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pterin Term loosely used for any of the compounds containing pteridine; specifically, 2-amino-4-hydroxypteridine. Some pteridines (e.g., xanthopterin, leucopterin) still retain the pterin root.
(05 Mar 2000)
pterin deaminase An aminohydrolase catalyzing hydrolytic deamination of 2-amino-4-hydroxypteridine to form 2,4-dihydroxypteridine and ammonia.
(05 Mar 2000)
pterin-4a-carbinolamine dehydratase <enzyme> Bifunctional protein which converts pterin-4a-carbinolamine to quinoid dihydrobiopterin and functions as dimerization cofactor for hnf-1alpha; deficiency results in an atypical form of phenylketonuria; proposed EC 4.2.1.96
Registry number: EC 4.2.1.-
Synonym: pt-c dehydratase, phenylalanine hydroxylase-stimulating protein, pterin-4alpha-carbinolamine dehydratase, dcoh protein, dimerization cofactor of hnf-1alpha, 4a-hydroxytetrahydrobiopterin dehydratase, 4a-carbinolamine dehydratase, bh3oh dehydratase, 4alpha-carbinolamine dehydratase
(26 Jun 1999)
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