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"multiple acyl CoA dehydrogenation deficiency"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
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  • milk dietary deficiency
    ¿ìÀ¯¿µ¾çÀå¾Ö(¡­ç½å×î¡äô).
  • mineral deficiency
    ¹«±âÁú°áÇÌ(Áõ)(ÙíѦòõÌÀù¹ñø).
  • myeloperoxidase deficiency
    ¸¶¿¡·ÎÆÛ¿Á½Ãµ¥À̽º °áÇÌ(¡­ ÌÀù¹)
  • niacin deficiency
    ³ªÀ̾ƽаáÇÌ
  • niacin, deficiency
    ³ªÀ̾ƽаáÇÌÁõ(¡­ ÌÀù¹ñø)
  • nutrition deficiency
    ¿µ¾ç°áÇÌÁõ.
  • nutritional deficiency
    ¿µ¾ç°áÇÌ(~ÌÀù¹).
  • nutritional deficiency disease
    ¿µ¾ç°áÇÌÁõ(~ÌÀù¹ñø).
  • nutritional deficiency state
    ¿µ¾ç°áÇÌ»óÅ (~ßÒ÷¾).
  • nutritional deficiency syndrome
    ¿µ¾ç°áÇÌÁõÈıº(~ñøý¦ÏØ).
  • organ deficiency
    ±â°üÀÌÁÖ°áÇÌ
  • organ deficiency (cryptorchidism)
    ±â°üÀÌÁÖ°áÇÌ (°íȯÀẹÁõ)
  • organogenetic deficiency
    ±â°ü¹ß»ý°áÇÌ
  • organogenetic deficiency
    organogenetic deficiency
  • oxygen deficiency =o. want, o. lack, o. deprivation, o. depletion
    »ê¼ÒºÎÁ·(¡­ÝÕðë), »ê¼Ò°áÇÌ(ß«áÈÌÀù¹).
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SID single intradermal [test]; Society for Investigative Dermatology; sucrase-isomaltase deficiency; sud...
SPD schizotypal personality disorder; sociopathic personality disorder; specific paroxysmal discharge; s...
SSDD steroid sulfatase deficiency disease
SYDS stomach yin deficiency syndrome
TD tabes dorsalis; tardive dyskinesia; T-cell dependent; temporary disability; terminal device; tetanus...
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LCHAD Long chain 3-hydroxyacyl-CoA-dehydrogenase
MCD Malonyl CoA decarboxylase
MCM Methylmalonyl CoA mutase
PCC Propionyl CoA carboxylase
SCD Stearoyl CoA desaturase
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 19
acetyl-CoA deacylase <enzyme> An enzyme that catalyses reversibly the hydrolysis of acetyl-CoA to yield CoA and acetate. The enzyme is involved in the oxidation of fatty acids.
Chemical name: Acetyl-CoA hydrolase
Registry number: EC 3.1.2.1
(12 Dec 1998)
acetyl-CoA hydrolase <enzyme> An enzyme that catalyses reversibly the hydrolysis of acetyl-CoA to yield CoA and acetate. The enzyme is involved in the oxidation of fatty acids.
Chemical name: Acetyl-CoA hydrolase
Registry number: EC 3.1.2.1
(12 Dec 1998)
acetyl-CoA ligase A ligase that catalyses the reaction of acetate and CoA and ATP to form AMP, pyrophosphate, and acetyl-CoA. A key step in the activation of acetate.
Synonym: acetate thiokinase, acetate-CoA ligase, acetyl-activating enzyme, acetyl-CoA synthetase.
(05 Mar 2000)
acetyl-CoA - lysine N6-acetyltransferase <enzyme> First step in catabolism of lysine by saccharomyces cerevisiae
Registry number: EC 2.3.1.-
Synonym: accoa lysine acetyltransferase, lysine n-6-acetyltransferase, lyc1 gene product
(26 Jun 1999)
acetyl-CoA synthetase A ligase that catalyses the reaction of acetate and CoA and ATP to form AMP, pyrophosphate, and acetyl-CoA. A key step in the activation of acetate.
Synonym: acetate thiokinase, acetate-CoA ligase, acetyl-activating enzyme, acetyl-CoA synthetase.
(05 Mar 2000)
acetyl-CoA thiolase An acetyltransferase forming acetoacetyl-CoA from two molecules of acetyl-CoA, releasing one CoA. A key step in ketogenesis and sterol synthesis.
Synonym: acetoacetyl-CoA thiolase, acetyl-CoA thiolase, thiolase.
(05 Mar 2000)
acryloyl-CoA reductase <enzyme> Clostridium kluyveri enzyme; contains fmn, ferredoxin, and flavodoxin; can act as electron donors
Registry number: EC 1.3.99.-
Synonym: acryloyo-coenzyme a reductase
(26 Jun 1999)
alpha-methylacyl-CoA racemase <enzyme> Involved in catabolism of branched-chain fatty acids derived from isoprenoids; acts on pristanoyl-CoA and trihydroxycoprostanoyl-CoA, but not on 3-methyl branched-chain or linear-chain acyl coas; amino acid sequence has been determined; genbank u89905 (rat) and u89906 (mouse); also isolated from human liver
Registry number: EC 5.1.99.-
Synonym: meac CoA racemase
(26 Jun 1999)
aralkyl-CoA-glycine N-acyltransferase <enzyme> Involved in conjugation of xenobiotics such as substituted benzoic acids or medium chain fatty-acyl-coas with glycine; n-terminal amino acid sequence given in first source
Registry number: EC 2.3.1.-
Synonym: aralkyltransferase, aralkyl-CoA-glycine n-glycyltransferase
(26 Jun 1999)
arylacetyl-CoA N-acetyltransferase <enzyme> Conjugates arylacetic acid derivatives with glycine, glutamine or arginine
Registry number: EC 2.3.1.-
Synonym: arylacetyl-CoA-amino acid n-acyltransferase
(26 Jun 1999)
benzoyl-CoA 3-monooxygenase <enzyme> A fad-dependent hydroxylase that hydroxylates benzoyl-CoA to 3-hydroxybenzoyl-CoA; mw 130 kD (composed of two identical subunits of 56 kD); from denitrifying pseudomonas sp.
Registry number: EC 1.14.13.-
Synonym: benzoyl-coenzyme a 3-monooxygenase
(26 Jun 1999)
benzoyl-CoA-anthranilate N-benzoyltransferase <enzyme> Specific for anthranilate; almost no activity towards 4-hydroxyanthranilate; involved in phytoalexin biosyntesis
Registry number: EC 2.3.1.-
Synonym: b-CoA-anb transferase, benzoyl-coenzyme a-anthranilate n-benzoyltransferase
(26 Jun 1999)
beta-hydroxy-beta-methylglutaryl-CoA -OOCCH2C(OH)(CH3)CH2COS-CoA;a key intermediate in the synthesis of ketone bodies and of steroids.
Synonym: 3-hydroxy-3-methylglutaryl-CoA.
Beta-hydroxy-beta-methylglutaryl-lyase, an enzyme, found primarily in liver and rumen epithelium that catalyses the formation of acetyl-CoA and acetoacetate from beta-hydroxy-beta-methylglutaryl-CoA; a key step in ketogenesis; a deficiency of this enzyme leads to episodes of severe metabolic acidosis without ketosis.
Beta-hydroxy-beta-methylglutaryl-reductase, an enzyme that catalyses the rate-limiting step of cholesterol biosynthesis, beta-hydroxy-beta-methylglutaryl-CoA + 2NADPH + 2H+ &rarr; mevalonate + 2NADP+ + coenzyme A.
Beta-hydroxy-beta-methylglutaryl-synthase, an enzyme in mitochondria that catalyses the reaction of acetyl-CoA with acetoacetyl-CoA and water to form beta-hydroxy-beta-methylglutaryl-CoA and coenzyme A, a step required for both ketogenesis and steroidogenesis to occur.
(05 Mar 2000)
bile acid-CoA ligase <enzyme> Catalyses the synthesis of all bile acid-coas; in order to measure the activity of all bile acids, the bile acid is coupled with c(14)-glycine and measured with bile acid-CoA glycine-taurine n-acetyltransferase
Registry number: EC 6.2.1.-
(26 Jun 1999)
butyrate-CoA ligase Fatty acid thiokinase (medium chain), a ligase forming acyl-CoA's from medium-chain fatty acids and CoA with the conversion of ATP to AMP and PPi. A key step in activation of fatty acids.
Synonym: acyl-activating enzyme, butyryl-CoA synthetase, octanoyl-CoA synthetase.
(05 Mar 2000)
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