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"leukodystrophy with diffuse Rosenthal fiber formation"¿¡ ´ëÇÑ ´ëÇÑÀÇÇù ÀÇÇпë¾î ¼¼ºÎ °Ë»ö °á°úÀÔ´Ï´Ù
À̰ÍÀ» ¿øÇϼ̽À´Ï±î?
leukodystrophy with diffuse Rosenthal fibre formation
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú :
15
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ÇѱÛ
basal vein of Rosenthal
·ÎÁ¨Å»¹Ù´ÚÁ¤¸Æ, ·ÎÁ¨Å»±âÀúÁ¤¸Æ
globoid cell leukodystrophy
°ø¼¼Æ÷¹é»öÁúÀå¾Ö, ±¸Çü¼¼Æ÷¹éÁúµð½ºÆ®·ÎÇÇ
leukodystrophy
¹é»öÁúÇü¼ºÀå¾Ö(Áõ), ¹éÁúµð½ºÆ®·ÎÇÇ
metachromatic leukodystrophy
ÀÌ¿°»ö¹é»öÁúÀå¾Ö, ÀÌ¿°¼º¹éÁúµð½ºÆ®·ÎÇÇ
aqueous formation
¹æ¼öÇü¼º
adipocere formation
½Ã¶øÇü¼º
compromise formation
ÀýÃæÇü¼º
concept formation
°³³äÇü¼º
cystic formation
³¶Çü¼º
formation
1. Çü¼º 2. Çüü, ü
rouleau formation
¿¬Àü»óÇü¼º
reaction formation
¹ÝÀÀÇü¼º, ¹Ýµ¿Çü¼º
reticular formation
±×¹°Ã¼, ¸Á»óü
rosette formation
·ÎÁ¦Æ®Çü¼º
degenerative diffuse cerebral sclerosis
ÅðÇ౤¹üÀ§´ë³ú°æÈ(Áõ)
´ÙÀ½
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú :
15
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1
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ÇѱÛ
leukodystrophy
¹é»öÁúÇü¼ºÀå¾Ö(Áõ)
formation
Çü¼º, Çüü
reaction formation
¹Ýµ¿Çü¼º, ¹ÝÀÀÇü¼º
diffuse goiter
±¤¹üÀ§°©»ó»ùÁ¾, ¹Ì¸¸°©»ó»ùÁ¾
diffuse esophageal spasm
±¤¹üÀ§½Äµµ¿¬Ãà
fiber
¼¶À¯
afferent nerve fiber
µé½Å°æ¼¶À¯
nerve fiber
½Å°æ¼¶À¯
parallel fiber
ÆòÇ༶À¯
postganglionic nerve fiber
½Å°æÀýÀÌÈļ¶À¯
preganglionic nerve fiber
½Å°æÀýÀÌÀü¼¶À¯
Purkinje fiber
½ÉÀåÀüµµ±ÙÀ°¼¶À¯, Ǫ¸£Å°´Ï¿¡¼¶À¯
red muscle fiber
Àû»ö±ÙÀ°¼¶À¯, Àû»ö±ÙÀ°¼¼Æ÷
reticular fiber
±×¹°¼¶À¯, ¸Á»ó¼¶À¯
smooth muscle fiber
¹Î¹«´Ì±ÙÀ°¼¶À¯, ¹Î¹«´Ì±ÙÀ°¼¼Æ÷
´ÙÀ½
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú :
15
ÆäÀÌÁö:
1
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ÇѱÛ
globoid cell leukodystrophy
°ø¼¼Æ÷¹é»öÁúÀå¾Ö
leukodystrophy
¹é»öÁúÀå¾Ö
metachromatic leukodystrophy
ÀÌ¿°»ö¹é»öÁúÀå¾Ö
adipocere formation
½Ã¶øÇü¼º
aqueous formation
¹æ¼öÇü¼º
compromise formation
ÀýÃæÇü¼º
concept formation
°³³äÇü¼º
cystic formation
³¶Çü¼º
formation
Çü¼º, Çüü
free radical formation toxicity
ÀÚÀ¯·¡µðÄ®Çü¼ºµ¶¼º
reaction formation
¹Ýµ¿Çü¼º, ¹ÝÀÀÇü¼º
reticular formation
±×¹°Ã¼
rosette formation
·ÎÁ¦Æ®Çü¼º
rouleau formation
¿°ÁÖÇü¼º
diffuse aneurysm
±¤¹üÀ§µ¿¸ÆÀÚ·ç, ±¤¹üÀ§µ¿¸Æ·ù
´ÙÀ½
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú :
15
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1
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ÇѱÛ
Fuchs-Rosenthal chamber
Ç«½º-·ÎÁ¨Å»¹æ
Melkersson-Rosenthal syndrome
¸áÄ¿½¼ ·ÎÁ¨Å» ÁõÈıº
Rosenthal-Kloepfer syndrome
·ÎÁ¨Å» Ŭ·Î¿¡ÆÛ ÁõÈıº
Hamman Rich syndrome =diffuse interstitial pulmonary fibrosis
ÇØ¸Õ- ¸®Ä¡ÁõÈıº.
glomerulonephritis,diffuse proliferative
¹Ì¸¸¼º Áõ½Ä¼º(ڵؼàõ ñòãÖàõ)
goiter,diffuse nontoxic(simple)
¹Ì¸¸¼º ºñµ¶¼º(´Ü¼ø)
progressive diffuse keratoderma
ÁøÇ༺ ±¤¹üÀ§ °¢ÇÇÁõ
adipocere formation
½Ã¶ø Çü¼º
ammonia formation
¾Ï¸ð´Ï¾ÆÇü¼º
antibody formation
Ç×üÇü¼º(ù÷ô÷û¡à÷).
aqueous formation
(¾È)¹æ¼öÇü¼º(äÑۮ⩠û¡à÷).
free radical formation
ÀÚÀ¯ ·¡µðÄ® Çü¼º
free radical formation,irradation injury
ÀÚÀ¯ ·¡µðÄ® Çü¼º, ¹æ»ç¼± ¼Õ»ó(Û¯ÞÒàÊ áßß¿)
free radical formation,lipid peroxidation
ÀÚÀ¯ ·¡µðÄ® Çü¼º, ÁöÁú °ú»êÈ(ò·òõ Φ߫ûù)
immunoglobulin M formation
¸é¿ª±Û·ÎºÒ¸° M Çü¼º
´ÙÀ½
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú :
15
ÆäÀÌÁö:
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ÇѱÛ
rosenthal fiber
·ÎÁ¨Å»¼¶À¯(àéë«)
syndrome, Melkersson-Rosenthal
¸áÄ¿½¼ ·ÎÁ¨Å» ÁõÈıº
leukodystrophy
¹éÁú ÀÌ¿µ¾çÁõ
leukodystrophy =leukodystropia
¹éÁúÀÌ¿µ¾çÁõ(ÛÜòõì¶ç½å×ñø)
leukodystrophy,globoid cell(body)
±¸¼ºÃ¼(ϰà÷ô÷)
leukodystrophy,metachromatic
ÀÌ¿°¼º(ì¶æúàõ)ÀÇ
metachromatic leukodystrophy
ÀÌ¿°¼º ¹éÁú(ܨßäàõÛÜòõ)ÀÌ¿µ¾çÁõ.
metachromatic leukodystrophy
ÀÌ¿°¼º ¹éÁú(¡ÛÜòõ) ÀÌ¿µ¾çÁõ
metachromatic leukodystrophy
ÀÌÇü¼º ¸ÆÁúÀÌ¿µ¾çÁõ
ascending nerve fiber, climbing fiber
¿À¸§¼¶À¯
perforating fiber [sharpeys fiber]
½Ã¸àÆ®Áú°üÅë¼¶À¯
degenerative diffuse cerebral sclerosis
ÅðÇ༺ ¹Ì¸¸¼º ³ú°æÈ(Áõ)(¡Ú¯Ø·àõ ÒàÌãûùñø).
diffuse
¹Ì¸¸¼º, »êÀ缺
diffuse abscess
¹Ì¸¸¼º ³ó¾ç(¡³ó¾ç).
diffuse alveolar damage
¹Ì¸¸¼ºÆóÆ÷¼Õ»ó(¡øËøàáßß¿)
´ÙÀ½
ÀÌ ¾Æ·¡ ºÎÅÍ´Â °á°ú°¡ ¾ø½À´Ï´Ù.
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