uroporphyrinogen : KMLE 의학 검색 엔진 - 의학사전, 의학용어, 의학약어, 의학논문, 약품/의약품 검색

MeSH(Medical Subject Headings) 맞춤 검색 (http://www.nlm.nih.gov) 결과 : 3 페이지: 1

Uroporphyrinogen Decarboxylase - 새창 An enzyme that catalyzes the decarboxylation of UROPORPHYRINOGEN III to coproporphyrinogen III by the conversion of four acetate groups to four methyl groups. It is the fifth enzyme in the 8-enzyme biosynthetic pathway of HEME. Several forms of cutaneous PORPHYRIAS are results of this enzyme deficiency as in PORPHYRIA CUTANEA TARDA; and HEPATOERYTHROPOIETIC PORPHYRIA.
Synonyms : Uroporphyrinogen III Decarboxylase, Carboxy-Lyase, Uroporphyrinogen, Decarboxylase, Uroporphyrinogen, Decarboxylase, Uroporphyrinogen III, Uroporphyrinogen Carboxy Lyase
Uroporphyrinogen III Synthetase - 새창 An enzyme that catalyzes the cyclization of hydroxymethylbilane to yield UROPORPHYRINOGEN III and water. It is the fourth enzyme in the 8-enzyme biosynthetic pathway of HEME, and is encoded by UROS gene. Mutations of UROS gene result in CONGENITAL ERYTHROPOIETIC PORPHYRIA.
Synonyms : Cosynthetase, Uroporphyrinogen III, Isomerase, Uroporphyrinogen, Synthase, Uroporphyrinogen-III, Synthetase, Uroporphyrinogen III, Uroporphyrinogen III Synthase
Uroporphyrinogens - 새창 Porphyrinogens which are intermediates in heme biosynthesis. They have four acetic acid and four propionic acid side chains attached to the pyrrole rings. Uroporphyrinogen I and III are formed from polypyrryl methane in the presence of uroporphyrinogen III cosynthetase and uroporphyrin I synthetase, respectively. They can yield uroporphyrins by autooxidation or coproporphyrinogens by decarboxylation.
Synonyms : Uroporphyrinogen III