| isovaleryl |
the radical of isovaleric acid; the thioester formed with coenzyme A, isovaleryl CoA, is an intermediate in the catabolism of leucine.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
|---|---|
| isovaleryl-CoA dehydrogenase |
[EC 1.3.99.10] an enzyme of the oxidoreductase class that catalyzes the dehydrogenation of isovaleryl CoA to 3-methylcrotonyl CoA, using ubiquinone as an electron acceptor. The reaction is a step in the use of leucine as a fuel. Deficiency of the enzyme, an autosomal recessive trait, results in isovalericacidemia.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
| isovalerylglycine |
a conjugate of isovaleric acid and the amide group of glycine; high levels are formed and excreted in the urine in isovalericacidemia.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|