| 3-methylcrotonylglycine |
a conjugate of 3-methylcrotonic acid and glycine, formed and excreted in excess in the urine when 3-methylcrotonoyl-CoA carboxylase activity is impaired.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| 3-methylglutaconic acid |
a dicarboxylic acid occurring at elevated levels in 3-methylglutaconicaciduria and 3-hydroxy-3-methylglutaricaciduria.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| 3-methylglutaconicaciduria |
an aminoacidopathy characterized by excessive urinary excretion of 3-methylglutaconic acid and occurring in two forms. A mild form caused by deficiency of methylglutaconyl-CoA hydratase is characterized by speech retardation; a more severe form, of unknown etiology, is characterized by urinary excretion also of 3-methylglutaric acid and by progressive neurologic deterioration with hypotonia and optic atrophy.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| 3-methylglutaconyl |
a radical of 3-methylglutaconic acid; the thioester formed with coenzyme A, 3-methylglutaconyl CoA, is an intermediate in the catabolism of leucine.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| 3-methylglutaric acid |
a dicarboxylic acid occurring at elevated levels in the urine in one form of 3-methylglutaconicaciduria and in 3-hydroxy-3-methylglutaricaciduria.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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