| chronic progressive chorea | A progressive disorder usually beginning in young to middle age, consisting of a triad of choreoathetosis, dementia, and autosomal dominant inheritance with complete penetrance. Bilateral marked wasting of the putamen and the head of the caudate nucleus is characteristic. Synonym: chronic progressive chorea, degenerative chorea, hereditary chorea, Huntington's disease. (05 Mar 2000) |
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| chronic progressive external ophthalmoplegia | A specific type of slowly worsening weakness of the ocular muscles, usually associated with a pigmentary retinopathy. See: Kearns-Sayre syndrome, oculopharyngeal dystrophy. Synonym: ocular myopathy. (05 Mar 2000) |
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| chronic progressive syphilitic meningoencephalitis | Syphilitic infection manifested as dementia (often with delusional features), dysarthria, seizures, myoclonic jerks, action tremor, impaired walking and standing, pupillary abnormalities, and abnormal CSF findings. Synonym: chronic progressive syphilitic meningoencephalitis. (05 Mar 2000) |
| ophthalmoplegia, chronic progressive external | One of the mitochondrial encephalomyopathies characterised by slowly progressive paralysis of the extraocular muscles. Muscle biopsies disclose the characteristic ragged red fibres and large numbers of mitochondria with deleted DNA. (12 Dec 1998) |
| acanthocytosis with chorea | A slowly progressive familial chorea with associated mental deterioration, diminished deep tendon reflexes, bilateral atrophy of the putamen and caudate nuclei and acanthocytosis (thorny appearance of blood erythrocytes); the disorder typically begins around late adolescence; inheritance is usually autosomal recessive. Synonym: acanthocytosis with chorea. (05 Mar 2000) |
| acute chorea | A postinfectious chorea appearing several months after a streptococcal infection with subsequent rheumatic fever. The chorea typically involves the distal limbs and is associated with hypotonia and emotional lability. Improvement occurs over weeks or months and exacerbations occur without associated infection recurrence. Synonym: acute chorea, chorea minor, chorea, juvenile chorea, rheumatic chorea, Sydenham's disease. (05 Mar 2000) |
| benign familial chorea | A rare, nonprogressive movement disorder characterised by chorea and athetosis appearing in early childhood, most commonly manifested as gait ataxia and upper limb coordination. Intellect is unaffected. Probably autosomal-dominance inheritance with incomplete penetrance. (05 Mar 2000) |
| rheumatic chorea | A postinfectious chorea appearing several months after a streptococcal infection with subsequent rheumatic fever. The chorea typically involves the distal limbs and is associated with hypotonia and emotional lability. Improvement occurs over weeks or months and exacerbations occur without associated infection recurrence. Synonym: acute chorea, chorea minor, chorea, juvenile chorea, rheumatic chorea, Sydenham's disease. (05 Mar 2000) |
| rhythmic chorea | Patterned movement in conversion hysteria. (05 Mar 2000) |
| chorea | Mature onset disease characterised by progressive loss of neuronal functioning. Caused by unstable amphlification of a trinucleotide (CAG)n repeat with the coding region of a gene encoding a 348 kD, widely exposed product. (18 Nov 1997) |
| chorea-acanthocytosis | A slowly progressive familial chorea with associated mental deterioration, diminished deep tendon reflexes, bilateral atrophy of the putamen and caudate nuclei and acanthocytosis (thorny appearance of blood erythrocytes); the disorder typically begins around late adolescence; inheritance is usually autosomal recessive. Synonym: acanthocytosis with chorea. (05 Mar 2000) |
| chorea cordis | Cardiac irregularity related to chorea. (05 Mar 2000) |
| chorea dimidiata | Chorea involving the muscles on one side only. Synonym: chorea dimidiata, hemilateral chorea. (05 Mar 2000) |
| chorea gravidarum | Sydenham's chorea occurring in pregnancy. (05 Mar 2000) |
| chorea major | A spasmodic attack occurring in patients with conversion hysteria. (05 Mar 2000) |
| chorea minor | A postinfectious chorea appearing several months after a streptococcal infection with subsequent rheumatic fever. The chorea typically involves the distal limbs and is associated with hypotonia and emotional lability. Improvement occurs over weeks or months and exacerbations occur without associated infection recurrence. Synonym: acute chorea, chorea minor, chorea, juvenile chorea, rheumatic chorea, Sydenham's disease. (05 Mar 2000) |