| dihydrolipoamide acetyltransferase | <enzyme> Part of the pyruvate dehydrogenase complex; acef isolated from e. Coli Registry number: EC 2.3.1.12 Synonym: dihydrolipoyl transacetylase, lipoate acetyltransferase, dihydrolipoyl acetyltransferase, acef gene product (26 Jun 1999) |
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| dihydrolipoamide acyltransferase | <enzyme> Component of branched-chain 2-oxo acid dehydrogenase multienzyme complex; mutation in this (e2) catalytic subunit identifies type II maple syrup urine disease Registry number: EC 2.3.1.- Synonym: dihydrolipoyl transacylase, branched chain acyltransferase, e2 transacylase (26 Jun 1999) |
| dihydrolipoamide dehydrogenase | <enzyme> An enzyme oxidizing dihydrolipoamide at the expense of NAD+; completes the oxidative decarboxylation of pyruvate; a part of several enzyme complexes (e.g., alpha-ketoglutarate dehydrogenase complex). Decreased activity leads to neuronal loss in brain resulting in psychomotor retardation. Synonym: coenzyme factor, lipoamide dehydrogenase, lipoamide reductase (NADH), lipoyl dehydrogenase. (05 Mar 2000) |
| dihydrolipoamide succinyltransferase | <enzyme> Component of the ketoglutarate dehydrogenase complex Registry number: EC 2.3.1.61 Synonym: succinyl-CoA-dihydrolipoate-s-succinyltransferase, dihydrolipoyl transsuccinylase, lipoyl transsuccinylase, lipoate succinyltransferase, lipoamide succinyltransferase, succinyl-coenzyme a-dihydrolipoate-s-succinyltransferase (26 Jun 1999) |