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  • cerebroside sulfatase
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CST Cerebroside sulfotransferase
CBS cerebroside sulfate
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cerebroside <biochemistry> Glycolipid found in brain (11% of dry matter). Sphingosine core with fatty amide or hydroxy fatty amide and a single monosaccharide on the alcohol group (either glucose or galactose).
(18 Nov 1997)
cerebroside lipidosis <disease> A chronic congenital disease of lipid metabolism caused by a deficiency of the beta-glucocerebrosidase enzyme. The defect is most common in Ashkenazi Jews. Clinical features are hepatosplenomegaly (enlargement of liver and spleen) and in severe early onset forms of the disease, with neurological dysfunction.
Inheritance: autosomal recessive.
(27 Sep 1997)
cerebroside-sulfatase <enzyme> An enzyme that catalyses the hydrolysis of cerebroside 3-sulfate (sulfatide) to yield a cerebroside and inorganic sulfate. A marked deficiency of arylsulfatase a, which is considered the heat-labile component of cerebroside sulfatase, has been demonstrated in all forms of metachromatic leukodystrophy (leukodystrophy, metachromatic).
Chemical name: Cerebroside-3-sulfate 3-sulfohydrolase
Registry number: EC 3.1.6.8
(12 Dec 1998)
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  • Cerebroside-Sulfatase - »õâ An enzyme that catalyzes the hydrolysis of cerebroside 3-sulfate (sulfatide) to yield a cerebroside and inorganic sulfate. A marked deficiency of arylsulfatase A, which is considered the heat-labile component of cerebroside sulfatase, has been demonstrated in all forms of metachromatic leukodystrophy (LEUKODYSTROPHY, METACHROMATIC). EC 3.1.6.8.
    Synonyms : Cerebroside Sulfatase, Sulfatase, Sulfatidate
  • Cerebrosides - »õâ Neutral glycosphingolipids that contain a monosaccharide, normally glucose or galactose, in 1-ortho-beta-glycosidic linkage with the primary alcohol of an N-acyl sphingoid (ceramide). In plants the monosaccharide is normally glucose and the sphingoid usually phytosphingosine. In animals, the monosaccharide is usually galactose, though this may vary with the tissue and the sphingoid is usually sphingosine or dihydrosphingosine. (From Oxford Dictionary of Biochemistry and Molecular Biology, 1st ed)
    Synonyms :
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cerebroside sulfatase [EC 3.1.6.8] an enzyme of the hydrolase class that catalyzes the cleavage of sulfate residues from sulfatides to form cerebrosides. Deficiency of the enzyme, an autosomal recessive trait, is one of the causes of metachromatic leukodystrophy. Called also arylsulfatase A.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
cerebroside leiten sich von den Ceramiden ab: Verbindung von Zucker u. Ceramiden
Ãâó: www.laserwelt.com/haarentfernung-laser-glossar/cou...
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