| pseudoxanthoma elasticum |
a rare, progressive disorder with autosomal recessive and dominant forms, usually appearing after puberty with skin, eye, and cardiovascular manifestations, most of which result from basophilic degeneration of elastic tissue. Symptoms include small yellow cutaneous macules and papules that merge to form plaques, mainly in flexural areas; lax, inelastic, redundant skin; angioid streaks in the retina; arterial insufficiency in the lower extremities; premature calcification of peripheral arteries; reduced arterial pulses; symptoms of coronary insufficiency, hypertension, and mitral valve prolapse; and gastrointestinal and other hemorrhages. Called also nevus elasticus.
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