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COPRO coproporphyrin
CP candle power; capillary pressure; cardiac pacing; cardiac performance; cardiopulmonary; caudate puta...
ECP ectrodactyly-cleft palate [syndrome]; effector cell precursor; endocardial potential; eosinophil cat...
FEC forced expiratory capacity; free erythrocyte coproporphyrin; freestanding emergency center; Friend e...
FECP free erythrocyte coproporphyrin
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COPRO coproporphyrin
CP coproporphyrin
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coproporphyrin A test which is used to measure red blood cell porphyrin levels. Porphyrins are pigments found in both animal and plant life. This test is useful in evaluating any number of porphyrin disorders (involving the various porphyrins) of red blood cells. Increased levels of coproporphyrins can indicate congenital erythropoietic porphyria or sideroblastic anaemia. Increased protoporphyrins may be seen in infection, thalassaemia, sideroblastic anaemia, iron deficient anaemia, increased erythropoiesis and lead poisoning. Increased uroporphyrins may indicate congenital erythropoietic porphyria or erythropoietic protoporphyria.
(27 Sep 1997)
coproporphyrinogen See: porphyrinogens.
Coproporphyrinogen oxidase, an enzyme that catalyses a step in porphyrin biosynthesis, reacting coproporphyrinogen-III and O2 to form protoporphyrinogen-IX and 2CO2. A deficiency of this enzyme will result in hereditary coproporphyria.
(05 Mar 2000)
coproporphyrinogen oxidase <enzyme> One of the enzymes active in haem biosynthesis. It catalyses the oxidative decarboxylation of coproporphyrinogen III to protoporphyrinogen III by the conversion of two propionic acid groups to two vinyl groups. It can act under both aerobic and anaerobic conditions.
Chemical name: Coproporphyrinogen:oxygen oxidoreductase (decarboxylating)
Registry number: EC 1.3.3.3
(12 Dec 1998)
coproporphyrinogens Porphyrinogens which are intermediates in the haem biosynthesis. They have four methyl and four propionic acid side chains attached to the pyrrole rings. Coproporphyrinogens I and III are formed in the presence of uroporphyrinogen decarboxylase from the corresponding uroporphyrinogen. They can yield coproporphyrins by autooxidation or protoporphyrin by oxidative decarboxylation.
(12 Dec 1998)
coproporphyrins Porphyrins with four methyl and four propionic acid side chains attached to the pyrrole rings. Coproporphyrin III is excreted in the feces of persons with hereditary coproporphyria.
(12 Dec 1998)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 3 ÆäÀÌÁö: 1
  • Coproporphyrinogen Oxidase - »õâ An enzyme that catalyzes the oxidative decarboxylation of coproporphyrinogen III to protoporphyrinogen IX by the conversion of two propionate groups to two vinyl groups. It is the sixth enzyme in the 8-enzyme biosynthetic pathway of HEME, and is encoded by CPO gene. Mutations of CPO gene result in HEREDITARY COPROPORPHYRIA.
    Synonyms : Coproporphyrinogen III Oxidases, III Oxidases, Coproporphyrinogen, Oxidase, Coproporphyrinogen, Oxidases, Coproporphyrinogen III
  • Coproporphyrinogens - »õâ Porphyrinogens which are intermediates in the heme biosynthesis. They have four methyl and four propionic acid side chains attached to the pyrrole rings. Coproporphyrinogens I and III are formed in the presence of uroporphyrinogen decarboxylase from the corresponding uroporphyrinogen. They can yield coproporphyrins by autooxidation or protoporphyrin by oxidative decarboxylation.
    Synonyms :
  • Coproporphyrins - »õâ Porphyrins with four methyl and four propionic acid side chains attached to the pyrrole rings. Elevated levels of Coproporphyrin III in the urine and feces are major findings in patients with HEREDITARY COPROPORPHYRIA.
    Synonyms :
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coproporphyrinogen (cop
Ãâó: www.mercksource.com/pp/us/cns/cns_hl_dorlands.jspz...
coproporphyrinogen oxidase (cop
Ãâó: www.mercksource.com/pp/us/cns/cns_hl_dorlands.jspz...
coproporphyrin (cop
Ãâó: www.mercksource.com/pp/us/cns/cns_hl_dorlands.jspz...
coproporphyrinuria (cop
Ãâó: www.mercksource.com/pp/us/cns/cns_hl_dorlands.jspz...
coproporphyrinuria Excess coproporphyrin in the urine.
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