| ichthyosiform erythroderma | A genodermatosis characterised by diffuse chronic erythema and scale formation which may be separated into bullous and nonbullous forms. Synonym: ichthyosiform erythroderma, ichthyosis spinosa, keratoma malignum. (05 Mar 2000) |
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| ichthyosiform erythroderma, congenital | Designation for several severe forms of ichthyosis, present at birth, that are characterised by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalised scaling. The forms include bullous (hyperkeratosis, epidermolytic), non-bullous (ichthyosis, lamellar), wet type, and dry type. (12 Dec 1998) |
| bullous congenital ichthyosiform erythroderma | Diffusely red, eroded skin at birth, with subsequent scaling, tending to improve in later life, characterised by generalised epidermolytic hyperkeratosis and autosomal dominant inheritance. See: epidermolytic hyperkeratosis. Synonym: generalised epidermolytic hyperkeratosis, ichthyismus hystrix, ichthyosis hystrix. (05 Mar 2000) |
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| congenital ichthyosiform erythroderma | A genodermatosis characterised by diffuse chronic erythema and scale formation which may be separated into bullous and nonbullous forms. Synonym: ichthyosiform erythroderma, ichthyosis spinosa, keratoma malignum. (05 Mar 2000) |
| nonbullous congenital ichthyosiform erythroderma | Erythroderma or a collodion membrane at birth, usually without improvement during childhood, characterised by proliferation of epidermal keratinocytes with lipid accumulation; autosomal recessive inheritance. (05 Mar 2000) |
| Sezary erythroderma | <syndrome> A form of cutaneous T-cell lymphoma manifested by generalised exfoliative erythroderma, intense pruritus, peripheral lymphadenopathy, and abnormal hyperchromatic mononuclear cells in the skin, lymph nodes, and peripheral blood (sezary cells). (12 Dec 1998) |
| erythroderma | A non-specific designation for intense and usually widespread reddening of the skin from dilatation of blood vessels, often preceding, or associated with exfoliation. Synonym: erythrodermatitis. Origin: erythro-+ G. Derma, skin (05 Mar 2000) |
| erythroderma desquamativum | Severe, extensive seborrheic dermatitis with exfoliative dermatitis, generalised lymphoadenopathy, and diarrhoea in the newborn; frequently occurs in undernourished, cachectic children. Synonym: Leiner's disease. (05 Mar 2000) |
| erythroderma exfoliativa | Familial continual skin peeling characterised by a separation of stratum corneum in leaflike flakes occurring everywhere except on the palms and soles; the cause is unknown. Synonym: erythema exfoliativa, erythroderma exfoliativa. (05 Mar 2000) |
| erythroderma psoriaticum | Extensive exfoliative dermatitis simulating psoriasis. (05 Mar 2000) |