| CPS | Carbamyl Phosphate Synthetase |
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| G3P, | G-3-P glyceraldehyde-3-phosphate; glycerol-3-phosphate |
| GPD | glucose-6-phosphate dehydrogenase; glycerol-phosphate dehydrogenase |
| PD | Doctor of Pharmacy; Dublin Pharmacopoeia; interpupillary distance; Paget disease; pancreatic duct; p... |
| PPP | pain perception profile; palatopharyngoplasty; palmoplantar pustulosis; pentose phosphate pathway; p... |
| CPS | Carbamoyl phosphate synthetase |
|---|---|
| CPSase | Carbamoyl phosphate synthetase |
| CP | Carbamoyl phosphate |
| 2-5A synthetase | 2', 5'-oligoadenylate synthetase |
| OCTase | Ornithine carbamoyl transferase |
| carbamoyl phosphate synthetase | A phosphotransferase catalyzing the formation of carbamoyl phosphate. There are two significant isozymes. Carbomoyl phosphate synthetase I is a mitochondrial enzyme that catalyses the reaction of 2ATP, NH3, CO2, and H2O to carbamoyl phosphate, 2ADP, and Pi. It is activated by N-acetylglutamate and participates in urea biosynthesis. A deficiency of carbamoyl phosphate synthetase I can result in hyperammonaemia. Carbamoyl phosphate synthetase II is a cytosolic enzyme that, under physiological conditions, uses l-glutamine as the nitrogen source (producing l-glutamate) instead of NH3, is not activated by N-acetylglutamate, and is found in pyrimidine biosynthesis. (05 Mar 2000) |
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| carbamoyl phosphate | H2NCO-OPO32-;a reactive intermediate capable of transferring its carbamoyl group (H2NCO-) to an acceptor molecule, forming citrulline from ornithine in the urea cycle, and ureidosuccinic acid from aspartic acid in pyrimidine ring formation. (05 Mar 2000) |
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| carbamoyl-phosphate synthase (ammonia) | <enzyme> An enzyme that catalyses the formation of carbamoyl phosphate from ATP, carbon dioxide, and ammonia. This enzyme is specific for arginine biosynthesis or the urea cycle. Chemical name: Carbon dioxide:ammonia ligase (ADP-forming, carbamate-phosphorylating) Registry number: EC 6.3.4.16 (12 Dec 1998) |
| carbamoyl-phosphate synthase (glutamine-hydrolyzing) | <enzyme> An enzyme that catalyses the formation of carbamoyl phosphate from ATP, carbon dioxide, and glutamine. This enzyme is important in the de novo biosynthesis of pyrimidines. Chemical name: Carbon dioxide:L-glutamine amido-ligase (ADP-forming, carbamate-phosphorylating) Registry number: EC 6.3.5.5 (12 Dec 1998) |
| carbamoyl | The acyl radical, NH2-CO-, the transfer of which plays an important role in certain biochemical reactions; e.g., in the urea cycle, via carbamoyl phosphate. (05 Mar 2000) |
| carboxyl and carbamoyl transferases | <enzyme> A group of enzymes that catalyze the transfer of carboxyl- or carbamoyl- groups. Registry number: EC 2.1.3 (12 Dec 1998) |
| N-carbamoyl-D-amino acid amidohydrolase | <enzyme> From comamonas sp.e222c; mw 120 kD; hydrolyzes d-enantiomers of various n-carbamoyl-d-amino acids to d-amino acids, ammonia and co2; sensitive to thiol reagents; does not require metal ions Registry number: EC 3.5.1.- Synonym: caa-amidohydrolase, carbamoyl d-aa amidohyrolase (26 Jun 1999) |
| 1-carbamoyl-L-amino acid amidohydrolase | <enzyme> From bacillus stearothermophilus; amino acid sequence given in first source Registry number: EC 3.5.1.- Synonym: carbamoyl l-aa amidohydrolase, n-carbamyl-l-amino acid amidohydrolase (26 Jun 1999) |
| bis(monoacylglycero)phosphate synthetase | <enzyme> Converts phosphatidylglycerol, 1-acyl- or 2-acyllysophosphatidylglycerol to bis(monoacylglycero)phosphate Registry number: EC 2.3.1.- (26 Jun 1999) |
| hexose phosphate synthetase | <enzyme> Ribulosephosphate formaldehyde gives d-erythro-l-glycero-3-hexulose Registry number: EC 4.1.2.- Synonym: 3-hexulose phosphate synthase, d-arabino-3-hexulose 6-phosphate formaldehyde-lyase, 3-hexulosephosphate synthase, d-arabino-3-hexulose-6-phosphate-lysase, hexulose-6-phosphate synthase, hump synthase (26 Jun 1999) |
| N-(5-amino-1-ribosyl-4-imidazolylcarbonyl)-L-aspartic acid 5'-phosphate synthetase | <enzyme> 5-amino-1-ribosyl-4-imidazole carboxylic acid 5'-phosphate (carboxy-air), ATP and aspartate yield n(5-amino-4-imidazolylcarbonyl)-l-aspartic acid 5'-phosphate(succino-aicar), ADP and p Registry number: EC 6.3.4.- (26 Jun 1999) |
| UDPacetylglucosamine-dolichyl-phosphate acetylglucosamine-1-phosphate transferase | <enzyme> Transfers n-acetylglucosamine 1-phosphate from udp-n-acetylglucosamine to dolichyl phosphate, forming n-acetylglucosaminylpyrophosphoryldolichol Chemical name: udp-glcnac-dolichyl-phosphate glcnac-1-phosphate transerase Registry number: EC 2.7.8.15 Synonym: n-acetylglucosamine-1-phosphate transferase, dol-p-p-glcnac synthase, dolichol pathway enzyme I, udp-acetylglucosamine-dolichol phosphate acetylglucosamine-1-phosphate transferase, glcnac-dp-1-phosphotransferase, udp-n-acetyl-d-glucosamine-dolichyl-phosphate n-acetyl-d-glucosaminephosphotransferase, dolichol-p-dependent n-acetylglucosamine-1-phosphate transferase, alg7 gene product (26 Jun 1999) |
| UDP-GlcNAc-undecaprenyl phosphate N-acetylglucosaminyl 1-phosphate transferase | <enzyme> Catalyses transfer of n-acetylglucosamine 1-phosphate from udp-glcnac to undecaprenyl phosphate Registry number: EC 2.7.8.- Synonym: glcnac-p-p-und synthase, gpt enzyme (26 Jun 1999) |
| acetoacetyl-CoA synthetase | <enzyme> Catalyses the conversion of acetoacetate and CoA in the presence of ATP to yield AMP, pyrophosphate and acetoacetyl-CoA; the latter is the first intermediate in cholesterogenesis; also acts more slowly on l-3-hydroxybutanoate Registry number: EC 6.2.1.16 Synonym: acetoacetyl-CoA ligase, acetoacetate-CoA ligase, acetoacetyl-coenzyme a synthetase (26 Jun 1999) |
| acetyl-CoA synthetase | A ligase that catalyses the reaction of acetate and CoA and ATP to form AMP, pyrophosphate, and acetyl-CoA. A key step in the activation of acetate. Synonym: acetate thiokinase, acetate-CoA ligase, acetyl-activating enzyme, acetyl-CoA synthetase. (05 Mar 2000) |
| acid cholesterol ester synthetase | <enzyme> Aortal enzyme, does not require exogenous ATP or CoA; reverse reaction of cholesterol esterase Registry number: EC 3.1.1.- Synonym: cholesterol ester synthetase (26 Jun 1999) |
| carbamoyl phosphate synthetase |
1. carbamoyl-phosphate synthase (ammonia); called also carbamoyl phosphate synthetase I (CPSI). 2. carbamoyl-phosphate synthase (glutamine-hydrolyzing); called also carbamoyl phosphate synthetase II (CPSII).
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| carbamoyl phosphate synthetase deficiency |
a genetic aminoacidopathy due to a deficiency of carbamoyl phosphate synthase (ammonia); characteristic symptoms include pronounced hyperammonemia without oroticaciduria, protein intolerance, and neurologic disorders. Symptoms may begin in the neonatal period or appear later in infancy, with varying degrees of severity. Written also carbamoyl phosphate synthetase I (CPSI) deficiency.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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