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lipoamide dehydrogenase (lipo
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lipoamide dehydrogenase deficiency (lipo
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lipoamide lipoic acid in amide linkage with lysine side chains of enzymes of the α-ketoglutarate dehydrogenase, branched-chain α-keto acid dehydrogenase, and pyruvate dehydrogenase complexes (q.v.). Its reactive disulfide group and long, flexible chain enable it to transfer intermediates among the enzymes of each complex.
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