Glutaryl-CoA Dehydrogenase - ț̢
A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase.
Synonyms : Glutaryl CoA Dehydrogenase, Glutaryl-Coenzyme A Dehydrogenase, CoA Dehydrogenase, Glutaryl, Dehydrogenase, Glutaryl CoA, Dehydrogenase, Glutaryl-CoA, Dehydrogenase, Glutaryl-Coenzyme A, Glutaryl Coenzyme A Dehydrogenase