| methylglutaconyl-CoA hydratase |
[EC 4.2.1.18] an enzyme of the lyase class that catalyzes the hydration of 3-methylglutaconyl CoA to form 3-hydroxy-3-methylglutaryl CoA, a step in the catabolism of leucine. Deficiency of the enzyme, an autosomal recessive trait, causes 3-methylglutaconicaciduria.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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