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"progressive diffuse keratoderma"¿¡ ´ëÇÑ ´ëÇÑÀÇÇù ÀÇÇпë¾î ¼¼ºÎ °Ë»ö °á°úÀÔ´Ï´Ù
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö ¸ÂÃã °Ë»ö °á°ú :
1
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progressive diffuse keratoderma
±¤¹üÀ§ÁøÇà°¢ÁúÇǺÎÁõ
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú :
15
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epidermolytic palmoplantar keratoderma
Ç¥Çǹڸ®¼Õ¹ß¹Ù´Ú°¢ÁúÇǺÎÁõ
hereditary palmoplantar keratoderma
À¯Àü¼Õ¹ß¹Ù´Ú°¢ÁúÇǺÎÁõ
keratoderma
1. °¢ÇÇ 2. °¢ÁúÇǺÎÁõ, °¢ÇÇÁõ
keratoderma blennorrhagicum
°í¸§°¢ÁúÇǺÎÁõ, ³ó·ç°¢ÇÇÁõ
keratoderma climactericum
°»³â±â°¢ÁúÇǺÎÁõ, °»³â±â°¢ÇÇÁõ
palmoplantar keratoderma
¼Õ¹ß¹Ù´Ú°¢ÁúÇǺÎÁõ, ¼Õ¹ß¹Ù´Ú°¢ÇÇÁõ
punctate keratoderma
Á¡¸ð¾ç°¢ÁúÇǺÎÁõ
degenerative diffuse cerebral sclerosis
ÅðÇ౤¹üÀ§´ë³ú°æÈ(Áõ)
diffuse
±¤¹üÀ§-, È®»ê-, ¹Ì¸¸-
diffuse aneurysm
±¤¹üÀ§µ¿¸ÆÀÚ·ç, ±¤¹üÀ§µ¿¸Æ·ù
diffuse arteriosclerosis
±¤¹üÀ§µ¿¸Æ°æÈ(Áõ)
diffuse atelectasis
±¤¹üÀ§¹«±âÆó
diffuse cerebral sclerosis
±¤¹üÀ§´ë³ú°æÈÁõ
diffuse cutaneous mastocytosis
±¤¹üÀ§ÇǺκñ¸¸¼¼Æ÷Áõ
diffuse esophageal spasm
±¤¹üÀ§½Äµµ¿¬Ãà
´ÙÀ½
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú :
5
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keratoderma
°¢ÁúÇǺÎÁõ
diffuse goiter
±¤¹üÀ§°©»ó»ùÁ¾, ¹Ì¸¸°©»ó»ùÁ¾
rapidly progressive glomerulonephritis
±Þ¼ÓÁøÇàÅ丮ÄáÆÏ¿°, ±Þ¼ÓÁøÇà»ç±¸Ã¼½Å¿°
progressive bulbar palsy
ÁøÇà¼û³ú¸¶ºñ, ÁøÇ࿬¼ö¸¶ºñ
diffuse esophageal spasm
±¤¹üÀ§½Äµµ¿¬Ãà
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö ¸ÂÃã °Ë»ö °á°ú :
1
ÆäÀÌÁö:
1
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ÇѱÛ
progressive diffuse keratoderma
±¤¹üÀ§ÁøÇà°¢ÁúÇǺÎÁõ
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú :
15
ÆäÀÌÁö:
1
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ÇѱÛ
epidermolytic palmoplantar keratoderma
Ç¥Çǹڸ®¼Õ¹ß¹Ù´Ú°¢ÁúÇǺÎÁõ
hereditary palmoplantar keratoderma
À¯Àü¼Õ¹ß¹Ù´Ú°¢ÁúÇǺÎÁõ
keratoderma
°¢ÁúÇǺÎÁõ
keratoderma blennorrhagicum
°í¸§°¢ÁúÇǺÎÁõ
keratoderma climactericum
°»³â±â°¢ÁúÇǺÎÁõ
palmoplantar keratoderma
¼Õ¹ß¹Ù´Ú°¢ÁúÇǺÎÁõ
punctate keratoderma
Á¡»ó°¢ÁúÇǺÎÁõ
diffuse aneurysm
±¤¹üÀ§µ¿¸ÆÀÚ·ç, ±¤¹üÀ§µ¿¸Æ·ù
diffuse arteriosclerosis
±¤¹üÀ§µ¿¸Æ°æÈÁõ
diffuse atelectasis
±¤¹üÀ§¹«±âÆó
diffuse intravascular coagulation
¹Ì¸¸Ç÷°ü³»ÀÀ°í
diffuse
±¤¹üÀ§-, È®»ê-, ¹Ì¸¸-
degenerative diffuse cerebral sclerosis
ÅðÇ౤¹üÀ§³ú°æÈ(Áõ)
diffuse erythema
±¤¹üÀ§È«¹Ý
diffuse goiter
¹Ì¸¸°©»ó»ùÁ¾, ±¤¹üÀ§¹æÆÐ»ùÁ¾
´ÙÀ½
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö ¸ÂÃã °Ë»ö °á°ú :
1
ÆäÀÌÁö:
1
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ÇѱÛ
progressive diffuse keratoderma
ÁøÇ༺ ±¤¹üÀ§ °¢ÇÇÁõ
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú :
15
ÆäÀÌÁö:
1
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Hamman Rich syndrome =diffuse interstitial pulmonary fibrosis
ÇØ¸Õ- ¸®Ä¡ÁõÈıº.
glomerulonephritis,diffuse proliferative
¹Ì¸¸¼º Áõ½Ä¼º(ڵؼàõ ñòãÖàõ)
goiter,diffuse nontoxic(simple)
¹Ì¸¸¼º ºñµ¶¼º(´Ü¼ø)
Keratoderma hereditaria mutilans
À¯Àü¼º Àý´Ü¼º ÇǺΰ¢ÈÁõ
Keratoderma palmoplantare transgrediens
¼Õ¹ß¹Ù´Ú Á¡ÁøÀÌÇ༺ ÇǺΰ¢ÇÇÁõ
hereditary plamoplantar keratoderma
À¯Àü¼º ¼Õ¹ß¹Ù´Ú°¢ÇÇÁõ
punctate keratoderma
Á¡»ó°¢ÇÇÁõ
acquired progressive lymphangioma
ÈÄõ¼º ÁøÇ༺ ¸²ÇÁ°üÁ¾
hereditary progressive mucinous histiocytosis X
À¯Àü¼º ÁøÇ༺ Á¡¾×¼ºÁ¶Á÷±¸Áõ
infantile progressive spinal muscular atrophy
¿µ¾ÆÁøÇ༺ ô¼ö¼º ±ÙÀ§Ãà(Áõ).
progressive
ÁøÇ༺
progressive
ÁøÇ༺ÀÇ(òäú¼àõ¡), Á÷Áø(¼º)ÀÇ(òÁòä(àõ)¡)
progressive bulbar palsy
ÁøÇ༺ ±¸<¿¬¼ö>¸¶ºñ(òäú¼àõϹ<æÅâÐ> Ýö).
progressive cardiomyopathic lentiginosis
ÁøÇ༺ ½É±Ùº´¼º ÈæÀÚÁõ
progressive case
ÁøÇ༺ ¿¹.
´ÙÀ½
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö ¸ÂÃã °Ë»ö °á°ú :
1
ÆäÀÌÁö:
1
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ÇѱÛ
progressive diffuse keratoderma
ÁøÇ༺ ±¤¹üÀ§ °¢ÇÇÁõ
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú :
15
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1
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keratosis extremitatum progrediens => progressive diffuse keratoderma
climacteric keratoderma
°»³â±â°¢ÇÇÁõ(¡ÊÇù«ñø)
epidermolytic palmoplantar keratoderma
Ç¥Çǹڸ®¼º ¼Õ¹ß¹Ù´Ú °¢ÇÇÁõ
hereditary plamoplantar keratoderma
À¯Àü¼º ¼Õ¹ß¹Ù´Ú°¢ÇÇÁõ
keratoderma
°¢ÇÇ(ÊÇù«).
keratoderma blenorrhagicum
³ó·ç¼º°¢ÇÇÁõ
keratoderma climactericum
°»³â±âÇǺΰ¢ÈÁõ
keratodermia = keratoderma ³ª
°¢ÇÇÁõ(ÊÇù«ñø)
mutilating palmoplantar keratoderma
Àý´Ü ¼Õ¹ß¹Ù´Ú °¢ÇÇÁõ
palmoplantar keratoderma
¼Õ¹ß¹Ù´Ú °¢ÇÇÁõ
papular palmoplantar keratoderma
±¸Áø¼º ¼Õ¹ß¹Ù´Ú °¢ÇÇÁõ
punctate keratoderma
Á¡»ó°¢ÇÇÁõ
symmetric keratoderma
´ëμº °¢ÇÇÁõ (¡ÊÇù«ñø)
tylosis palmaris et plantaris => palmoplantar keratoderma ³ª
¼öÀåÁ·Àú°¢È(Áõ)
degenerative diffuse cerebral sclerosis
ÅðÇ༺ ¹Ì¸¸¼º ³ú°æÈ(Áõ)(¡Ú¯Ø·àõ ÒàÌãûùñø).
´ÙÀ½
ÀÌ ¾Æ·¡ ºÎÅÍ´Â °á°ú°¡ ¾ø½À´Ï´Ù.
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö ¸ÂÃã °Ë»ö °á°ú :
0
ÆäÀÌÁö:
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ÅëÇÕ°Ë»ö ¿Ï·á
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