| alpha-GalCer | Alpha-galactosylceramide |
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| galactosylceramide | A sphingolipid that accumulates in individuals with Krabbe's disease. (05 Mar 2000) |
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| galactosylceramide lipoidosis | <radiology> Dysmyelinating disease, autosomal recessive, usually presents by 1 yr, specific enzyme deficiency identified, rapid spontaneous nystagmus, poikilothermia Synonym: Krabbe leukodystrophy (12 Dec 1998) |
| galactosylceramide sulfotransferase | <enzyme> Models for the study of inborn errors of metabolism Registry number: EC 2.8.2.11 Synonym: cerebroside sulfotransferase, galactocerebroside sulfotransferase, glycosphingolipid sulfotransferase, galcst, glycolipid sulfotransferase, galcer-st, galactosylceramide sulphotransferase (26 Jun 1999) |
| galactosylceramides | Cerebrosides which contain as their polar head group a galactose moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in beta-galactosidase, is the cause of galactosylceramide lipidosis or globoid cell leukodystrophy. (12 Dec 1998) |
| galactosyl(alpha 1-4)galactosylceramide galactosyl hydrolase | <enzyme> Active in pH 3.0 component of human plasma (pn-a-2); greatly decreased in fabry's disease Registry number: EC 3.2.1.- Synonym: digalactosylceramidase (26 Jun 1999) |
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Synonyms : Ceramides, Galactosyl
| galactosylceramide |
galactocerebroside.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| galactosylceramide β-galactosidase |
galactosylceramidase.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| galactosylceramide l. |
Krabbe's disease.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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