| BSE | behavior summarized evaluation; bilateral intranasal sphenoethmoiclectomy; bilateral symmetrical and... |
|---|---|
| SE | saline enema; sanitary engineering; side effect; smoke exposure; solid extract; sphenoethmoidal; spi... |
| SSE | saline solution enema; skin self-examination; soapsuds enema; steady state exercise; subacute spongi... |
| GCL | globoid cell leukodystrophy |
| GLD | globoid leukodystrophy; glutamate dehydrogenase |
| GLD | Globoid cell leukodystrophy |
|---|---|
| MLD | Metachromatic Leukodystrophy |
| BSE | Bovine Spongiform Encephalopathy |
| TSE | Transmissible Spongiform Encephalopathies |
| TSEs | Transmissible Spongiform Encephalopathies |
| adrenal leukodystrophy | Sudanophilic leukodystrophy with bronzing of skin and adrenal atrophy. A metabolic disorder of young males, characterised by widespread myelin degeneration and associated adrenal insufficiency. The myelin degeneration is massive in various portions of the brain and sometimes the spinal cord, with the accumulation of degradation products of myelin in macrophages: sudanophilic demyelination; atrophy is present in the adrenal glands and testes, and markedly increased amounts of very long-chain fatty acid are present in both the brain and adrenal glands. Symptoms include bronzing of the skin, dysarthria, cortical blindness, bilateral hemiplegia, pseudobulbar paralysis, and progressive dementia. Probably sex-linked recessive inheritance. (05 Mar 2000) |
|---|---|
| bovine spongiform encephalitis | <pathology> A neuro-degenerative disease found in domestic cattle which is related to a number of other similar diseases found in other animal species, including humans. The most well-known of these other diseases are scrapie, found in sheep, and Creutzfeldt-Jakob Disease, found in humans. The family of diseases is caused by an abnormally-configured protein called a prion. The function of the protein in its normal configuration is not certain. The diseases are similar to Alzheimer's disease in humans, except the progressive loss of brain function is more rapid. (09 Oct 1997) |
| bovine spongiform encephalopathy | A new disease of cattle, first reported in 1986 in Great Britain, characterised clinically by apprehensive behaviour, hyperesthesia, and ataxia and histopathologically by spongiform changes in the gray-matter neuropil of the brain stem; it is thought to be caused by an agent, possibly a prion, similar to that observed as the cause of scrapie. Synonym: mad cow disease. (05 Mar 2000) |
| globoid cell leukodystrophy | <radiology> Dysmyelinating disease, autosomal recessive, usually presents by 1 yr, specific enzyme deficiency identified, rapid spontaneous nystagmus, poikilothermia Synonym: Krabbe leukodystrophy (12 Dec 1998) |
| metachromatic leukodystrophy | <radiology> Dysmyelinating disease, autosomal recessive, aryl sulfatase A -- absent from urine and serum, most present by 2 yrs, die at 3-4 yrs, may arise at any age, CT: decreased density of white matter, primarily in centrum semiovale, with or without focal gall bladder defects (!) (12 Dec 1998) |
| spongiform | 1. Soft, and full of cavities; of an open, loose, pliable texture; as, a spongy excrescence; spongy earth; spongy cake; spongy bones. 2. Wet; drenched; soaked and soft, like sponge; rainy. "Spongy April." 3. Having the quality of imbibing fluids, like a sponge. <chemistry> Spongy lead, sponge lead. See Sponge. Spongy platinum. See Platinum. Source: Websters Dictionary (01 Mar 1998) |
| spongiform encephalopathies | A group of diseases characterised by long incubation and fatal progressive course with characteristic spongiform degeneration of grey matter of the cortex. The two main human diseases are kuru and Creutzfeldt Jakob disease. Diseases such as scrapie, mink encephalopathy and bovine spongiform encephalopathy (BSE) are considered to be similar. Controversy still surround the causative agent, the two main theories being slow viruses or prions. See: Gerstmann Straussler Scheinker syndrome. (18 Nov 1997) |
| spongiform encephalopathy | An encephalopathy characterised by vacuolation within nerve and glial cells. (05 Mar 2000) |
| subacute spongiform encephalopathy | A form of spongiform encephalopathy that is associated with a "slow virus", which to date has not been adequately described, is transmissible, and has a rapidly progressive, fatal course; e.g., Creutzfeldt-Jakob disease, kuru, Gerstmann-Straussler syndrome, scrapie. (05 Mar 2000) |
| encephalopathy, bovine spongiform | Scrapie-like neurological disorder of cattle. The infection appears to be caused by the consumption of scrapie-infected ruminant-derived protein (prions). (12 Dec 1998) |
| leukodystrophy | <radiology> Type of dysmyelinating disease, hereditary, peripheral nervous system unaffected in some disorders Specific diseases: adrenoleukodystrophy, metachromatic leukodystrophy, spongy degeneration (Canavan), globoid cell (Krabbe) leukodystrophy, Alexander disease, Pelizaeus-Merzbacher disease, Cockayne syndrome (12 Dec 1998) |
| leukodystrophy, globoid cell | An inherited metabolic disorder of the nervous system, particularly the white matter. It is characterised histologically by a paucity of myelin and oligodendroglia, severe astrocytic gliosis, and massive infiltration with unique multinucleated globoid cells which are enriched in galactosylceramide. The primary genetic defect is a deficiency of galactosylceramidase. (12 Dec 1998) |
| leukodystrophy, metachromatic | A sphingolipidosis where there is defective desulfation of galactosyl-3-sulfate ceramide due to a defective enzyme cerebroside sulfatase (arylsulfatase a). The result is an accumulation of sulfatide in neural and non-neural tissues which manifests as mental deterioration and severe disturbances of the central nervous system. (12 Dec 1998) |
| leukodystrophy with diffuse Rosenthal fibre formation | A metabolic disorder whose onset can be in infancy, adolescence, or adulthood; characterised pathologically by widespread cerebral demyelination with astrocyte and primitive oligodendroglial cell proliferation; refractile Rosenthal fibres result from the degeneration of these proliferating cells; aetiology unknown, but possibly due to a metabolic defect of astrocytes; sex-linked recessive disorder. (05 Mar 2000) |
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|