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IBED Inter-African Bureau for Epizootic Diseases
ICDA International Classification of Diseases, Adapted
ICD-9-CM International Classification of Diseases-ninth revision-Clinical Modification
ICD-10 International Statistical Classification of Diseases and Health-related Problems, 10th revision
ICD-O International Classification of Diseases-Oncology
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lymphatic diseases Diseases of lymph or lymph vessels.
(12 Dec 1998)
lysosomal diseases Diseases (also called storage diseases) in which a deficiency of a particular lysosomal enzyme leads to accumulation of the undigested substrate for that enzyme within cells. Not immediately fatal, but within a few years lead to serious neurological and skeletal disorders and eventually to death.
See: the following conditions: Hurler sundrome, Hunter syndrome, San Fillipo, Gaucher's disease, Niemann-Pick, Pompe's disease, Tay Sachs disease.
(18 Nov 1997)
lysosomal storage diseases Inborn errors of metabolism characterised by defects in specific lysosomal hydrolases and resulting in intracellular accumulation of unmetabolised substrates.
(12 Dec 1998)
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