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AGD agar gel diffusion; agarose diffusion; alpha-ketoglutarate dehydrogenase
AHB alpha-hydroxybutyric acid
AHH alpha-hydrazine analog of histidine; anosmia and hypogonadotropic hypogonadism [syndrome]; arylhydro...
AHSG alpha-2HS-glycoprotein
'Greek letter alpha' angular acceleration; first [carbon atom next to the carbon atom bearing the active group in organic...
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alpha-CGRP Alpha calcitonin gene-related peptide
alpha-GST Alpha glutathione S-transferase
alpha-hANP Alpha human atrial natriuretic polypeptide
IFN alpha Alpha interferon
alpha IFN Alpha interferon
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alpha-ketoarginine decarboxylase <enzyme> Alpha-ketoarginine gives gamma-guanidinobutyraldehyde
Registry number: EC 4.1.1.-
Synonym: alpha keto-arginine decarboxylase
(26 Jun 1999)
alpha-ketobutyrate dehydrogenase <enzyme> Rat liver enzyme oxidatively decarboxylates alpha-ketobutyrate to carbon dioxide and propionyl CoA; requires nad, fad and thiamine pyrophosphate
Registry number: EC 1.2.1.-
(26 Jun 1999)
alpha-ketodecarboxylase Formerly, the enzyme system converting pyruvate (a 2-oxoacid) to acetyl-CoA and CO2, with reduction of NAD+ to NADH and the participation of lipoamide and thiamin pyrophosphate; now known to involve at least three enzymes in succession: pyruvate dehydrogenase, dihydrolipoamide acetyltransferase, and dihydrolipoamide dehydrogenase.
Compare: pyruvate dehydrogenase (lipoamide).
(05 Mar 2000)
alpha-ketoglutaramic acid H2N-COCH2CH2COCOOH;a metabolite of glutamine formed by the action of glutamine aminotransferase; elevated in certain cases of hepatocoma.
Synonym: 2-oxoglutaric acid.
(05 Mar 2000)
alpha-ketoglutarate A salt or ester of alpha-ketoglutaric acid.
Alpha-ketoglutarate dehydrogenase, an enzyme that catalyses the oxidative decarboxylation of 2-ketoglutaric acid to succinyldihydrolipoate; the succinyl group is later transferred to CoA and the reduced lipoate is oxidised by NAD+; a complex that is a part of the tricarboxylic acid cycle.
Synonym: 2-oxoglutarate dehydrogenase, alpha-ketoglutarate dehydrogenase complex.
(05 Mar 2000)
alpha-ketoglutarate dehydrogenase complex alpha-ketoglutarate dehydrogenase
alpha-ketoglutarate permease <chemical> From E coli; 432-amino acid protein; amino acid sequence given in first source
Synonym: kGTP gene product, wita protein, alpha-ketoglutarate transporter
(26 Jun 1999)
alpha-ketoisocaproate oxygenase <enzyme> From rat liver cytosol; oxidatively decarboxylates and hydroxylates alpha-ketoisocaporate to form beta-hydroxyisovalerate; requires fe(2+) and thiol; activated by ascorbate
Registry number: EC 1.13.11.-
Synonym: 2-ketoisocaproate oxygenase, alpha-ketoisocaproate dioxygenase
(26 Jun 1999)
alpha-ketosuccinamic acid NH2-CO-CH2-CO-COOH;the transamination product of asparagine; acted upon by &omega;-amidase.
(05 Mar 2000)
alpha-lactyl-thiamin pyrophosphate An intermediate formed in the oxidative decarboxylation of pyruvate.
Compare: pyruvate dehydrogenase (lipoamide).
Synonym: alpha-lactyl-thiamin pyrophosphate.
(05 Mar 2000)
alpha-l-iduronidase <enzyme> An enzyme that hydrolyzes terminal desulfated alpha-l-iduronic acid residues of dermatan sulfate and of heparan sulfate; a deficiency of this enzyme is associated with Hurler syndrome and Scheie syndrome.
(05 Mar 2000)
alpha-linolenic acid <chemical> (z,z,z)-9,12,15-octadecatrienoic acid. A fatty acid that is found in plants and involved in the formation of prostaglandins.
Chemical name: 9,12,15-Octadecatrienoic acid, (Z,Z,Z)-
(12 Dec 1998)
alpha-macroglobulins Glycoproteins with a molecular weight of approximately 620,000 to 680,000. Precipitation by electrophoresis is in the alpha region. They include alpha 1-macroglobulins and alpha 2-macroglobulins. These proteins exhibit trypsin-, chymotrypsin-, thrombin-, and plasmin-binding activity and function as hormonal transporters.
(12 Dec 1998)
alpha-mannosidase <enzyme> Catalyses hydrolysis of terminal, non-reducing alpha-d-mannose residues in alpha-d-mannosides
Registry number: EC 3.2.1.24
Synonym: alpha-d-mannoside mannohydrolase, alpha-d-mannosidase, neutral alpha-mannosidase, alpha mannosidase a, alpha mannosidase b, lysosomal alpha-mannosidase, laman
(26 Jun 1999)
alpha-methylacyl-CoA racemase <enzyme> Involved in catabolism of branched-chain fatty acids derived from isoprenoids; acts on pristanoyl-CoA and trihydroxycoprostanoyl-CoA, but not on 3-methyl branched-chain or linear-chain acyl coas; amino acid sequence has been determined; genbank u89905 (rat) and u89906 (mouse); also isolated from human liver
Registry number: EC 5.1.99.-
Synonym: meac CoA racemase
(26 Jun 1999)
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