| mucopolysaccharidosis IH |
MPS due to a deficiency of the enzyme α-L-iduronidase with accumulation of dermatan sulfate and heparan sulfate. Clinically, there are lens opacities, coarse facies, skeletal dyspl
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| mucopolysaccharidosis IHS |
Hurler-Scheie syndrome. An intermediate form of MPS between MPS IH and MPS IS, due to the same enzyme deficiency. Mental development may be normal.
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| mucopolysaccharidosis IS |
MPS due to the same enzyme defect as MPS IH and with similar clinical characteristics, except mental retardation is absent. SYN: Scheie's syndrome.
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