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  • multiple exostoses =diaphyseal aclasis
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  • multiple exostosis =diaphyseal aclasis
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diaphysial aclasis A disturbance of enchondral bone growth in which multiple, generally benign osteochondromas of long bones appear during childhood, commonly with shortening of the radius and fibula; the ill-effects are usually mechanical but malignant change is rare; autosomal dominant inheritance.
Synonym: diaphysial aclasis, hereditary deforming chondrodystrophy, multiple exostosis, osteochondromatosis.
(05 Mar 2000)
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aclasis A state of continuity between normal and abnormal tissue.
Synonym: aclasia.
Origin: G. A-priv. + klasis, a breaking away, a fragment
(05 Mar 2000)
tarsoepiphyseal aclasis Epiphysealis hemimelica, affects ankles and knees leading to limitation of motion.
Synonym: Trevor's disease.
(05 Mar 2000)
diaphysial Relating to a diaphysis.
Synonym: diaphyseal.
(05 Mar 2000)
diaphysial centre Primary centre of ossification in the shaft of a long bone.
(05 Mar 2000)
diaphysial dysplasia Progressive, symmetrical fusiform enlargement of the shafts of long bones characterised by the formation of excessive new periosteal and endosteal bone and irregular conversion of this cortical bone into cancellous bone; anaemia does not occur as a rule, as in osteopetrosis.
Synonym: Engelmann's disease.
(05 Mar 2000)
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