ìº´ C³ª Rosenthal ÁõÈıºÀ¸·Î ºÒ¸®´Â Àü½Å¼º Ç÷¾× ÀÀ°í Àå¾Ö¸¦ ÀÏÀ¸Å°´Âµ¥ °íÀüÀû Ç÷¿ìº´°ú À¯»çÇÏ´Ù.
  • folate deficiency anemia
    ¿±»ê °áÇ̼º ºóÇ÷
  • folic acid deficiency anemia
    ¿±»ê °áÆð¼º ºóÇ÷
  • fructokinase deficiency
    ÇÁÁ¦ °áÇÌ
  • hexokinase deficiency
    Çí¼ÒŰ³ªÁ¦ °áÇÌ
  • immune deficiency disease
    ¸é¿ª °áÇÌ Áúȯ, ¸é¿ª °áÇ̺´
    ¸é¿ª °èÅëÀ» ±¸¼ºÇÏ´Â ¿ä¼ÒÀÇ ±â´É Àå¾Ö¿¡ ÀÇÇÏ¿© ÃÊ·¡µÇ´Â Áúȯ ±º.
  • immunity deficiency
    ¸é¿ª °áÇÌ
    µ¿ÀǾî=immunodeficiency.
  • immunological deficiency state
    ¸é¿ª °áÇÌ »óÅÂ
  • iron deficiency anemia
    ö °áÇ̼º ºóÇ÷
    1. Àú»ö¼Ò¼º, ¼Ò±¸¼º ÀûÇ÷±¸¼º ºóÇ÷ÀÇ ´ëÇ¥Àû Áúȯ. öÀÇ °áÇÌ¿¡ ÀÇÇÏ¿© Ç÷»ö¼ÒÀÇ »ý¼ºÀÌ ÃæºÐÈ÷ ÇàÇÏ¿©ÁöÁö ¾Ê±â ¶§¹®¿¡ ÀûÇ÷±¸ ¼öº¸´Ùµµ Ç÷»ö¼Ò ³óµµ°¡ ÇöÀúÇÏ°Ô °¨¼ÒÇÑ´Ù. 2. ö ÀúÀå·®ÀÇ ÀúÇÏ, °áÇÌ, Ç÷û ö ³óµµÀÇ ÀúÇÏ, transferrin¾ç »ó½Â, transferrin Æ÷È­µµÀÇ ÀúÇÏ, Àú»ö¼Ò¼º ´ëÀûÇ÷±¸¸¦ Ư¡À¸·Î ÇÏ´Â ºóÇ÷.
  • isolated T-cell deficiency
    T ¼¼Æ÷ °áÇÌ
  • lactase deficiency
    ¶ôŸÁ¦ °áÇÌ
  • mental deficiency
    Áö´É ¹Ú¾à, Áö´É ¹Ú¾àÁõ, Á¤½Å ¹Ú¾àÁõ
    ¿©·¯ °¡Áö ¿øÀο¡ ÀÇÇØ¼­ Áö´É ¹ß´ÞÀÌ Æò±Õº¸´Ù ³·°í Á¤½ÅÀû, ½ÅüÀû Àå¾Ö·Î ÀÎÇØ »çȸ »ýȰ¿¡ ´ëÇÑ ÀûÀÀÀÌ °ï¶õÇÑ »óÅÂ. Á¤½Å Áöü¶ó°íµµ ÇÑ´Ù. Çö´ë ÀÇÇп¡¼­´Â ÁøÇ༺ ¸¶ºñ¿¡ ÀÇÇÑ Ä¡¸Å³ª ÀϽÃÀûÀÎ Á¤½Å ±â´ÉÀÇ ÅðÇà°ú ±¸º°ÇÏ¿© Ç×±¸ÀûÀÎ Áöü »óŸ¦ ÀǹÌÇÑ´Ù. ¶ÇÇÑ ÀÏ¹Ý Áö´ÉÀÇ °áÇÔ¸¸ÀÌ ¾Æ´Ï¶ó '»çȸ »ýȰ¿¡¼­ÀÇ ½ÇõÀû Áö´É'À̶ó ºÎ¸¦ ¸¸ÇÑ Ãø¸é¿¡µµ ÁÖ¸ñÇÏ°Ô µÇ¸é¼­ Á¤½Å ¹Ú¾àÀÇ ºÐ·ù´Â »çȸÀÇ ÀûÀÀµµ¿Í »çȸÀû »ýȰ ´É·Â Á¤µµ¸¦ ¹èÇÕ½ÃŰ°Ô µÇ¾ú´Ù.
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 2
aniline hydroxylase <enzyme> A drug-metabolizing, cytochrome p-450 enzyme which catalyses the hydroxylation of aniline to hydroxyaniline in the presence of reduced flavoprotein and molecular oxygen.
Registry number: EC 1.14.14.-
(12 Dec 1998)
arachidonic acid 18-hydroxylase <enzyme> Converts arachidonic acid to 18-hydroxy-5,8,11,14-eicosatetraenoic acid in the presence of NADPH; cytochrome p450 enzyme
Registry number: EC 1.14.13.-
Synonym: arachidonic acid 18(r)-hydroxylase, arachidonic acid omega 3-hydroxylase
(26 Jun 1999)
arylamine N-hydroxylase <enzyme> Cytochrome p-448 dependent
Registry number: EC 1.14.13.-
Synonym: 2-aminofluorene n-hydroxylase
(26 Jun 1999)
benzopyrene hydroxylase <enzyme> A drug-metabolizing, cytochrome p-448 (p-450) enzyme which catalyses the hydroxylation of benzopyrene to 3-hydroxybenzopyrene in the presence of reduced flavoprotein and molecular oxygen. Also acts on certain anthracene derivatives.
Registry number: EC 1.14.14.-
(12 Dec 1998)
beta-carotene hydroxylase <enzyme> O2-dependent NADPH-dependent monooxygenase from erwinia herbicola; forms zeaxanthin; amino acid sequence has been determined; genbank m87280
Registry number: EC 1.14.13.-
Synonym: beta-carotene monooxygenase, crtz gene product
(26 Jun 1999)
biphenyl-4-hydroxylase <enzyme> Mixed function oxidase
Registry number: EC 1.14.14.-
(26 Jun 1999)
bufuralol 1'-hydroxylase <enzyme> Liver microsomal enzyme utilizing NADPH and cytochrome p-450; competetive inhibition by debrisoquine
Registry number: EC 1.14.99.-
Synonym: bufuralol 1'-monooxygenase
(26 Jun 1999)
bunitrolol 4-hydroxylase <enzyme> Mediated by cytochrome p-450; catalyses the hydroxylation of bunitrolol
Registry number: EC 1.14.99.-
(26 Jun 1999)
camphor-6-exo-hydroxylase <enzyme> A cytochrome p-450-dependent monooxygenase that catalyses the hydroxylation of camphor to 6-hydroxycamphor in sage and mycobacterium
Registry number: EC 1.14.15.-
(26 Jun 1999)
vanillate 1-hydroxylase <enzyme> Catalyses the oxidative decarboxylation of vanillic acid to 2-methoxyhydroquinone
Registry number: EC 1.14.13.-
(26 Jun 1999)
geraniol 10-hydroxylase <enzyme> Catalyses the conversion of geraniol to 10-hydroxygeraniol; a cytochrome p-450 enzyme
Registry number: EC 1.14.-
(26 Jun 1999)
gibberellin 2beta, 3beta-hydroxylase <enzyme> Bifunctional enzyme from pumpkin endosperm; catalyses all 3 beta hydroxylations of c19 and c20 gibberillins and all 2 beta hydroxylations of c20 gibberellins; genbank u63650
Registry number: EC 1.14.99.-
Synonym: cm3h gene product, ga 2beta, 3beta-hydroxylase
(26 Jun 1999)
gibberellin 3beta-hydroxylase <enzyme> Product of le (stem length) gene of pea (pisum sativum) described by mendel; genbank u93210
Registry number: EC 1.14.99.-
Synonym: ga4 gene product, le gene product, ga 3beta-hydroxylase
(26 Jun 1999)
cephalosporin 7-alpha-hydroxylase <enzyme> A dioxygenase from streptomyces clavuligerus; requires 2-oxoglutarate, fe2+ and a reducing agent such as ascorbic acid
Registry number: EC 1.14.11.-
(26 Jun 1999)
pentachlorophenol hydroxylase <enzyme> Catalyses the conversion of pcp to 2,3,4,5-tetrachlorohydroquinone in the presence of NADPH and oxygen; flavoprotein from flavobacterium sp. Strain atcc 39723
Registry number: EC 1.14.13.-
Synonym: pcp hydroxylase, pcp-4-monooxygenase, pcpb gene product, pentachlorophenol-4-monooxygenase
(26 Jun 1999)
ÀÌ ¾Æ·¡ ºÎÅÍ´Â °á°ú°¡ ¾ø½À´Ï´Ù.
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