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"polyendocrinopathies, autoimmune"¿¡ ´ëÇÑ ¼¼ºÎ °Ë»ö °á°úÀÔ´Ï´Ù
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  • Polyendocrinopathies, Autoimmune - »õâ Autoimmune diseases affecting multiple endocrine organs. Type I is characterized by childhood onset and chronic mucocutaneous candidiasis (CANDIDIASIS, CHRONIC MUCOCUTANEOUS), while type II exhibits any combination of adrenal insufficiency (ADDISON'S DISEASE), lymphocytic thyroiditis (THYROIDITIS, AUTOIMMUNE;), HYPOPARATHYROIDISM; and gonadal failure. In both types organ-specific ANTIBODIES against a variety of ENDOCRINE GLANDS have been detected. The type II syndrome differs from type I in that it is associated with HLA-A1 and B8 haplotypes, onset is usually in adulthood, and candidiasis is not present.
    Synonyms : Autoimmune Polyglandular Syndrome Type I, Autoimmune Polyglandular Syndrome Type II, Autoimmune Polyendocrinopathies, Autoimmune Polyendocrinopathy, Autoimmune Polyendocrinopathy Candidiasis Ectodermal Dystrophy, Polyendocrinopathy, Autoimmune
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MeSH(Medical Subject Headings) À¯»ç °Ë»ö (http://www.nlm.nih.gov) °á°ú : 0 ÆäÀÌÁö: 1
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