| trihexosylceramide | <biochemistry> A type of glycolipid compound which accumulates in the blood vessel walls of people with Fabry disease as a result of a deficiency in alpha-galactosidase A, a type of galactosidase enzyme. (09 Oct 1997) |
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| trihexosylceramides | Glycosphingolipids which contain as their polar head group a trisaccharide (galactose-galactose-glucose) moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in ceramide trihexosidase, is the cause of angiokeratoma corporis diffusum (fabry's disease). (12 Dec 1998) |