| iduronate |
a salt, ester, or anionic form of iduronic acid.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| iduronate-2-sulfatase |
[EC 3.1.6.13] a lysosomal enzyme of the hydrolase class that catalyzes the cleavage of sulfate groups from the L-iduronate residues of dermatan sulfate and heparan sulfate, a step in the degradation of these glycosaminoglycans. Deficiency of the enzyme, an X-linked recessive trait, results in Hunter's syndrome (mucopolysaccharidosis II).
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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