| propionyl | <chemistry> The hypothetical radical C3H5O, regarded as the essential residue of propionic acid and certain related compounds. Source: Websters Dictionary (01 Mar 1998) |
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| propionyl CoA hydrolase | <enzyme> Nadh sensitive; found in brown adipose tissue mitochondria of rat; prevents a deterimental increase of propionyl-CoA in mitochondria; mw at least 240 kD Registry number: EC 3.1.2.- Synonym: propionyl coenzyme a hydrolase (26 Jun 1999) |
| propionyl-CoA | The coenzyme A thioester derivative of propionic acid; an intermediate in the degradation of l-valine, l-isoleucine, l-threonine, l-methionine, and odd-chain fatty acids; a precursor for the synthesis of odd-chain fatty acids; it accumulates in individuals with a deficiency of propionyl-CoA carboxylase. Propionyl-CoA carboxylase, an enzyme that catalyses the reaction of propionyl-CoA with CO2 and ATP to produce ADP, inorganic phosphate, and d-methylmalonyl-CoA; a biotin-dependent enzyme; an inherited deficiency of this enzyme will lead to propionic acidemia and developmental retardation. (05 Mar 2000) |
| propionyl-CoA carboxylase | <enzyme> See also propionyl CoA carboxylase (ATP-hydrolyzing) (EC 6.4.1.4) Registry number: EC 4.1.1.41 Synonym: methylmalonyl-CoA decarboxylase, propionyl-coenzyme a carboxylase (26 Jun 1999) |
| propionylcholinesterase | <enzyme> Aspect of cholinesterase EC 3.1.1.8 Registry number: EC 3.1.1.- (26 Jun 1999) |
| propionylglycine | CH3CH2CONHCH2COOH;a minor metabolite that accumulates in individuals with propionic acidemia. (05 Mar 2000) |