| cystathionine beta-lyase | <enzyme> An enzyme catalyzing the hydrolysis of l-cystathionine to pyruvate, l-homocysteine, and NH3. See: cystathionine gamma-lyase. Synonym: beta-cystathionase, cystine lyase. (05 Mar 2000) |
|---|---|
| cystathionine beta-synthase | <enzyme> A multifunctional pyridoxal phosphate enzyme. In the second stage of cysteine biosynthesis it catalyses the reaction of homocysteine with serine to form cystathionine with the elimination of water. Chemical name: L-Serine hydro-lyase (adding homocysteine) Registry number: EC 4.2.1.22 (12 Dec 1998) |
| progesterone 5 beta-reductase | <enzyme> A stereospecific enzyme; forms 5 beta-pregnane-3,20-dione from progesterone; see also progesterone 5 alpha-reductase Registry number: EC 1.3.1.- (26 Jun 1999) |
| proline-beta-naphthylamidase | <enzyme> From pig intestinal mucosa; hydrolyzes proline-beta-naphthylamidase; distinct from proline aminopeptidase; inhibited by active site serine-specific protease inhibitors Registry number: EC 3.4.11.- Synonym: pro-naphthylamidase (26 Jun 1999) |
| xyloglucan 4-beta-D-glucosyltransferase | <enzyme> Catalyses formation of xyloglucan from udp-glucose Registry number: EC 2.4.1.- Synonym: xylo-glctransferase, xyloglucan glucosyltransferase (26 Jun 1999) |
| xyloglucan endo(1-4)-beta-D-glucanase | <enzyme> Hydrolyzes only xyloglucans Registry number: EC 3.2.1.- Synonym: xyloglucanase (26 Jun 1999) |
| xylosylprotein 4-beta-galactosyltransferase | <enzyme> Catalyses the second glycosyl transfer reaction in the assembly of the dermatan sulfate chain Registry number: EC 2.4.1.133 Synonym: galactosyltransferase i (26 Jun 1999) |
| short-chain beta-hydroxyacyl-CoA dehydrase | <enzyme> Forms trans-2-enoyl-CoA; maximal activity with trans-2-hexenoyl-CoA, followed by crotonyl-CoA; not the same as EC 4.2.1.17 Registry number: EC 4.2.1.- Synonym: beta-hydroxybutyryl-CoA dehydrase, short-chain beta-hydroxyacyl-coenzyme a dehydrase (26 Jun 1999) |
| hyper-beta-alaninaemia | Elevated levels of beta-alanine in the serum; believed to be due to a deficiency of beta-alanine:pyruvate aminotransferase; leads to impaired CNS function. (05 Mar 2000) |
| hyper-beta-aminoisobutyric aciduria | Elevated levels of beta-aminoisobutyric acid in the urine; believed to be due to a deficiency of liver R-beta-aminoisobutyrate:pyruvate aminotransferase. (05 Mar 2000) |
| N6-acetyl-beta-lysine transaminase | <enzyme> Involved in oxidative catabolism of lysine by candida maltosa; forms 2-keto-6-acetamidocaproate Registry number: EC 2.6.1.65 Synonym: n6-acetyllysine transaminase, acl-at, n6-acetyllysine 2-oxoglutarate aminotransferase (26 Jun 1999) |
| N-acetylglucosamine 4-beta-galactosyltransferase | <enzyme> From schistosoma mansoni Registry number: EC 2.4.1.- Synonym: glcnac-4-galactosyltransferase (26 Jun 1999) |
| N-acetyllactosaminide beta-1,6-N-acetylglucosaminyltransferase | <enzyme> From novikoff ascites tumour cells; asialo-alpha 1-acid glycoprotein acts as acceptor; involved in blood group I antigen synthesis Registry number: EC 2.4.1.150 Synonym: udpgnac 1-6 transferase, udp n-acetyllactosaminide beta-1-6 n-acetylglucosaminyl transferase (26 Jun 1999) |
| N-acetylneuraminylgalactosylglucosylceramide beta-1,4-N-acetylgalactosaminyltransferase | <enzyme> Requires mn2+; only substances containing sialic acid residues can act as acceptors; bovine fetuin is the best aceptor tested Registry number: EC 2.4.1.165 Synonym: neuacgal-1,4-galnactransferase, udp-galnac-neuacalpha2,3galbeta-r(galnac to gal)beta1,4-n-acetylgalactosaminyltransferase (26 Jun 1999) |
| N-benzoyl-beta-D-glucosaminidase | <enzyme> Splits 4-nitrophenyl-2-benzamido-2-deoxy-beta-d-glucopyranoside from liver of the scallop mizuhopecten yessoensis Registry number: EC 3.2.1.- (26 Jun 1999) |