| iduronidase | <enzyme> An enzyme that hydrolyzes iduronosidic linkages in desulfated dermatan. Deficiency of this enzyme produces hurler's syndrome. Chemical name: Glycosaminoglycan alpha-L-iduronohydrolase Registry number: EC 3.2.1.76 (12 Dec 1998) |
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| alpha-l-iduronidase | <enzyme> An enzyme that hydrolyzes terminal desulfated alpha-l-iduronic acid residues of dermatan sulfate and of heparan sulfate; a deficiency of this enzyme is associated with Hurler syndrome and Scheie syndrome. (05 Mar 2000) |
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