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MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 3 ÆäÀÌÁö: 1
  • Galactosylceramidase - »õâ An enzyme that hydrolyzes galactose from ceramide monohexosides. Deficiency of this enzyme may cause globoid cell leukodystrophy (LEUKODYSTROPHY, GLOBOID CELL). EC 3.2.1.46.
    Synonyms : Galactosylceramide Galactosidase, Galactosylceramide beta-Galactosidase, Galactosylcerebroside beta-Galactosidase, Galactosidase, Galactosylceramide, beta-Galactosidase, Galactosylceramide, beta-Galactosidase, Galactosylcerebroside
  • Galactosylceramides - »õâ Cerebrosides which contain as their polar head group a galactose moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in beta-galactosidase, is the cause of galactosylceramide lipidosis or globoid cell leukodystrophy.
    Synonyms : Ceramides, Galactosyl
  • Galactosyltransferases - »õâ Enzymes that catalyze the transfer of galactose from a nucleoside diphosphate galactose to an acceptor molecule which is frequently another carbohydrate. EC 2.4.1.-.
    Synonyms :
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MeSH(Medical Subject Headings) À¯»ç °Ë»ö (http://www.nlm.nih.gov) °á°ú : 0 ÆäÀÌÁö: 1
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