| 영문 | porphyria | 한글 | 포르피린증 |
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| 설명 | 포르피린 또는 그 전구물질의 형성이나 배설의 현저한 증가를 특징으로 하는 포르피린 대사장애에 대한 총칭. 네 개의 피롤핵이 메틸기로 연결된 포피린유도체의 총칭이다. 측쇄에 메틸기, 에틸기, 비닐기, 프로피온산기 등이 들어간 유로포피린, 코프로포피린, 프로토포피린, 헤마토포피린 등이 알려져 있다. 포르피린환에 Fe2+가 들어간 GPA은 글로빈과 결합하여 혈색소를 구성한다. 철포르피린으로서는 헤모글로빈, 시토크롬, 카타라아제 등이 있고, Mg2+를 갖는 것으로서는 엽록소가 있다. 생체조직 중, 주로 골수의 어린 적혈구 그리고 간에서 이루어지는 헴합성의 중간대사물질로, 혈색소나 각종 헴단백의 소재가 된다. 헴합성 이상에 의해 적혈구, 혈장, 소변, 대변의 포르피린체가 증가한다. 헴합성의 이상은 각 형의 포피리아, 빈혈, 납중독 등에서 볼 수 있다. |
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| AIP | Acute Intermittent Porphyria; 급성 간혈증 Porphyria |
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| CEP | Congenital Erythropoetic Porphyria(= Gnther Disease; 선천성 조혈기성 Porphyria |
| PCT | 1) Post-Coital Test = Sims-Hubner Test 2) Porp... |
| VP | 1) Variegate Porphyria; 발문상 Porphyria 2) Viral Protein |
| CEP | chronic eosinophilic pneumonia; chronic erythropoietic porphyria; congenital erythropoietic porphyri... |
| GSHV | Ground squirrel hepatitis virus |
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| SMRV | Squirrel monkey retrovirus |
| AIP | Acute Intermittent Porphyria |
| CEP | Congenital erythropoietic porphyria |
| HEP | Hepatoerythropoietic porphyria |
| squirrel porphyria | Porphyria as an apparently normal metabolic state seen in the Florida fox squirrel (Sciurus niger). (05 Mar 2000) |
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| squirrel | 1. <zoology> Any one of numerous species of small rodents belonging to the genus Sciurus and several allied genera of the famly Sciuridae. Squirrels generally have a bushy tail, large erect ears, and strong hind legs. They are commonly arboreal in their habits, but many species live in burrows. Among the common North American squirrels are the gray squirrel (Scirius Carolinensis) and its black variety; the fox, or cat, sqirrel (S. Cinereus, or S. Niger) which is a large species, and variable in colour, the southern variety being frequently black, while the northern and western varieties are usually gray or rusty brown; the red squirrel (see Chickaree); the striped, or chipping, squirrel (see Chipmunk); and the California gray squirrel (S. Fossor). Several other species inhabit Mexico and Central America. The common European species (Sciurus vulgaris) has a long tuft of hair on each ear. The so-called Australian squirrels are marsupials. See Petaurist, and Phalanger. 2. One of the small rollers of a carding machine which work with the large cylinder. <zoology> Barking squirrel . See Jelerang. <botany> Squirrel corn, a grass (Hordeum jubatum) found in salt marshes and along the Great Lakes, having a dense spike beset with long awns. Origin: OE. Squirel, OF. Esquirel, escurel, F. Ecureuil, LL. Squirelus, squirolus, scuriolus, dim. Of L. Sciurus, Gr. Sioyros; skia shade + o'yra tail. Cf. Shine. Source: Websters Dictionary (01 Mar 1998) |
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| squirrel plague conjunctivitis | One of the causes of Parinaud's conjunctivitis. Synonym: tularaemic conjunctivitis, conjunctivitis tularensis. (05 Mar 2000) |
| flying squirrel | <zoology> One of a group of squirrels, of the genera Pteromus and Sciuropterus, having parachute-like folds of skin extending from the fore to the hind legs, which enable them to make very long leaps. The species of Pteromys are large, with bushy tails, and inhabit southern Asia and the East Indies; those of Sciuropterus are smaller, with flat tails, and inhabit the northern parts of Europe, Asia, and America. The American species (Sciuropterus volucella) is also called Assapan. The Australian flying squrrels, or flying phalangers, are marsupials. See Flying phalanger (above). Source: Websters Dictionary (01 Mar 1998) |
| acute intermittent porphyria | <gastroenterology, haematology> A group of rare inherited metabolic disorders that result from a disturbance in porphyrin metabolism, causing increased formation and excretion of porphyrin or its precursors. It is caused by hepatic overproduction of d-aminolevulinic acid, which has greatly increased urinary excretion and of porphobilinogen, and some increase of uroporphyrin, due to a deficiency of porphobilinogen deaminase. Clinical features: intermittent acute attacks of hypertension, abdominal colic, psychosis, and polyneuropathy, but with no photosensitivity. It is exacerbated by the ingestion of certain drugs such as; barbiturates). Inheritance: autosomal dominant. (20 Sep 2002) |
| acute porphyria | <gastroenterology, haematology> A group of metabolic disorders that result from a disturbance in porphyrin metabolism, causing increased formation and excretion of porphyrin or its precursors. Acute intermittent porphyria is a rare inherited (autosomal dominant) form that can result in abdominal pain, photosensitivity and neurological disturbances. The various forms can be differntiated measuring various blood prophyrins. (27 Sep 1997) |
| bovine porphyria | Porphyria as a mendelian recessive trait in certain breeds of cattle. (05 Mar 2000) |
| variegate porphyria | Porphyria characterised by abdominal pain and neuropsychiatric abnormalities, by dermal sensitivity to light and mechanical trauma, by increased faecal excretion of proto-and coproporphyrin, and by increased urinary excretion of d-aminolevulinic acid, porphobilinogen, and porphyrins; due to a deficiency of protoporphyrinogen oxidase; autosomal dominant inheritance. Synonym: protocoproporphyria hereditaria, South African type porphyria. (05 Mar 2000) |
| congenital erythropoietic porphyria | A group of metabolic disorders that result from a disturbance in porphyrin metabolism, causing increased formation and excretion of porphyrin or its precursors. Acute intermittent porphyria is a rare inherited (autosomal dominant) form that can result in abdominal pain, photosensitivity and neurological disturbances. The various forms can be differntiated measuring various blood prophyrins. Inheritance: autosomal dominant. (27 Sep 1997) |
| porphobilinogen synthase porphyria | An inherited disorder in which there is a deficiency of porphobilinogen synthase; d-aminolevulinate levels are elevated, leading to neurological disturbances. Synonym: porphobilinogen synthase porphyria. (05 Mar 2000) |
| porphyria | A pathological state in man and some lower animals that is often due to genetic factors, is characterised by abnormalities of porphyrin metabolism and results in the excretion of large quantities of porphyrins in the urine and in extreme sensitivity to light. (18 Nov 1997) |
| porphyria, acute intermittent | A form of hepatic porphyria (porphyria, hepatic) characterised by periodic attacks of gastrointestinal disturbances, abdominal colic, paralyses, and psychiatric disorders. The onset of this condition is usually in the third or fourth decade of life. (12 Dec 1998) |
| porphyria cutanea tarda | A form of hepatic porphyria (porphyria, hepatic) characterised by photosensitivity resulting in bullae that rupture easily to form shallow ulcers. This condition occurs in two forms: a sporadic, nonfamilial form that begins in middle age and has normal amounts of uroporphyrinogen decarboxylase with diminished activity in the liver; and a familial form in which there is an autosomal dominant inherited deficiency of uroporphyrinogen decarboxylase in the liver and red blood cells. (12 Dec 1998) |
| porphyria cutanea tarda hereditaria | A form of hepatic porphyria (porphyria, hepatic) characterised by photosensitivity resulting in bullae that rupture easily to form shallow ulcers. This condition occurs in two forms: a sporadic, nonfamilial form that begins in middle age and has normal amounts of uroporphyrinogen decarboxylase with diminished activity in the liver; and a familial form in which there is an autosomal dominant inherited deficiency of uroporphyrinogen decarboxylase in the liver and red blood cells. (12 Dec 1998) |
| porphyria cutanea tarda symptomatica | A form of hepatic porphyria (porphyria, hepatic) characterised by photosensitivity resulting in bullae that rupture easily to form shallow ulcers. This condition occurs in two forms: a sporadic, nonfamilial form that begins in middle age and has normal amounts of uroporphyrinogen decarboxylase with diminished activity in the liver; and a familial form in which there is an autosomal dominant inherited deficiency of uroporphyrinogen decarboxylase in the liver and red blood cells. (12 Dec 1998) |
| porphyria, erythrohepatic | A form of porphyria characterised by a wide range of photocutaneous changes, liver disease, and an excess of protoporphyrin. (12 Dec 1998) |
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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