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juvenile nasopharyngeal f. see under angiofibroma.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
juvenile nephronophthisis–medullary cystic disease c. a term preferred by some authorities to denote familial juvenile nephronophthisis (def. 1), on the grounds that although the various diseases have identical clinical manifestations, their modes of inheritance and ages of onset are different. Four variants are recognized: a sporadic form; familial juvenile nephronophthisis (def. 2), inherited recessively; Senior-Loken syndrome or renal-retinal dysplasia, inherited recessively and associated with retinitis pigmentosa; and adult-onset medullary cystic disease (def. 2), inherited dominantly.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
juvenile p. general paralysis in young persons.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
juvenile p. a´gitans a condition developing in early life, usually familial but occasionally occurring sporadically, marked by increased muscle tonus with the characteristic attitude and facies of paralysis agitans, due to progressive degeneration of the globus pallidus; involvement of the substantia nigra and pyramidal tracts may occur. Called also paleostriatal syndrome, pallidal atrophy, pallidal syndrome, and Ramsay Hunt syndrome.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
juvenile p.’s small, benign hemispheric hamartomas of the large intestine occurring sporadically in children; histologically, there is an abundant loose fibrovascular stroma containing widely spaced glands; called also retention p's.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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