| porphyrin | <protein> Porphyrins are pigments found in both animal and plant life. They are all chelates with metals (Fe, Mg, Co, Zn, Cu, Ni) and constituents of haemoglobin, chlorophyll, cytochromes. Increased levels of coproporphyrins can indicate congenital erythropoietic porphyria or sideroblastic anaemia. Increased protoporphyrins may be seen in infection, thalassaemia, sideroblastic anaemia, iron deficient anaemia, increased erythropoiesis and lead poisoning. Increased uroporphyrins may indicate congenital erythropoietic porphyria or erythropoietic protoporphyria. (27 Sep 1997) |
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| porphyrin cytochrome c peroxidase | <enzyme> From yeast; haem group of cytochrome c peroxidase (EC 1.11.1.5) replaced by protoporphyrin ix Registry number: EC 1.11.1.- Synonym: pcc-peroxidase (26 Jun 1999) |
| porphyrinogen carboxy-lyase | <enzyme> Consider uroporphyrinogen decarboxylase Registry number: EC 4.1.1.- (26 Jun 1999) |
| porphyrinogens | Colourless reduced precursors of porphyrins in which the pyrrole rings are linked by methylene (-ch2-) bridges. (12 Dec 1998) |
| porphyrinopathy | A syndrome which results from abnormal porphyrin metabolism such as acute porphyria. Synonym: porphyrism. Origin: porphyrin + G. Pathos, disease (05 Mar 2000) |
| porphyrins | A group of compounds containing the porphin structure, four pyrrole rings connected by methine bridges in a cyclic configuration to which a variety of side chains are attached. The nature of the side chain is indicated by a prefix, as uroporphyrin, haematoporphyrin, etc. The porphyrins, in combination with iron, form the haem component in biologically significant compounds such as haemoglobin and myoglobin. (12 Dec 1998) |
| porphyrinuria | Excretion of porphyrins and related compounds in the urine. Synonym: porphyruria, purpurinuria. (05 Mar 2000) |
| blood porphyrin level | A test which is used to measure red blood cell porphyrin levels. Porphyrins are pigments found in both animal and plant life. This test is useful in evaluating any number of porphyrin disorders (involving the various porphyrins) of red blood cells. Increased levels of coproporphyrins can indicate congenital erythropoietic porphyria or sideroblastic anaemia. Increased protoporphyrins may be seen in infection, thalassaemia, sideroblastic anaemia, iron deficient anaemia, increased erythropoiesis and lead poisoning. Increased uroporphyrins may indicate congenital erythropoietic porphyria or erythropoietic protoporphyria. (27 Sep 1997) |
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