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"Primary Immunodeficiency Syndrome"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
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  • ¿µ¹®
    ÇѱÛ
  • McCune-Albright syndrome
    ¸ÆÄï-¿Ãºê¶óÀÌÆ®ÁõÈıº
  • meconium plug syndrome
    ꝏ¶°³ÁõÈıº
  • megacystis-megaureter syndrome
    °Å´ë¹æ±¤°Å´ë¿ä°üÁõÈıº
  • Meigs¡¯ syndrome
    ¸ÞÀ̱×ÁõÈıº
  • nephritic syndrome
    ÄáÆÏ¿°ÁõÈıº, ½ÅÀå¿°ÁõÈıº
  • nephrotic syndrome
    ÄáÆÏÁõÈıº, ½ÅÁõÈıº
  • neuroleptic malignant syndrome
    ½Å°æÀÌ¿ÏÁ¦¾Ç¼ºÁõÈıº
  • neurovascular syndrome
    ½Å°æÇ÷°üÁõÈıº
  • Noonan¡¯s syndrome
    ´©³­ÁõÈıº
  • nutritional deficiency syndrome
    ¿µ¾ç°áÇÌÁõÈıº
  • Ogilvie syndrome
    ¿À±æºñÁõÈıº
  • oral-facial-digital syndrome
    ÀÔ¾ó±¼¼Õ°¡¶ôÁõÈıº, ±¸°­¾È¸é¼öÁ·ÁöÁõÈıº
  • orbital apex syndrome
    ´«È®²ÀÁöÁõÈıº, ¾È¿Í÷´ÜÁõÈıº
  • organic brain syndrome
    ±âÁú¼º³úÁõÈıº
  • organic mental syndrome
    ±âÁú¼ºÁ¤½ÅÁõÈıº
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  • ¿µ¹®
    ÇѱÛ
  • pluriglandular syndrome
    ¹µ»ùÁõÈıº, ¿©·¯»ùÁõÈıº
  • positive and negative syndrome
    ¾ç¼ºÀ½¼ºÁõÈıº
  • post-infarction syndrome
    °æ»öÈÄÁõÈıº
  • postelectric shock syndrome
    Àü±âÃæ°ÝÈÄÁõÈıº
  • postencephalitic behavioral syndrome
    ³ú¿°ÈÄÇൿÁõÈıº
  • postmenopausal syndrome
    Æó°æÈÄÁõÈıº
  • postpartum mood syndrome
    »êÈıâºÐÁõÈıº
  • premenstrual syndrome
    ¿ù°æÀüÁõÈıº
  • presbyophrenia syndrome
    ³ëÀÎÄ¡¸Å
  • prodromal radiation syndrome
    Á¶Áü¹æ»ç¼±ÁõÈıº
  • prune-belly syndrome
    ¸»¸°´ëÃßÁõÈıº
  • psychomotor syndrome
    Á¤½Å¿îµ¿ÁõÈıº
  • punch-drunken syndrome
    (¢¡boxer¡¯s dementia) ±ÇÅõ¼±¼öÄ¡¸Å
  • quadrilateral space syndrome
    ³×¸ð°ø°£ÁõÈıº
  • radicular syndrome
    ½Å°æ»Ñ¸®ÁõÈıº
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  • ¿µ¹®
    ÇѱÛ
  • Acquiered immune deficiency syndrome
    ÈÄõ¼º ¸é¿ª °áÇÌÁõÈıº
  • Adams Stokes syndrome
    ¾Ö´ý½º-½ºÅäÅ©½ºÁõÈıº.
  • Albrights syndrome
    ¾Ëºê¶óÀÌÆ® ÁõÈıº(~ ñøý¦ÏØ)
  • Alezzandrinis syndrome
    ¾Ë·¹Àܵ帮´ÏÁõÈıº
  • Alports syndrome
    ¾ËÆ÷Æ® ÁõÈıº
  • Alstr ms syndrome
    ¾Ë½ºÆ®·Ý ÁõÈıº
  • Angelmans syndrome
    ¾Þ°Ö¸¸ ÁõÈıº
  • Aperts syndrome
    ¿¡ÀÌÆÛÆ® ÁõÈıº
  • Aperts syndrome => acrocephalosyndactyly
    ¸»´Ü µÎÇÕÁöÁõ
  • Aschers syndrome
    ¾Ö¼ÅÁõÈıº
  • Aspergers syndrome
    ¾Æ½ºÆÛ°Å ÁõÈıº
  • Axenfeld syndrome
    ¾Ç¼¾ÆçÆ®ÁõÈıº
  • B-K mole syndrome
    B-K¸ð¹Ý ÁõÈıº
  • Bantis syndrome
    ¹ÝƼÁõÈıº.
  • Bare lymphocyte syndrome
    ¹«Ç¥Áö¸²ÇÁ±¸ÁõÈıº
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  • ¿µ¹®
    ÇѱÛ
  • primary stage
    Ãʱâ(ôøÑ¢).
  • primary stem villus
    ÀÏÂ÷°£À¶¸ð(¡­ÊÏëÖÙ¾).
  • primary sterility
    ¿ø¹ß¼º »ý½ÄºÒ´É(ê«Û¡àõßæãÖÝÕÒö), 1Â÷¼º »ý½ÄºÒ´É.
  • primary sterility
    ¿ø¹ßºÒÀÓ(ê«Û¡ÝÕìô)
  • primary structure
    ÀÏÂ÷±¸Á¶(¡­Ï°ðã).
  • primary suture
    ÀÏÂ÷ºÀÇÕ(¡­ºÀÇÕ).
  • primary symptom
    ÀÏÂ÷¼º¡¡Áõ»ó
  • primary syphilis
    Àϱâ¸Åµ¶,Ãʱâ¸Åµ¶(ôøÑ¢ØÞÔ¸)
  • primary syphilis
    Àϱâ¸Åµ¶(ìéÑ¢ØÞÔ¸), Ãʱâ¸Åµ¶(ôøÑ¢ØÞÔ¸)
  • primary systemic amyloidosis
    ¿ø¹ß¼º Àü½Å À¯ÀüºÐÁõ
  • primary taste ³ª fundamental t.
    ±âº»ÀÇ ¹Ì(ÐñÜâ¡­Ú«), ±âº»¹Ì°¢(¡­Ú«ÊÆ).
  • primary teeth
    À¯Ä¡(êáöÍ).
  • primary tone
    ¿øÀ½
  • primary trilaminar cortex
    ÀÏÂ÷»ïÃþÆÇ°ÑÁú
  • primary tuberculosis
    ÀÏÂ÷°áÇÙ(Áõ)(¡­Ì¿ú· ñø), Ãʱâ°áÇÙ(Áõ).
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JVP [POMD P 49 - 52]
  1) Jugular Vein Pressure
  2) Jugular Venous Pulse
...
PAPS 3'-phosphoadenosine-5'-phosphosulfate; primary antiphospholipid antibody syndrome
PAWS primary withdrawal syndrome
pSS primary Sjogren syndrome
SOPA Survey of Pain Attitudes; syndrome of primary aldosteronism
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PPH Primary Pulmonary Hypertension
PRP Primary Raynaud's Phenomenon
PSC Primary Sclerosing Cholangitis
PAM Primary acquired melanosis
PAD Primary afferent depolarization
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  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • effort syndrome
    ¿¡Æ÷Æ® ÁõÈıº
  • electrolyte deficiency syndrome
    ÀüÇØÁú °áÇÌ ÁõÈıº
  • empty sella syndrome
    °ø Å;îŰ¾È ÁõÈıº
    °¡Àå ÈçÇϰԴ ÁöÁÖ¸·ÀÌ Å;îŰ¾È Ⱦ°Ý¸·ÀÇ °á¼ÕºÎ¸¦ ÅëÇÏ¿© ºüÁ® µé¾î¿À´Â °ÍÀε¥ Çϼöü °æÀÌ Áö³ª´Â ±¸¸ÛÀÌ Å©´ÙµçÁö ¶Ç´Â ´Ù¸¥ °á¼ÕºÎ°¡ ÀÖ¾î ÀϾ´Ù. ³ú ô¼ö¾×¾ÐÀ¸·Î ÀÎÇØ Çϼöü°¡ À§ÃàµÇ°í Å;îŰ¾ÈÀº ºó ¸ð½ÀÀÌ µÈ´Ù. ´Ù¸¥ ¿øÀÎÀ¸·Î´Â Sheehan ÁõÈıº, ¼±Á¾ÀÇ ¿ÏÀü °æ»ö ÈÄ ¼¶À¯¼º ¹ÝÈçÈ­ ±×¸®°í ¼ö¼úÀ̳ª ¹æ»ç¼±Àû Çϼöü ÀýÁ¦ µîÀÌ´Ù. ´ë°³ ȯÀÚ´Â Çϼöü ºÎÀüÀ» ¹æÁöÇÒ ¸¸ÇÑ ÃæºÐÇÑ ½ÇÁúÀÌ º¸Á¸µÈ´Ù. ±×·¯³ª ¶§·Î´Â Ç⼺ È£¸£¸ó ÇÑ Á¾·ù ¶Ç´Â ±× ÀÌ»óÀÇ ºÐºñ ºÎÁ·ÀÌ ÀÖ´Ù.
  • encephalitis syndrome
    ³ú¿° ÁõÈıº
  • encephalotrigeminal syndrome
    ³ú »ïÂ÷ ½Å°æ ÁõÈıº
  • eosinophilia myalgia syndrome
    È£»ê±¸¼º ±ÙÀ°Åë ÁõÈıº, È£»ê±¸ Áõ´Ù¼º ±ÙÀ°Åë ÁõÈıº
  • eosinophilic pulmonary syndrome
    È£»ê¼º Æó ÁõÈıº
    ¸¸¼º È£»ê±¸¼º Æó·ÅÀº ÆóÆ÷ ¼¼Ã´À̳ª »ý°Ë»ó È£»ê±¸°¡ Æó Á¶Á÷ÀÇ ¸»Ãʺο¡ Ä§ÂøµÈ ¼Ò°ßÀ» Ư¡À¸·Î ÇÏ´Â ÁõÈıºÀ» ÀǹÌÇÑ´Ù. Ç÷¾× È£»ê±¸ Áõ°¡°¡ ´ëºÎºÐ °üÂûµÈ´Ù. ¸¸¼º È£»ê±¸¼º Æó·ÅÀº ÁÖ·Î ¿©ÀÚ¿¡ ³ªÅ¸³ª¸ç, ¹ß¿­, ¹ßÇÑ, üÁß °¨¼Ò, È£Èí °ï¶õÀÌ Æ¯Â¡ÀÌ´Ù. Ä¡·á´Â °æ±¸
  • epidermal nevus syndrome
    Ç¥ÇÇ ¸ð¹Ý ÁõÈıº
  • excited skin syndrome
    ÈïºÐ¼º ÇǺΠÁõÈıº
  • extrapyramidal syndrome
    Ãßü¿Ü·Î ÁõÈıº
  • facio-auriculo-vertebral syndrome
    ¾È¸é-ÀÌ-ôÃß ÁõÈıº
  • Fanconi's syndrome
    Fanconi ÁõÈıº
    1. Ç÷±¸°¨¼ÒÁõ, °ñ¼öÀÇ Çü¼º ºÎÀü, ¸á¶ó´Ñ Ä§Âø¿¡ ÀÇÇÑ ÇǺÎÀÇ »ö¼Ò¹Ý, ±Ù°ñ°Ý°è¿Í ºñ´¢ »ý½Ä°èÀÇ ¼±Ãµ¼º ÀÌ»óÀ» Ư¡À¸·Î ÇÏ´Â À¯Àü¼º Áúȯ. 2. ±ÙÀ§ ¼¼´¢°üÀÇ ±â´ÉÀå¾Ö·Î ÀÎÇÑ ÀÏ·ÃÀÇ ÁúȯÀ» °¡¸£Å°´Â ¿ë¾î. °íÀλ괢, ´ç´¢, Àü¾Æ¹Ì³ë»ê´¢, Áßź»ê¿°°ú ¼öºÐÀÇ ¼Õ½ÇÀÌ ÀÖ´Ù.
  • fat embolism syndrome
    Áö¹æ »öÀü ÁõÈıº
    Áö¹æ ¼ººÐÀÌ ´ëºÎºÐÀΠȲ»ö °ñ¼ö·Î µÈ °ñÀÇ °ñÀý ¶Ç´Â Áö¹æ Á¶Á÷ÀÇ ½ÉÇÑ ¿Ü»ó ÈÄ¿¡ Á¡ÁøÀû Æó ºÎÀüÁõ, Á¤½Å·Â ÀúÇÏ¿Í ½Å ºÎÀüÁõÀ» ÃÊ·¡ÇÏ´Â °ÍÀ» ¸»ÇÑ´Ù. ÀÌ´Â ÆÄ¿­µÈ Ç÷°ü ¼ÓÀ¸·Î ¹«¼öÇÑ Áö¹æ±¸°¡ µé¾î°¡ ¿©·¯ Àå±â¿¡ ºÐÆ÷ÇÑ Ç÷°ü¿¡ »öÀüÁõÀ» ¾ß±âÇÔÀ¸·Î½á ÀϾ´Ù. ÀϹÝÀûÀ¸·Î º´ÀηÐÀº º¹ÇÕÀûÀÌ´Ù. ÀÏ´Ü ÀÌ ÁõÈıºÀÌ ¹ß»ýÇÏ¸é ¸Å¿ì À§µ¶ÇÏ¿© ´ë·« 10-15%ÀÇ »ç¸Á·üÀ» ³ªÅ¸³½´Ù.
  • Felty's syndrome
    ÆçƼ ÁõÈıº
    À§Ã༺ ´Ù°üÀý¿°. ºñÁ¾. ¹éÇ÷±¸ ¹× Ç÷¼ÒÆÇ °¨¼ÒÁõ, Àú»ö¼ÒÁõ¼º ºóÇ÷, ¹ß¿­ ÇǺΠ»ö¼Ò Ä§Âø.
  • fetal distress syndrome
    ÅÂ¾Æ °ï¶õ ÁõÈıº
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 17
antiphospholipid syndrome <immunology, syndrome> An uncommon disorder that is characterised by hypercoagulability due to the presence of antibodies against phospholipids.
These patients exhibit a tendency for recurrent and life-threatening thrombosis and embolic events (for example stroke). Individuals with antiphospholipid syndrome also have an increased tendency toward deep venous thrombosis, myocardial infarction and spontaneous abortions in females.
Antiphospholipid syndrome may be seen by itself or in association with other autoimmune illnesses (for example lupus) or with some infections.
Treatment includes long-term heparin and warfarin.
(13 Jan 1998)
Anton's syndrome <syndrome> In cortical blindness, lack of awareness of being blind.
(05 Mar 2000)
anxiety syndrome <syndrome> The constellation of autonomic nervous system signs and symptoms accompanying the apprehension of danger and dread.
See: anxiety.
(05 Mar 2000)
aortic arch syndrome <syndrome> Aortic arch syndrome, also referred to by many as vertebral-basilar artery disease, carotid artery occlusive syndrome and subclavian steal syndrome is characterised by a constellation of signs and symptoms which occur secondary to abnormalities in the major arteries which extend off of the aortic arch. These abnormalities are structural and most often secondary to the effects of atherosclerosis, blood clots, trauma or a congenital abnormality. Symptoms of this condition include various neurologic symptoms, reduction in pulse and changes in blood pressure.
(27 Sep 1997)
apallic syndrome Diffuse, bilateral cerebral cortical degeneration caused by head injury, anoxia, or encephalitis, a state of persistent unresponsiveness, such as akinetic mutism, caused by brain damage.
See: vegetative.
Synonym: apallic syndrome, apallic.
(05 Mar 2000)
Apert's syndrome <paediatrics> A usually inherited disorder characterised by premature closing of the cranial suture lines resulting in a peaked shaped head and abnormal facial appearance.
Since it is usually autosomal dominant one or both parents also have the disorder. Surgery is used to correct skull and facial abnormalities.
Inheritance: autosomal dominant.
(29 Dec 1997)
Apert syndrome <syndrome> Apert (1906) defined a syndrome characterised by skull malformation (acrocephaly of brachysphenocephalic type) due to the premature closure of the cranial sutures and syndactyly of the hands and feet of a special type (complete distal fusion with a tendency to fusion also of the bony structures). The hand, when all the fingers are webbed, has been compared to a spoon and, when the thumb is free, to an obstetric hand.
Two clinical categories are distinguished, a 'typical' acrocephalosyndactyly, to which Apert's name is appropriately applied and other forms lumped together as 'atypical' acrocephalosyndactyly.
The feature distinguishing the two types is a middigital hand mass with a single nail common to digits 2-4, found in Apert syndrome and lacking in the others. A frequency of Apert syndrome of 1 in 160,000 births is estimated.
Evidence suggests that Apert syndrome results from mutations in the gene encoding fibroblast growth factor receptor-2.
Progressive synostosis occurs in the feet, hands, carpus, tarsus, cervical vertebrae, and skull, and proposed 'progressive synosteosis with syndactyly' is possibly a more appropriate designation.
Clinical features: flat facies, shallow orbits, hypertelorism, narrow palate, craniosynostosis, brachysphenocephalic acrocephaly, syndactyly, broad thumb, broad great toe, single nail digits 2-4, variable mental retardation, corpus callosum and/or limbic malformations, fused cervical vertebrae.
A skull X-ray can confirm the diagnosis. Treatment is surgical.
Inheritance: autosomal dominant, paternal age effect.
(05 Aug 1998)
Argonz-Del Castillo syndrome <syndrome> Unphysiological lactation and amenorrhoea not following pregnancy characterised by hyperprolactinaemia and a pituitary adenoma.
Synonym: Argonz-Del Castillo syndrome.
(05 Mar 2000)
Arndt-Gottron syndrome Generalised lichen myxoedematosus with diffuse thickening of the skin underlying the papules.
Synonym: Arndt-Gottron syndrome.
(05 Mar 2000)
Arnold-Chiari syndrome <radiology> Chiari I herniation of medulla and cerebellar tonsils, 4th ventricle in normal position, Chiari II herniation of medulla, tonsils, vermis, 4th ventricle at foramen magnum, myelomeningocele, aqueductal stenosis most likely to be hydrocephalus, Chiari III further herniation, 4th ventricle below foramen magnum, encephalocele or myelomeningocele associated with: agenesis of corpus callosum, syrinx
(12 Dec 1998)
arterial thoracic outlet syndrome <syndrome> A rare disorder due to compression of the subclavian artery (with resultant poststenotic dilation) by a fully formed cervical rib; thrombi form in the dilated distal arterial segment, and distal limb ischemia may occur due to thromboembolic events.
(05 Mar 2000)
arteriovenous strabismus syndrome <syndrome> Strabismus in which the angle of deviation is more marked on looking upward or downward.
See: A-esotropia, V-esotropia, A-exotropia, V-exotropia.
(05 Mar 2000)
Ascher's syndrome <syndrome> A condition in which a congenital double lip is associated with blepharochalasis and nontoxic thyroid gland enlargement.
(05 Mar 2000)
Asherman's syndrome <syndrome> Synechiae within the endometrial cavity, often causing amenorrhoea and infertility.
(05 Mar 2000)
asplenia syndrome <syndrome> Syndrome seen in patients who had no functional spleen, either due to surgical removal of disease (e.g., sickle cell anaemia); includes increased susceptibility to bacterial infection, especially pneumococcal infection.
(05 Mar 2000)
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