| progressive choroidal atrophy | An x chromosome-linked abnormality characterised by atrophy of the choroid and degeneration of the retinal pigment epithelium causing night blindness. (12 Dec 1998) |
|---|---|
| progressive circumscribed cerebral atrophy | Circumscribed atrophy of the cerebral cortex. Synonym: lobar sclerosis, progressive circumscribed cerebral atrophy. (05 Mar 2000) |
| progressive infantile spinal muscular atrophy | Transmitted as autosomal recessive on chromosome 5q. Progressive dysfunction of the anterior horn cells in the spinal cord and brainstem cranial nerves with profound weakness and bulbar dysfunction occurring in the first two years of life. Three groups, based on age of clinical onset, are recognised. Synonym: familial spinal muscular atrophy, Hoffmann's muscular atrophy, infantile muscular atrophy, infantile progressive spinal muscular atrophy, progressive infantile spinal muscular atrophy, Werdnig-Hoffmann disease, Werdnig-Hoffmann muscular atrophy. (05 Mar 2000) |
| progressive muscular atrophy | A serious neurologic disease that results from the progressive degeneration of the motor neurons. (27 Sep 1997) |
| progressive spinal muscular atrophy | One of the subgroups of motor neuron disease; a progressive degenerative disorder of the motor neurons of the spinal cord, manifested as progressive, often symmetrical, weakness and wasting, typically beginning in the distal portions of the limbs, particularly in the upper extremities, and spreading proximally; fasciculation potentials are often present, but evidence of corticospinal tract disease (e.g., increased deep tendon reflexes, Babinski sign) is not. (05 Mar 2000) |
| infantile progressive spinal muscular atrophy | Transmitted as autosomal recessive on chromosome 5q. Progressive dysfunction of the anterior horn cells in the spinal cord and brainstem cranial nerves with profound weakness and bulbar dysfunction occurring in the first two years of life. Three groups, based on age of clinical onset, are recognised. Synonym: familial spinal muscular atrophy, Hoffmann's muscular atrophy, infantile muscular atrophy, infantile progressive spinal muscular atrophy, progressive infantile spinal muscular atrophy, Werdnig-Hoffmann disease, Werdnig-Hoffmann muscular atrophy. (05 Mar 2000) |
| essential progressive atrophy of iris | Progressive atrophy of the iris without inflammatory signs, characterised by patchy loss of all layers of the iris with hole formation, migration of the pupil, degeneration of the corneal endothelium, peripheral anterior synechiae, and secondary glaucoma; usually unilateral, predominantly affecting women in their middle years. (05 Mar 2000) |
| unilateral | <anatomy> Affecting only one side. Origin: L. Latus = side (18 Nov 1997) |
| unilateral anaesthesia | <neurology> The inability to feel touches (tactile sensations) on one side of the body. (09 Oct 1997) |
| unilateral hemianopia | Uniocular hemianopia, loss of sight in one-half of the visual field of one eye only. (05 Mar 2000) |
| unilateral hermaphroditism | Hermaphroditism in which the doubling of sex characteristics occurs on one side only: ovotestis on one side and either ovary or testis on the other. (05 Mar 2000) |
| unilateral hyperlucent lung | Chronic bronchiolitis obliterans predominating on one side. See: unilateral lobar emphysema. (05 Mar 2000) |
| unilateral large kidney | <radiology> Multifocal: xanthogranulomatous pyelonephritis (XGP), malakoplakia, multicystic dysplastic kidney Cf: other urographic patterns smooth kidney: renal vein thrombosis, acute arterial infarction, obstructive uropathy, acute bacterial nephritis, compensatory hypertrophy, duplicated pelvocalyceal system Cf: other urographic patterns multifocal: solid neoplastic mass, malignant, adenocarcinoma, adult nephroblastoma, invasive transitional cell carcinoma, sarcoma, metastasis, benign, hamartoma, adenoma, mesenchymal tumour cystic mass, simple cyst, focal hydronephrosis, multilocular cystic nephroma, arteriovenous malformation Cf: other urographic patterns (12 Dec 1998) |
| unilateral lobar emphysema | A state in which the roentgenographic density of one lung (or one lobe) is markedly less than the density of the other(s) because of the presence of air trapped during expiration. Synonym: Macleod's syndrome, Swyer-James syndrome. (05 Mar 2000) |
| unilateral rib notching | <radiology> Aortic coarctation, proximal to left subclavian artery most likely to be right, anomalous right subclavian artery most likely to be left, subclavian artery stenosis / atresia, most likely to be IPSIlateral, Blalock-Taussig shunt, anastamosis of subclavian artery to pulmonary artery, for Tetralogy of Fallot, most likely to be IPSIlateral (12 Dec 1998) |