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glucosylceramidase <enzyme> A glycosidase that hydrolyzes a glucosylceramide to yield free ceramide plus glucose. Deficiency of this enzyme leads to abnormally high concentrations of glucosylceramide in the brain in gaucher's disease.
Chemical name: D-Glucosyl-N-acylsphingosine glucosylhydrolase
Registry number: EC 3.2.1.45
(12 Dec 1998)
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